Cluster composition

Functions

CategoryNameIntersectionWithQueryPValueGenesInTermGenesInQueryGenesInTermInQueryID
GeneOntologyMolecularFunctioncalcium ion binding

SNED1 HSPG2 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 ADAMTS13 LTBP3 EGFL7 LTBP4 AGRN FBN3 NOTCH4 STAB1

1.17e-157495921GO:0005509
GeneOntologyMolecularFunctionextracellular matrix structural constituent

HSPG2 FBN1 FBN2 COMP HMCN1 LAMB1 LAMB3 LTBP4 SSPOP AGRN FBN3

7.25e-121885911GO:0005201
GeneOntologyMolecularFunctionstructural molecule activity

HSPG2 FBN1 FBN2 COMP HMCN1 KRT83 LAMB1 LAMB3 LTBP4 SSPOP AGRN FBN3

9.33e-068915912GO:0005198
GeneOntologyMolecularFunctionintegrin binding

ITGBL1 FBN1 COMP LAMB1 ADAMTS13 LTBP4

1.28e-05175596GO:0005178
GeneOntologyMolecularFunctionlow-density lipoprotein particle receptor activity

LRP1 LRP2 STAB1

1.34e-0516593GO:0005041
GeneOntologyMolecularFunctionlipoprotein particle receptor activity

LRP1 LRP2 STAB1

3.14e-0521593GO:0030228
GeneOntologyMolecularFunctiontransforming growth factor beta binding

LTBP3 LTBP4 AGRN

6.07e-0526593GO:0050431
GeneOntologyMolecularFunctionNotch binding

SNED1 EGFL7 NOTCH4

6.81e-0527593GO:0005112
GeneOntologyMolecularFunctionheparan sulfate proteoglycan binding

COMP LRP1 AGRN

8.48e-0529593GO:0043395
GeneOntologyMolecularFunctiongrowth factor binding

ERBB3 LRP2 LTBP3 LTBP4 AGRN

9.72e-05156595GO:0019838
GeneOntologyMolecularFunctionlipoprotein particle receptor binding

HSPG2 LRP1 LRP2

2.08e-0439593GO:0070325
GeneOntologyMolecularFunctionproteoglycan binding

COMP LRP1 AGRN

4.61e-0451593GO:0043394
GeneOntologyMolecularFunctionextracellular matrix constituent conferring elasticity

FBN1 FBN2

5.56e-0412592GO:0030023
GeneOntologyMolecularFunctionstructural molecule activity conferring elasticity

FBN1 FBN2

7.63e-0414592GO:0097493
GeneOntologyMolecularFunctionglycosaminoglycan binding

FBN1 COMP LTBP4 AGRN STAB1

1.16e-03268595GO:0005539
GeneOntologyMolecularFunctioncytokine binding

COMP LTBP3 LTBP4 AGRN

1.20e-03157594GO:0019955
GeneOntologyMolecularFunctioncell adhesion molecule binding

ITGBL1 FBN1 COMP LAMB1 ADAMTS13 LTBP4 STAT1

1.86e-03599597GO:0050839
GeneOntologyMolecularFunctionBMP binding

COMP AGRN

1.91e-0322592GO:0036122
GeneOntologyMolecularFunctionprotease binding

HSPG2 COMP ACR LRP1

2.02e-03181594GO:0002020
GeneOntologyMolecularFunctioncargo receptor activity

LRP1 LRP2 STAB1

2.04e-0385593GO:0038024
GeneOntologyMolecularFunctionK63-linked polyubiquitin modification-dependent protein binding

RNF169 OTUD7A

2.67e-0326592GO:0070530
GeneOntologyMolecularFunctionscavenger receptor activity

LRP1 STAB1

2.87e-0327592GO:0005044
GeneOntologyMolecularFunctionlow-density lipoprotein particle receptor binding

HSPG2 LRP2

4.53e-0334592GO:0050750
GeneOntologyBiologicalProcessaxon guidance

HSPG2 CELSR3 MEGF8 SEMA5B LRP1 LRP2 LAMB1 LAMB3 AGRN

1.11e-07285599GO:0007411
GeneOntologyBiologicalProcessneuron projection guidance

HSPG2 CELSR3 MEGF8 SEMA5B LRP1 LRP2 LAMB1 LAMB3 AGRN

1.14e-07286599GO:0097485
GeneOntologyBiologicalProcesstube development

HSPG2 CELSR1 FBN1 COMP MEGF8 PKD1 ADGRB1 LRP1 LRP2 LTBP3 MESP1 EGFL7 STAT1 PSPN NOTCH4 STAB1

1.28e-0614025916GO:0035295
GeneOntologyBiologicalProcessaxon development

HSPG2 CELSR3 MEGF8 SEMA5B FIGNL2 ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

1.75e-066425911GO:0061564
GeneOntologyBiologicalProcesscirculatory system development

ATF7 HSPG2 ERBB3 FBN1 COMP MEGF8 PKD1 ADGRB1 LRP1 LRP2 MESP1 EGFL7 STAT1 NOTCH4 DNMT1 STAB1

1.85e-0614425916GO:0072359
GeneOntologyBiologicalProcessresponse to wounding

THBD ERBB3 CELSR1 COMP FIGNL2 LRP1 ADAMTS13 HPS5 NOTCH4 TFF1 PEAR1

2.26e-066595911GO:0009611
GeneOntologyBiologicalProcesstube morphogenesis

HSPG2 CELSR1 COMP MEGF8 PKD1 ADGRB1 LRP1 LRP2 MESP1 EGFL7 STAT1 PSPN NOTCH4 STAB1

2.52e-0611255914GO:0035239
GeneOntologyBiologicalProcessvasculature development

HSPG2 COMP MEGF8 PKD1 ADGRB1 LRP1 LRP2 MESP1 EGFL7 STAT1 NOTCH4 DNMT1 STAB1

2.71e-069695913GO:0001944
GeneOntologyBiologicalProcessaxonogenesis

HSPG2 CELSR3 MEGF8 SEMA5B ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

4.19e-065665910GO:0007409
GeneOntologyBiologicalProcessartery morphogenesis

COMP MEGF8 LRP1 LRP2 NOTCH4

6.55e-0692595GO:0048844
GeneOntologyBiologicalProcessmorphogenesis of an epithelium

CELSR1 MEGF8 FIGNL2 PKD1 LRP2 MESP1 SYNE4 STAT1 PSPN NOTCH4

9.20e-066195910GO:0002009
GeneOntologyBiologicalProcessanimal organ morphogenesis

DGCR2 HSPG2 CELSR1 FBN2 COMP MEGF8 PKD1 LRP2 LAMB1 LAMB3 LTBP3 MESP1 STAT1 PSPN

1.01e-0512695914GO:0009887
GeneOntologyBiologicalProcessblood vessel development

HSPG2 COMP MEGF8 PKD1 ADGRB1 LRP1 LRP2 MESP1 EGFL7 STAT1 NOTCH4 STAB1

1.03e-059295912GO:0001568
GeneOntologyBiologicalProcesswound healing

THBD ERBB3 CELSR1 COMP FIGNL2 ADAMTS13 HPS5 NOTCH4 PEAR1

1.03e-05493599GO:0042060
GeneOntologyBiologicalProcessextracellular matrix organization

HSPG2 COMP HMCN1 LRP1 LAMB1 LAMB3 ADAMTS13 LTBP4

1.14e-05377598GO:0030198
GeneOntologyBiologicalProcessextracellular structure organization

HSPG2 COMP HMCN1 LRP1 LAMB1 LAMB3 ADAMTS13 LTBP4

1.16e-05378598GO:0043062
GeneOntologyBiologicalProcessexternal encapsulating structure organization

HSPG2 COMP HMCN1 LRP1 LAMB1 LAMB3 ADAMTS13 LTBP4

1.18e-05379598GO:0045229
GeneOntologyBiologicalProcesstransforming growth factor beta receptor superfamily signaling pathway

FBN1 FBN2 COMP MEGF8 LRP1 LRP2 LTBP3 LTBP4

3.73e-05445598GO:0141091
GeneOntologyBiologicalProcessartery development

COMP MEGF8 LRP1 LRP2 NOTCH4

3.91e-05133595GO:0060840
GeneOntologyBiologicalProcesscell morphogenesis involved in neuron differentiation

HSPG2 CELSR3 MEGF8 SEMA5B ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

4.66e-057485910GO:0048667
GeneOntologyBiologicalProcesstissue morphogenesis

CELSR1 MEGF8 FIGNL2 PKD1 LRP2 MESP1 SYNE4 STAT1 PSPN NOTCH4

4.76e-057505910GO:0048729
GeneOntologyBiologicalProcesssequestering of TGFbeta in extracellular matrix

FBN1 FBN2

4.81e-054592GO:0035583
GeneOntologyBiologicalProcesscell surface receptor protein serine/threonine kinase signaling pathway

FBN1 FBN2 COMP MEGF8 LRP1 LRP2 LTBP3 LTBP4

6.54e-05482598GO:0007178
GeneOntologyBiologicalProcesspositive regulation of lysosomal protein catabolic process

LRP1 LRP2

8.00e-055592GO:1905167
GeneOntologyBiologicalProcesschemoattraction of axon

LRP1 LRP2

8.00e-055592GO:0061642
GeneOntologyBiologicalProcessaorta development

MEGF8 LRP1 LRP2 NOTCH4

8.12e-0580594GO:0035904
GeneOntologyBiologicalProcessneuron projection morphogenesis

HSPG2 CELSR3 MEGF8 SEMA5B ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

8.34e-058025910GO:0048812
GeneOntologyBiologicalProcesscoronary vasculature development

MEGF8 LRP1 LRP2 MESP1

9.37e-0583594GO:0060976
GeneOntologyBiologicalProcessblood vessel morphogenesis

HSPG2 COMP MEGF8 ADGRB1 LRP1 LRP2 EGFL7 STAT1 NOTCH4 STAB1

9.72e-058175910GO:0048514
GeneOntologyBiologicalProcessplasma membrane bounded cell projection morphogenesis

HSPG2 CELSR3 MEGF8 SEMA5B ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

9.92e-058195910GO:0120039
GeneOntologyBiologicalProcesscell projection morphogenesis

HSPG2 CELSR3 MEGF8 SEMA5B ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

1.06e-048265910GO:0048858
GeneOntologyBiologicalProcessskeletal system morphogenesis

HSPG2 FBN2 COMP MEGF8 PKD1 LTBP3

1.38e-04277596GO:0048705
GeneOntologyBiologicalProcesscell-substrate adhesion

SNED1 ITGBL1 PKD1 LRP1 LAMB1 LAMB3 ADAMTS13

1.63e-04410597GO:0031589
GeneOntologyBiologicalProcesspositive regulation of protein catabolic process in the vacuole

LRP1 LRP2

1.67e-047592GO:1904352
GeneOntologyBiologicalProcesssmooth muscle cell differentiation

COMP MESP1 NOTCH4 DNMT1

1.86e-0499594GO:0051145
GeneOntologyBiologicalProcessepithelial tube morphogenesis

CELSR1 MEGF8 PKD1 LRP2 MESP1 PSPN NOTCH4

1.92e-04421597GO:0060562
GeneOntologyBiologicalProcessmaintenance of protein location in extracellular region

FBN1 FBN2

2.23e-048592GO:0071694
GeneOntologyBiologicalProcessbasement membrane organization

HMCN1 LAMB1 LAMB3

2.53e-0443593GO:0071711
GeneOntologyBiologicalProcesscell recognition

CELSR3 MEGF8 ACR ADGRB1 PEAR1

2.55e-04198595GO:0008037
GeneOntologyBiologicalProcessheart development

ATF7 HSPG2 ERBB3 FBN1 MEGF8 PKD1 LRP1 LRP2 MESP1

2.79e-04757599GO:0007507
GeneOntologyBiologicalProcessapoptotic cell clearance

ADGRB1 LRP1 PEAR1

3.51e-0448593GO:0043277
GeneOntologyBiologicalProcesscellular response to transforming growth factor beta stimulus

FBN1 FBN2 LRP1 LTBP3 LTBP4 DNMT1

3.89e-04336596GO:0071560
GeneOntologyBiologicalProcessresponse to transforming growth factor beta

FBN1 FBN2 LRP1 LTBP3 LTBP4 DNMT1

4.34e-04343596GO:0071559
GeneOntologyBiologicalProcesssecondary heart field specification

LRP2 MESP1

4.35e-0411592GO:0003139
GeneOntologyBiologicalProcesssequestering of extracellular ligand from receptor

FBN1 FBN2

4.35e-0411592GO:0035581
GeneOntologyBiologicalProcessbone morphogenesis

HSPG2 COMP MEGF8 LTBP3

4.39e-04124594GO:0060349
GeneOntologyBiologicalProcessenzyme-linked receptor protein signaling pathway

ERBB3 FBN1 FBN2 COMP MEGF8 LRP1 LRP2 LTBP3 LTBP4 AGRN PSPN

4.74e-0411865911GO:0007167
GeneOntologyBiologicalProcesscell morphogenesis

HSPG2 CELSR3 MEGF8 SEMA5B ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN NOTCH4

5.02e-0411945911GO:0000902
GeneOntologyBiologicalProcessregulation of lysosomal protein catabolic process

LRP1 LRP2

5.21e-0412592GO:1905165
GeneOntologyBiologicalProcessbasement membrane assembly

LAMB1 LAMB3

5.21e-0412592GO:0070831
GeneOntologyBiologicalProcessvascular associated smooth muscle cell differentiation

COMP MESP1 DNMT1

5.25e-0455593GO:0035886
GeneOntologyBiologicalProcessnegative regulation of developmental process

HSPG2 FBN1 FIGNL2 ADGRB1 TMEM131L LTBP3 MESP1 STAT1 NOTCH4 DNMT1 STAB1

6.01e-0412205911GO:0051093
GeneOntologyBiologicalProcessextracellular regulation of signal transduction

FBN1 FBN2

6.15e-0413592GO:1900115
GeneOntologyBiologicalProcessextracellular negative regulation of signal transduction

FBN1 FBN2

6.15e-0413592GO:1900116
GeneOntologyBiologicalProcessextracellular matrix assembly

LAMB1 LAMB3 LTBP4

6.45e-0459593GO:0085029
GeneOntologyBiologicalProcesscellular response to growth factor stimulus

FBN1 FBN2 COMP MEGF8 LRP1 LRP2 LTBP3 LTBP4 DNMT1

6.49e-04850599GO:0071363
GeneOntologyBiologicalProcessnegative regulation of cell adhesion

HSPG2 ERBB3 LRP1 TMEM131L LAMB1 NOTCH4

6.94e-04375596GO:0007162
GeneOntologyBiologicalProcessregulation of protein catabolic process in the vacuole

LRP1 LRP2

7.16e-0414592GO:1904350
GeneOntologyBiologicalProcessmotor neuron migration

CELSR1 CELSR3

8.25e-0415592GO:0097475
GeneOntologyBiologicalProcessmorphogenesis of a branching structure

CELSR1 FIGNL2 PKD1 PSPN NOTCH4

8.50e-04258595GO:0001763
GeneOntologyBiologicalProcessresponse to growth factor

FBN1 FBN2 COMP MEGF8 LRP1 LRP2 LTBP3 LTBP4 DNMT1

8.51e-04883599GO:0070848
GeneOntologyBiologicalProcesscell-cell adhesion

ITGBL1 CELSR1 CELSR3 COMP HMCN1 PKD1 TMEM131L LAMB1 NOTCH4 PEAR1

8.79e-0410775910GO:0098609
GeneOntologyBiologicalProcessblood coagulation

THBD COMP ADAMTS13 HPS5 PEAR1

8.80e-04260595GO:0007596
GeneOntologyBiologicalProcessneuron projection development

HSPG2 CELSR3 MEGF8 SEMA5B FIGNL2 ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

9.24e-0412855911GO:0031175
GeneOntologyBiologicalProcessbone development

HSPG2 FBN1 COMP MEGF8 LTBP3

9.42e-04264595GO:0060348
GeneOntologyBiologicalProcesscoagulation

THBD COMP ADAMTS13 HPS5 PEAR1

9.75e-04266595GO:0050817
GeneOntologyBiologicalProcesshemostasis

THBD COMP ADAMTS13 HPS5 PEAR1

1.01e-03268595GO:0007599
GeneOntologyBiologicalProcesscell-matrix adhesion

SNED1 ITGBL1 PKD1 LRP1 ADAMTS13

1.04e-03270595GO:0007160
GeneOntologyBiologicalProcessheart field specification

LRP2 MESP1

1.06e-0317592GO:0003128
GeneOntologyBiologicalProcessplatelet activation

THBD COMP ADAMTS13 PEAR1

1.09e-03158594GO:0030168
GeneOntologyBiologicalProcesstransforming growth factor beta receptor signaling pathway

FBN1 FBN2 LRP1 LTBP3 LTBP4

1.15e-03276595GO:0007179
GeneOntologyBiologicalProcessregulation of motor neuron apoptotic process

ERBB3 AGRN

1.48e-0320592GO:2000671
GeneOntologyBiologicalProcessmulti-multicellular organism process

HSPG2 THBD FBN2 ACR LAMB1

1.52e-03294595GO:0044706
GeneOntologyBiologicalProcessnegative regulation of angiogenesis

HSPG2 ADGRB1 STAT1 STAB1

1.58e-03175594GO:0016525
GeneOntologyBiologicalProcessnegative regulation of blood vessel morphogenesis

HSPG2 ADGRB1 STAT1 STAB1

1.69e-03178594GO:2000181
GeneOntologyBiologicalProcessnegative regulation of vasculature development

HSPG2 ADGRB1 STAT1 STAB1

1.76e-03180594GO:1901343
GeneOntologyBiologicalProcessskeletal system development

HSPG2 FBN1 FBN2 COMP MEGF8 PKD1 LTBP3

1.80e-03615597GO:0001501
GeneOntologyBiologicalProcesshomophilic cell adhesion via plasma membrane adhesion molecules

CELSR1 CELSR3 HMCN1 PKD1

2.02e-03187594GO:0007156
GeneOntologyBiologicalProcesslysosomal protein catabolic process

LRP1 LRP2

2.13e-0324592GO:1905146
GeneOntologyBiologicalProcesstranscytosis

LRP1 LRP2

2.13e-0324592GO:0045056
GeneOntologyBiologicalProcessregulation of transforming growth factor beta receptor signaling pathway

FBN1 FBN2 LRP1 LTBP4

2.22e-03192594GO:0017015
GeneOntologyBiologicalProcessregulation of bone mineralization

FBN2 COMP LTBP3

2.26e-0391593GO:0030500
GeneOntologyBiologicalProcessregulation of cellular response to transforming growth factor beta stimulus

FBN1 FBN2 LRP1 LTBP4

2.35e-03195594GO:1903844
GeneOntologyBiologicalProcessBMP signaling pathway

FBN1 COMP MEGF8 LRP2

2.44e-03197594GO:0030509
GeneOntologyBiologicalProcessbranching morphogenesis of an epithelial tube

CELSR1 PKD1 PSPN NOTCH4

2.48e-03198594GO:0048754
GeneOntologyBiologicalProcessregulation of muscle cell differentiation

LAMB1 MESP1 NOTCH4 DNMT1

2.53e-03199594GO:0051147
GeneOntologyBiologicalProcessneuron development

HSPG2 CELSR3 MEGF8 SEMA5B FIGNL2 ADGRB1 LRP1 LRP2 LAMB1 LAMB3 AGRN

2.61e-0314635911GO:0048666
GeneOntologyBiologicalProcessepithelium development

CELSR1 MEGF8 KRT83 FIGNL2 PKD1 LRP2 MESP1 SYNE4 STAT1 PSPN NOTCH4

2.70e-0314695911GO:0060429
GeneOntologyBiologicalProcesspositive regulation of cholesterol efflux

LRP1 ZDHHC8

2.70e-0327592GO:0010875
GeneOntologyBiologicalProcessembryo implantation

HSPG2 FBN2 LAMB1

2.71e-0397593GO:0007566
GeneOntologyCellularComponentextracellular matrix

SNED1 HSPG2 FBN1 FBN2 COMP HMCN1 MEGF6 LAMB1 LAMB3 ADAMTS13 LTBP3 EGFL7 LTBP4 SSPOP AGRN FBN3

2.31e-116565916GO:0031012
GeneOntologyCellularComponentexternal encapsulating structure

SNED1 HSPG2 FBN1 FBN2 COMP HMCN1 MEGF6 LAMB1 LAMB3 ADAMTS13 LTBP3 EGFL7 LTBP4 SSPOP AGRN FBN3

2.42e-116585916GO:0030312
GeneOntologyCellularComponentcollagen-containing extracellular matrix

HSPG2 FBN1 FBN2 COMP HMCN1 MEGF6 LAMB1 LAMB3 LTBP3 EGFL7 LTBP4 SSPOP AGRN

2.15e-095305913GO:0062023
GeneOntologyCellularComponentmicrofibril

FBN1 FBN2 LTBP4 FBN3

4.01e-0813594GO:0001527
GeneOntologyCellularComponentbasement membrane

HSPG2 FBN1 HMCN1 LAMB1 LAMB3 AGRN

1.22e-06122596GO:0005604
GeneOntologyCellularComponentaxonal growth cone

LRP1 LRP2 AGRN

2.79e-0445593GO:0044295
GeneOntologyCellularComponentlaminin complex

LAMB1 LAMB3

3.47e-0410592GO:0043256
MousePhenoheart right ventricle hypertrophy

FBN1 PKD1 LRP2 LTBP4

1.85e-0542534MP:0000276
MousePhenoabnormal pelvic girdle bone morphology

DGCR2 HSPG2 FBN1 FBN2 COMP

1.89e-0587535MP:0004509
MousePhenoabnormal respiratory system morphology

HSPG2 THBD CELSR1 FBN1 CELSR3 MEGF8 PKD1 LRP2 LAMB3 NUBP1 LTBP3 LTBP4 AGRN STAT1

1.95e-0510275314MP:0002132
MousePhenoabnormal heart right ventricle morphology

HSPG2 FBN1 MEGF8 PKD1 LRP2 LTBP4

2.61e-05156536MP:0003920
MousePhenodecreased chondrocyte proliferation

HSPG2 COMP PKD1

2.78e-0516533MP:0014101
MousePhenodecreased respiration

HSPG2 ERBB3 FBN1 CELSR3 LRP2 NUBP1

4.23e-05170536MP:0014274
MousePhenoabnormal heart right ventricle wall morphology

FBN1 PKD1 LRP2 LTBP4

4.36e-0552534MP:0031534
MousePhenoincreased heart right ventricle size

FBN1 PKD1 LRP2 LTBP4

5.44e-0555534MP:0010563
MousePhenoabnormal chondrocyte proliferation

HSPG2 COMP PKD1

5.61e-0520533MP:0014099
MousePhenoosteoarthritis

HSPG2 COMP LTBP3

6.52e-0521533MP:0003560
MousePhenoabnormal ophthalmic nerve morphology

ERBB3 MEGF8

8.42e-054532MP:0009798
MousePhenoabnormal lung morphology

THBD CELSR1 FBN1 CELSR3 MEGF8 PKD1 LRP2 NUBP1 LTBP4 AGRN STAT1

1.16e-047675311MP:0001175
MousePhenomicrognathia

FBN2 MEGF8 PKD1 LRP2

1.25e-0468534MP:0002639
MousePhenoabnormal atrioventricular valve morphology

ERBB3 FBN1 MEGF8 PKD1

1.33e-0469534MP:0002745
MousePhenoabnormal jaw morphology

HSPG2 FBN1 FBN2 MEGF8 PKD1 OTUD7A LRP2 LAMB3 LTBP3

1.51e-04530539MP:0000454
MousePhenolimbs/digits/tail phenotype

HSPG2 CELSR1 FBN1 FBN2 COMP MEGF8 PKD1 LRP1 LRP2 LAMB1 NUBP1 HPS5 AGRN STAT1

1.79e-0412585314MP:0005371
MousePhenoabnormal heart atrium and ventricle connection

ERBB3 FBN1 MEGF8 PKD1

1.83e-0475534MP:0010435
MousePhenoabnormal aorta morphology

HSPG2 FBN1 MEGF8 PKD1 LRP2 LTBP4

1.99e-04225536MP:0000272
MousePhenoabnormal heart right ventricle size

FBN1 PKD1 LRP2 LTBP4

2.13e-0478534MP:0010577
MousePhenodelayed neural tube closure

CELSR1 LRP2 MESP1

2.15e-0431533MP:0002621
MousePhenoaneurysm

HSPG2 FBN1 PKD1

3.09e-0435533MP:0003279
MousePhenoabnormal viscerocranium morphology

HSPG2 FBN1 FBN2 MEGF8 PKD1 OTUD7A LRP2 LAMB3 LTBP3

3.49e-04593539MP:0005274
MousePhenodecreased circulating total protein level

TSPOAP1 KRT83 PKD1 TFF1 PEAR1

3.60e-04162535MP:0005567
MousePhenooverexpanded pulmonary alveolus

FBN1 LRP2 LTBP4

3.65e-0437533MP:0001183
MousePhenoemphysema

FBN1 LRP2 LTBP4

3.65e-0437533MP:0001958
MousePhenoabnormal heart valve morphology

HSPG2 ERBB3 FBN1 MEGF8 PKD1

3.70e-04163535MP:0000285
MousePhenorespiratory failure

HSPG2 ERBB3 CELSR3 LRP2 NUBP1

3.92e-04165535MP:0001953
MousePhenoabnormal appendicular skeleton morphology

DGCR2 HSPG2 FBN1 FBN2 COMP MEGF8 PKD1 LTBP3 LTBP4 SSPOP STAT1

4.47e-048965311MP:0009250
MousePhenoabnormal bone structure

ATRN ATF7 DGCR2 HSPG2 RNF169 FBN1 FBN2 ATXN7L2 MCHR1 MEGF6 PKD1 LRP2 LTBP3 STAT1

4.64e-0413795314MP:0003795
MousePhenoincreased aorta wall thickness

FBN1 LTBP4

4.99e-049532MP:0010996
MousePhenoaortic dissection

FBN1 PKD1

4.99e-049532MP:0004044
MousePhenoabnormal lung size

THBD CELSR1 PKD1 NUBP1 LTBP4

4.99e-04174535MP:0004881
MousePhenoabnormal chondrocyte physiology

HSPG2 COMP PKD1

5.32e-0442533MP:0009780
MousePhenoabnormal skeleton physiology

HSPG2 RNF169 FBN1 FBN2 COMP MEGF8 PKD1 LTBP3 STAT1

5.55e-04632539MP:0001533
MousePhenoabnormal cartilage physiology

HSPG2 COMP PKD1

5.71e-0443533MP:0031306
MousePhenodecreased compact bone mass

MCHR1 PKD1

6.22e-0410532MP:0010962
MousePhenoatelectasis

CELSR3 LRP2 LTBP4 AGRN

7.37e-04108534MP:0001177
MousePhenohemopericardium

HSPG2 FBN1 PKD1

7.42e-0447533MP:0005244
MousePhenoabnormal cranium morphology

HSPG2 CELSR1 FBN1 FBN2 MEGF8 PKD1 OTUD7A LRP2 LAMB3 LTBP3

8.33e-048135310MP:0000438
MousePhenoabnormal craniofacial bone morphology

HSPG2 CELSR1 FBN1 FBN2 MEGF8 PKD1 OTUD7A LRP2 LAMB3 LTBP3

9.50e-048275310MP:0002116
MousePhenoabnormal systemic artery morphology

HSPG2 FBN1 MEGF8 PKD1 LRP2 LTBP4

9.79e-04304536MP:0011655
MousePhenoabnormal heart layer morphology

HSPG2 THBD ERBB3 MEGF8 PKD1 LRP2 LTBP4

1.01e-03422537MP:0010545
MousePhenoomphalocele

MEGF8 LRP1 LRP2

1.05e-0353533MP:0003052
MousePhenoatrioventricular valve regurgitation

ERBB3 FBN1

1.07e-0313532MP:0006046
MousePhenopulmonary hypoplasia

CELSR1 PKD1 NUBP1

1.11e-0354533MP:0001178
MousePhenodecreased circulating protein level

THBD FBN2 TSPOAP1 KRT83 PKD1 ADGRB1 STAT1 TFF1 PEAR1

1.13e-03698539MP:0014502
MousePhenoheart hemorrhage

HSPG2 FBN1 PKD1

1.17e-0355533MP:0009698
MousePhenoaortic aneurysm

FBN1 PKD1

1.25e-0314532MP:0006278
MousePhenoabnormal aorta elastic fiber morphology

FBN1 LTBP4

1.25e-0314532MP:0003211
MousePhenoabnormal artery morphology

HSPG2 FBN1 MEGF8 PKD1 LRP2 HPS5 LTBP4

1.29e-03440537MP:0002191
MousePhenoperinatal lethality, complete penetrance

ERBB3 CELSR1 CELSR3 PKD1 LRP1 LRP2 LAMB3 NUBP1 AGRN

1.29e-03712539MP:0011089
MousePhenodisproportionate dwarf

HSPG2 COMP PKD1

1.30e-0357533MP:0002427
DomainEGF_1

ATRN SNED1 HSPG2 ITGBL1 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LAMB1 LAMB3 LTBP3 EGFL7 LTBP4 SSPOP AGRN FBN3 NOTCH4 PEAR1 STAB1

1.35e-332555826PS00022
DomainEGF_2

ATRN SNED1 HSPG2 ITGBL1 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LAMB1 LAMB3 LTBP3 EGFL7 LTBP4 SSPOP AGRN FBN3 NOTCH4 PEAR1 STAB1

3.80e-332655826PS01186
DomainEGF

ATRN SNED1 HSPG2 ITGBL1 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LAMB1 LTBP3 EGFL7 LTBP4 AGRN FBN3 NOTCH4 PEAR1 STAB1

6.60e-312355824SM00181
DomainEGF-like_dom

ATRN SNED1 HSPG2 ITGBL1 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LAMB1 LTBP3 EGFL7 LTBP4 AGRN FBN3 NOTCH4 PEAR1 STAB1

2.77e-302495824IPR000742
DomainEGF_CA

SNED1 HSPG2 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 AGRN FBN3 NOTCH4 STAB1

5.89e-301225820SM00179
DomainEGF-like_Ca-bd_dom

SNED1 HSPG2 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 AGRN FBN3 NOTCH4 STAB1

8.36e-301245820IPR001881
DomainEGF-like_CS

ATRN SNED1 HSPG2 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LAMB1 LAMB3 LTBP3 EGFL7 LTBP4 AGRN FBN3 NOTCH4 PEAR1 STAB1

8.87e-302615824IPR013032
DomainGrowth_fac_rcpt_

ATRN HSPG2 THBD ERBB3 CELSR1 FBN1 FBN2 COMP HMCN1 MEGF6 MEGF8 KRT83 LRP1 LRP2 LAMB1 LTBP3 EGFL7 LTBP4 FBN3 NOTCH4 STAB1

1.46e-291565821IPR009030
DomainEGF_3

ATRN SNED1 HSPG2 THBD CELSR1 FBN1 FBN2 CELSR3 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 SSPOP AGRN FBN3 NOTCH4 PEAR1 STAB1

3.94e-292355823PS50026
DomainASX_HYDROXYL

SNED1 THBD CELSR1 FBN1 FBN2 CELSR3 HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 FBN3 NOTCH4

8.65e-241005816PS00010
DomainEGF-type_Asp/Asn_hydroxyl_site

SNED1 THBD CELSR1 FBN1 FBN2 CELSR3 HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 FBN3 NOTCH4

2.34e-231065816IPR000152
DomainEGF_Ca-bd_CS

SNED1 THBD FBN1 FBN2 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 FBN3 NOTCH4

4.32e-22975815IPR018097
DomainEGF_CA

SNED1 THBD FBN1 FBN2 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 FBN3 NOTCH4

5.98e-22995815PS01187
DomainEGF_CA

THBD FBN1 FBN2 COMP HMCN1 MEGF6 MEGF8 LRP1 LRP2 LTBP3 EGFL7 LTBP4 FBN3 NOTCH4

5.47e-21865814PF07645
DomainLaminin_EGF

ATRN HSPG2 CELSR1 CELSR3 MEGF6 MEGF8 LAMB1 LAMB3 AGRN PEAR1 STAB1

3.73e-20355811PF00053
DomainEGF_Lam

ATRN HSPG2 CELSR1 CELSR3 MEGF6 MEGF8 LAMB1 LAMB3 AGRN PEAR1 STAB1

3.73e-20355811SM00180
DomainLaminin_EGF

ATRN HSPG2 CELSR1 CELSR3 MEGF6 MEGF8 LAMB1 LAMB3 AGRN PEAR1 STAB1

1.07e-19385811IPR002049
DomainEGF

ATRN SNED1 HSPG2 THBD CELSR1 CELSR3 HMCN1 MEGF6 LRP1 LRP2 AGRN FBN3 NOTCH4 STAB1

1.52e-181265814PF00008
DomainEGF_LAM_2

ATRN HSPG2 CELSR1 CELSR3 MEGF8 LAMB1 LAMB3 AGRN STAB1

1.91e-1630589PS50027
DomainEGF_LAM_1

ATRN HSPG2 CELSR1 CELSR3 MEGF8 LAMB1 LAMB3 AGRN STAB1

1.91e-1630589PS01248
DomaincEGF

THBD FBN1 FBN2 HMCN1 LRP1 LRP2 LTBP3 FBN3

7.82e-1526588IPR026823
DomaincEGF

THBD FBN1 FBN2 HMCN1 LRP1 LRP2 LTBP3 FBN3

7.82e-1526588PF12662
DomainTB

FBN1 FBN2 LTBP3 LTBP4 FBN3

5.06e-127585PF00683
Domain-

FBN1 FBN2 LTBP3 LTBP4 FBN3

1.35e-1185853.90.290.10
DomainTB

FBN1 FBN2 LTBP3 LTBP4 FBN3

3.02e-119585PS51364
DomainTB_dom

FBN1 FBN2 LTBP3 LTBP4 FBN3

3.02e-119585IPR017878
DomainhEGF

SNED1 FBN2 MEGF6 LTBP3 FBN3 NOTCH4

2.46e-1028586PF12661
DomainLDLRA_1

DGCR2 HSPG2 PKD1 LRP1 LRP2 SSPOP

7.63e-0948586PS01209
DomainLDLRA_2

DGCR2 HSPG2 PKD1 LRP1 LRP2 SSPOP

8.67e-0949586PS50068
DomainFBN

FBN1 FBN2 FBN3

2.84e-083583IPR011398
DomainEGF_extracell

ATRN ITGBL1 MEGF6 LRP2 EGFL7 STAB1

3.02e-0860586IPR013111
DomainEGF_2

ATRN ITGBL1 MEGF6 LRP2 EGFL7 STAB1

3.02e-0860586PF07974
DomainLDLR_class-A_CS

DGCR2 HSPG2 LRP1 LRP2 SSPOP

1.47e-0740585IPR023415
DomainEMI

MEGF6 EGFL7 SSPOP PEAR1

1.93e-0717584PS51041
DomainLdl_recept_a

DGCR2 HSPG2 LRP1 LRP2 SSPOP

2.69e-0745585PF00057
Domain-

DGCR2 HSPG2 LRP1 LRP2 SSPOP

3.01e-07465854.10.400.10
DomainLDrepeatLR_classA_rpt

DGCR2 HSPG2 LRP1 LRP2 SSPOP

4.16e-0749585IPR002172
DomainLDLa

DGCR2 HSPG2 LRP1 LRP2 SSPOP

4.16e-0749585SM00192
DomainTSP_1

HMCN1 SEMA5B ADGRB1 ADAMTS13 SSPOP

1.48e-0663585PF00090
DomainTSP1

HMCN1 SEMA5B ADGRB1 ADAMTS13 SSPOP

1.73e-0665585SM00209
DomainTSP1_rpt

HMCN1 SEMA5B ADGRB1 ADAMTS13 SSPOP

1.73e-0665585IPR000884
DomainTSP1

HMCN1 SEMA5B ADGRB1 ADAMTS13 SSPOP

1.73e-0665585PS50092
DomainGPS

CELSR1 CELSR3 PKD1 ADGRB1

3.62e-0634584SM00303
DomainGPS

CELSR1 CELSR3 PKD1 ADGRB1

4.08e-0635584PF01825
DomainGPS

CELSR1 CELSR3 PKD1 ADGRB1

4.58e-0636584PS50221
DomainGAIN_dom_N

CELSR1 CELSR3 ADGRB1

4.61e-0611583IPR032471
DomainGAIN

CELSR1 CELSR3 ADGRB1

4.61e-0611583PF16489
DomainGPS

CELSR1 CELSR3 PKD1 ADGRB1

5.12e-0637584IPR000203
DomainLAM_G_DOMAIN

HSPG2 CELSR1 CELSR3 AGRN

5.71e-0638584PS50025
DomainLamG

HSPG2 CELSR1 CELSR3 AGRN

1.04e-0544584SM00282
Domain-

HSPG2 CELSR1 CELSR3 COMP AGRN

1.13e-05955852.60.120.200
Domain-

ATRN DGCR2 THBD PKD1 STAB1

1.25e-05975853.10.100.10
DomainC-type_lectin-like/link

ATRN DGCR2 THBD PKD1 STAB1

1.39e-0599585IPR016186
DomainEMI_domain

MEGF6 EGFL7 PEAR1

1.55e-0516583IPR011489
DomainCTDL_fold

ATRN DGCR2 THBD PKD1 STAB1

2.02e-05107585IPR016187
DomainLaminin_G

HSPG2 CELSR1 CELSR3 AGRN

3.13e-0558584IPR001791
DomainConA-like_dom

HSPG2 CELSR1 CELSR3 COMP TRIM58 AGRN

5.91e-05219586IPR013320
DomainHormR

CELSR1 CELSR3 ADGRB1

6.23e-0525583SM00008
DomainHRM

CELSR1 CELSR3 ADGRB1

8.81e-0528583PF02793
DomainPSI

ATRN MEGF8 SEMA5B

1.32e-0432583PF01437
DomainPlexin_repeat

ATRN MEGF8 SEMA5B

1.32e-0432583IPR002165
DomainLectin_C

ATRN DGCR2 THBD PKD1

1.34e-0484584PF00059
DomainCLECT

ATRN DGCR2 THBD PKD1

1.34e-0484584SM00034
DomainC_TYPE_LECTIN_2

ATRN DGCR2 THBD PKD1

1.41e-0485584PS50041
DomainC-type_lectin-like

ATRN DGCR2 THBD PKD1

1.47e-0486584IPR001304
DomainG_PROTEIN_RECEP_F2_1

CELSR1 CELSR3 ADGRB1

2.59e-0440583PS00649
DomainGPCR_2_extracellular_dom

CELSR1 CELSR3 ADGRB1

2.59e-0440583IPR001879
DomainLaminin_G_2

HSPG2 CELSR1 CELSR3

2.59e-0440583PF02210
DomainG_PROTEIN_RECEP_F2_3

CELSR1 CELSR3 ADGRB1

2.59e-0440583PS50227
DomainPSI

ATRN MEGF8 SEMA5B

3.44e-0444583IPR016201
DomainPSI

ATRN MEGF8 SEMA5B

3.92e-0446583SM00423
DomainG_PROTEIN_RECEP_F2_2

CELSR1 CELSR3 ADGRB1

5.02e-0450583PS00650
Domain7tm_2

CELSR1 CELSR3 ADGRB1

5.02e-0450583PF00002
DomainFol_N

SNED1 AGRN

5.12e-0411582IPR003645
Domain-

HMCN1 STAB1

5.12e-04115822.40.155.10
DomainGFP-like

HMCN1 STAB1

5.12e-0411582IPR023413
DomainLaminin_G_1

HSPG2 AGRN

5.12e-0411582PF00054
DomainFOLN

SNED1 AGRN

5.12e-0411582SM00274
DomainCUB

ATRN MEGF8 ADAMTS13

5.96e-0453583PS01180
DomainEGF_3

MEGF8 STAB1

6.13e-0412582PF12947
DomainEGF_dom

MEGF8 STAB1

6.13e-0412582IPR024731
DomainCUB_dom

ATRN MEGF8 ADAMTS13

7.38e-0457583IPR000859
DomainSEA

HSPG2 AGRN

8.42e-0414582SM00200
DomainTIL_dom

LRP2 SSPOP

8.42e-0414582IPR002919
DomainLdl_recept_b

LRP1 LRP2

8.42e-0414582PF00058
DomainLDLRB

LRP1 LRP2

8.42e-0414582PS51120
DomainGPCR_2_secretin-like

CELSR1 CELSR3 ADGRB1

8.58e-0460583IPR000832
DomainGPCR_2-like

CELSR1 CELSR3 ADGRB1

8.58e-0460583IPR017981
DomainG_PROTEIN_RECEP_F2_4

CELSR1 CELSR3 ADGRB1

9.00e-0461583PS50261
DomainLY

LRP1 LRP2

9.70e-0415582SM00135
DomainLDLR_classB_rpt

LRP1 LRP2

9.70e-0415582IPR000033
DomainLaminin_N

LAMB1 LAMB3

1.11e-0316582IPR008211
DomainLAMININ_NTER

LAMB1 LAMB3

1.11e-0316582PS51117
DomainLaminin_N

LAMB1 LAMB3

1.11e-0316582PF00055
DomainLamNT

LAMB1 LAMB3

1.11e-0316582SM00136
DomainSEA

HSPG2 AGRN

2.10e-0322582PF01390
DomainSEA

HSPG2 AGRN

2.30e-0323582PS50024
DomainSEA_dom

HSPG2 AGRN

2.30e-0323582IPR000082
PathwayREACTOME_EXTRACELLULAR_MATRIX_ORGANIZATION

HSPG2 FBN1 FBN2 COMP LAMB1 LAMB3 LTBP3 LTBP4 AGRN FBN3

2.15e-083004410M610
PathwayREACTOME_MOLECULES_ASSOCIATED_WITH_ELASTIC_FIBRES

FBN1 FBN2 LTBP3 LTBP4 FBN3

9.48e-0837445M27134
PathwayREACTOME_ELASTIC_FIBRE_FORMATION

FBN1 FBN2 LTBP3 LTBP4 FBN3

2.32e-0744445M26969
PathwayKEGG_MEDICUS_REFERENCE_PLASMIN_MEDIATED_ACTIVATION_OF_LATENT_TGF_BETA

FBN1 LTBP3 LTBP4

1.57e-068443M47850
PathwayREACTOME_MOLECULES_ASSOCIATED_WITH_ELASTIC_FIBRES

FBN1 FBN2 LTBP3 LTBP4

2.78e-0632444MM14854
PathwayREACTOME_DEGRADATION_OF_THE_EXTRACELLULAR_MATRIX

HSPG2 FBN1 FBN2 LAMB1 LAMB3 FBN3

4.46e-06140446M587
PathwayREACTOME_DISEASES_OF_GLYCOSYLATION

HSPG2 SEMA5B ADAMTS13 SSPOP AGRN NOTCH4

5.04e-06143446M27275
PathwayKEGG_ECM_RECEPTOR_INTERACTION

HSPG2 COMP LAMB1 LAMB3 AGRN

6.03e-0684445M7098
PathwayREACTOME_ELASTIC_FIBRE_FORMATION

FBN1 FBN2 LTBP3 LTBP4

6.27e-0639444MM14601
PathwayREACTOME_EXTRACELLULAR_MATRIX_ORGANIZATION

FBN1 FBN2 COMP MEGF6 LTBP3 LTBP4 AGRN

1.36e-05258447MM14572
PathwayREACTOME_METABOLISM_OF_FAT_SOLUBLE_VITAMINS

HSPG2 LRP1 LRP2 AGRN

1.45e-0548444M27642
PathwayREACTOME_NON_INTEGRIN_MEMBRANE_ECM_INTERACTIONS

HSPG2 LAMB1 LAMB3 AGRN

3.32e-0559444M27218
PathwayREACTOME_DISEASES_ASSOCIATED_WITH_O_GLYCOSYLATION_OF_PROTEINS

SEMA5B ADAMTS13 SSPOP NOTCH4

5.81e-0568444M27303
PathwayWP_HYPOTHESIZED_PATHWAYS_IN_PATHOGENESIS_OF_CARDIOVASCULAR_DISEASE

FBN1 FBN2 FBN3

6.22e-0525443M39713
PathwayREACTOME_ECM_PROTEOGLYCANS

HSPG2 COMP LAMB1 AGRN

8.99e-0576444M27219
PathwayREACTOME_LAMININ_INTERACTIONS

HSPG2 LAMB1 LAMB3

1.09e-0430443M27216
PathwayREACTOME_DISEASES_OF_METABOLISM

HSPG2 SEMA5B ADAMTS13 SSPOP AGRN NOTCH4

1.18e-04250446M27554
PathwayREACTOME_INTEGRIN_CELL_SURFACE_INTERACTIONS

HSPG2 FBN1 COMP AGRN

1.39e-0485444M16441
PathwayREACTOME_SIGNALING_BY_TGF_BETA_RECEPTOR_COMPLEX

FBN1 LTBP3 LTBP4 STAT1

2.05e-0494444M1041
PathwayREACTOME_TGF_BETA_RECEPTOR_SIGNALING_ACTIVATES_SMADS

FBN1 LTBP3 LTBP4

2.22e-0438443MM14874
PathwayREACTOME_O_GLYCOSYLATION_OF_TSR_DOMAIN_CONTAINING_PROTEINS

SEMA5B ADAMTS13 SSPOP

2.40e-0439443M27417
PathwayREACTOME_O_GLYCOSYLATION_OF_TSR_DOMAIN_CONTAINING_PROTEINS

SEMA5B ADAMTS13 SSPOP

2.40e-0439443MM15165
PathwayREACTOME_VISUAL_PHOTOTRANSDUCTION

HSPG2 LRP1 LRP2 AGRN

2.60e-04100444M27158
PathwayREACTOME_METABOLISM_OF_FAT_SOLUBLE_VITAMINS

LRP1 LRP2 AGRN

3.67e-0445443MM15344
PathwayPID_A6B1_A6B4_INTEGRIN_PATHWAY

ERBB3 LAMB1 LAMB3

3.92e-0446443M239
PathwayREACTOME_TGF_BETA_RECEPTOR_SIGNALING_ACTIVATES_SMADS

FBN1 LTBP3 LTBP4

4.18e-0447443M646
PathwayPID_INTEGRIN4_PATHWAY

LAMB1 LAMB3

5.14e-0411442M158
PathwayWP_TGFBETA_RECEPTOR_SIGNALING_IN_SKELETAL_DYSPLASIAS

FBN1 LTBP3 STAT1

8.16e-0459443M39886
PathwayREACTOME_DEFECTIVE_EXT2_CAUSES_EXOSTOSES_2

HSPG2 AGRN

8.46e-0414442M27263
PathwayPID_INTEGRIN1_PATHWAY

FBN1 LAMB1 LAMB3

1.13e-0366443M18
PathwayREACTOME_SIGNALING_BY_TGFB_FAMILY_MEMBERS

FBN1 LTBP3 LTBP4 STAT1

1.56e-03161444M27871
PathwayREACTOME_ATTACHMENT_AND_ENTRY

HSPG2 AGRN

1.57e-0319442M41729
PathwayREACTOME_DEFECTIVE_B4GALT7_CAUSES_EDS_PROGEROID_TYPE

HSPG2 AGRN

1.75e-0320442M27258
PathwayREACTOME_SIGNALING_BY_TGF_BETA_RECEPTOR_COMPLEX

FBN1 LTBP3 LTBP4

1.77e-0377443MM14670
PathwayREACTOME_RESPIRATORY_SYNCYTIAL_VIRUS_RSV_ATTACHMENT_AND_ENTRY

HSPG2 AGRN

2.31e-0323442M48234
PathwayREACTOME_HS_GAG_DEGRADATION

HSPG2 AGRN

2.52e-0324442M636
PathwayREACTOME_VISUAL_PHOTOTRANSDUCTION

LRP1 LRP2 AGRN

2.94e-0392443MM14881
PathwayREACTOME_A_TETRASACCHARIDE_LINKER_SEQUENCE_IS_REQUIRED_FOR_GAG_SYNTHESIS

HSPG2 AGRN

2.95e-0326442M708
Pubmed

Comparison of an expanded ataxia interactome with patient medical records reveals a relationship between macular degeneration and ataxia.

HSPG2 FBN1 MEGF6 MEGF8 TSPOAP1 LRP1 LAMB1 LTBP3 LTBP4 AGRN

7.48e-15118591021078624
Pubmed

Quantitative proteomic profiling of the extracellular matrix of pancreatic islets during the angiogenic switch and insulinoma progression.

HSPG2 FBN1 FBN2 HMCN1 MEGF6 LAMB1 EGFL7 LTBP4 SSPOP AGRN

4.08e-13175591028071719
Pubmed

Comparative proteomic analysis of supportive and unsupportive extracellular matrix substrates for human embryonic stem cell maintenance.

HSPG2 FBN1 FBN2 LAMB1 EGFL7 AGRN

2.75e-105059623658023
Pubmed

The matrisome: in silico definition and in vivo characterization by proteomics of normal and tumor extracellular matrices.

HSPG2 FBN1 HMCN1 LAMB1 LAMB3 EGFL7 LTBP4 AGRN

4.30e-1016759822159717
Pubmed

ESCPE-1 mediates retrograde endosomal sorting of the SARS-CoV-2 host factor Neuropilin-1.

ATRN DGCR2 HSPG2 CELSR1 FBN1 FBN2 CELSR3 MEGF8 LRP1 TMEM131L LAMB1 LAMB3 LTBP3 AGRN DNMT1

1.04e-091201591535696571
Pubmed

Local anesthetics impair the growth and self-renewal of glioblastoma stem cells by inhibiting ZDHHC15-mediated GP130 palmitoylation.

FBN1 FBN2 LRP1 LRP2 LTBP3 SSPOP

2.41e-097159633541421
Pubmed

Chr21 protein-protein interactions: enrichment in proteins involved in intellectual disability, autism, and late-onset Alzheimer's disease.

ATRN ERBB3 FBN1 CELSR3 MCHR1 KRT83 PKD1 LRP1 LRP2 LAMB1 ZNF76 LTBP3 STAT1 DNMT1 STAB1

2.61e-091285591535914814
Pubmed

Characterization of the Extracellular Matrix of Normal and Diseased Tissues Using Proteomics.

HSPG2 FBN1 FBN2 LAMB1 EGFL7 LTBP4 AGRN

3.27e-0913559728675934
Pubmed

A dual-activity topoisomerase complex regulates mRNA translation and turnover.

ZXDC DGCR2 HSPG2 CELSR1 CELSR3 MEGF6 MEGF8 PKD1 LAMB3 LTBP3 LTBP4 ZDHHC8 AGRN SYNE4

3.45e-091105591435748872
Pubmed

A protein-protein interaction network for human inherited ataxias and disorders of Purkinje cell degeneration.

HSPG2 ATXN7L2 MEGF6 MEGF8 LRP2 LAMB1 EGFL7 LTBP4 SSPOP AGRN TFF1

5.58e-09608591116713569
Pubmed

Extracellular matrix remodelling in response to venous hypertension: proteomics of human varicose veins.

HSPG2 FBN1 COMP LAMB1 LTBP3 LTBP4 AGRN

5.65e-0914659727068509
Pubmed

Latent transforming growth factor beta-binding protein 1 interacts with fibrillin and is a microfibril-associated protein.

FBN1 FBN2 LTBP4

1.85e-08459312429738
Pubmed

Heparin/heparan sulfate controls fibrillin-1, -2 and -3 self-interactions in microfibril assembly.

FBN1 FBN2 FBN3

1.85e-08459325034023
Pubmed

Protein interactome reveals converging molecular pathways among autism disorders.

ITGBL1 FBN1 MEGF6 MEGF8 LTBP3 EGFL7 LTBP4 AGRN DNMT1 STAB1

3.35e-08560591021653829
Pubmed

Development, composition, and structural arrangements of the ciliary zonule of the mouse.

HSPG2 FBN1 FBN2

4.63e-08559323493297
Pubmed

Proteomics analysis of cardiac extracellular matrix remodeling in a porcine model of ischemia/reperfusion injury.

HSPG2 HMCN1 LAMB1 SSPOP AGRN

8.34e-086459522261194
Pubmed

Biochemical Reduction of the Topology of the Diverse WDR76 Protein Interactome.

HSPG2 FBN1 FBN2 LRP1 LAMB1 EGFL7 AGRN

9.21e-0821959731353912
Pubmed

Loss of Daxx, a promiscuously interacting protein, results in extensive apoptosis in early mouse development.

LAMB1 NOTCH4 DNMT1

9.24e-08659310444590
Pubmed

Basement membrane assembly of the integrin α8β1 ligand nephronectin requires Fraser syndrome-associated proteins.

HSPG2 LAMB1 LAMB3 AGRN

1.72e-072959422613833
Pubmed

O-fucosylation of thrombospondin type 1 repeats restricts epithelial to mesenchymal transition (EMT) and maintains epiblast pluripotency during mouse gastrulation.

HMCN1 SEMA5B ADGRB1 ADAMTS13 SSPOP

1.86e-077559520637190
Pubmed

Extracellular matrix secretion by cardiac fibroblasts: role of microRNA-29b and microRNA-30c.

HSPG2 ITGBL1 FBN1 COMP LAMB1 LTBP4 AGRN

2.14e-0724859724006456
Pubmed

TBX1 is required for normal stria vascularis and semicircular canal development.

ATRN FBN1 COMP STAB1

2.27e-073159431550482
Pubmed

Extracellular matrix signatures of human primary metastatic colon cancers and their metastases to liver.

HSPG2 FBN1 LAMB1 LAMB3 EGFL7 LTBP4

2.44e-0715359625037231
Pubmed

Specific 3-O-sulfated heparan sulfate domains regulate salivary gland basement membrane metabolism and epithelial differentiation.

HSPG2 ERBB3 LAMB1 LAMB3 AGRN

2.74e-078159539217171
Pubmed

Identification of high-molecular-weight proteins with multiple EGF-like motifs by motif-trap screening.

CELSR3 MEGF6 MEGF8

3.87e-0795939693030
Pubmed

Microfibril-associated glycoprotein-2 interacts with fibrillin-1 and fibrillin-2 suggesting a role for MAGP-2 in elastic fiber assembly.

FBN1 FBN2 MEGF6

3.87e-07959312122015
Pubmed

Glycoproteomics Reveals Decorin Peptides With Anti-Myostatin Activity in Human Atrial Fibrillation.

HSPG2 FBN1 LAMB1 LTBP4 AGRN

6.76e-079759527559042
Pubmed

Proteomics characterization of extracellular space components in the human aorta.

HSPG2 FBN1 COMP LTBP4 AGRN

8.26e-0710159520551380
Pubmed

Proteomic identification of common SCF ubiquitin ligase FBXO6-interacting glycoproteins in three kinds of cells.

ATRN HSPG2 FBN2 MEGF8 LRP1 TMEM131L LAMB1 LTBP3 LTBP4

8.88e-0761359922268729
Pubmed

Mesangial cells organize the glomerular capillaries by adhering to the G domain of laminin alpha5 in the glomerular basement membrane.

HSPG2 LAMB1 AGRN

1.31e-061359312682087
Pubmed

Nell1-deficient mice have reduced expression of extracellular matrix proteins causing cranial and vertebral defects.

THBD COMP SEMA5B PKD1 LAMB3 LTBP3

1.56e-0621059616537572
Pubmed

Basement membrane composition in the early mouse embryo day 7.

HSPG2 LAMB1 LAMB3

2.08e-061559315895400
Pubmed

Lack of cadherins Celsr2 and Celsr3 impairs ependymal ciliogenesis, leading to fatal hydrocephalus.

CELSR1 CELSR3 SSPOP

2.08e-061559320473291
Pubmed

Homo- and heterotypic fibrillin-1 and -2 interactions constitute the basis for the assembly of microfibrils.

FBN1 FBN2

2.83e-06259212399449
Pubmed

Fibrillin-1 and fibrillin-2 are essential for formation of thick oxytalan fibers in human nonpigmented ciliary epithelial cells in vitro.

FBN1 FBN2

2.83e-06259221851253
Pubmed

Fibrillins can co-assemble in fibrils, but fibrillin fibril composition displays cell-specific differences.

FBN1 FBN2

2.83e-06259212429739
Pubmed

New Evidence Supporting the Role of FBN1 in the Development of Adolescent Idiopathic Scoliosis.

FBN1 FBN2

2.83e-06259230044367
Pubmed

Genetic analysis of the contribution of LTBP-3 to thoracic aneurysm in Marfan syndrome.

FBN1 LTBP3

2.83e-06259226494287
Pubmed

Material and mechanical properties of bones deficient for fibrillin-1 or fibrillin-2 microfibrils.

FBN1 FBN2

2.83e-06259221440062
Pubmed

Agrin and perlecan mediate tumorigenic processes in oral squamous cell carcinoma.

HSPG2 AGRN

2.83e-06259225506919
Pubmed

MAGP-2 has multiple binding regions on fibrillins and has covalent periodic association with fibrillin-containing microfibrils.

FBN1 FBN2

2.83e-06259215131124
Pubmed

Endocytic Protein Defects in the Neural Crest Cell Lineage and Its Pathway Are Associated with Congenital Heart Defects.

LRP1 LRP2

2.83e-06259234445520
Pubmed

Control of lung development by latent TGF-β binding proteins.

LTBP3 LTBP4

2.83e-06259220945348
Pubmed

Fibrillin-1 and fibrillin-2 in human embryonic and early fetal development.

FBN1 FBN2

2.83e-06259212524050
Pubmed

Microfibril structure masks fibrillin-2 in postnatal tissues.

FBN1 FBN2

2.83e-06259220404337
Pubmed

LTBP3 Pathogenic Variants Predispose Individuals to Thoracic Aortic Aneurysms and Dissections.

FBN1 LTBP3

2.83e-06259229625025
Pubmed

Fibrillln mutations in Marfan syndrome and related phenotypes.

FBN1 FBN2

2.83e-0625928791520
Pubmed

Comparative immunolocalisation of fibrillin-1 and perlecan in the human foetal, and HS-deficient hspg2 exon 3 null mutant mouse intervertebral disc.

HSPG2 FBN1

2.83e-06259223104139
Pubmed

Structure and expression of fibrillin-2, a novel microfibrillar component preferentially located in elastic matrices.

FBN1 FBN2

2.83e-0625928120105
Pubmed

The fibrillinopathies: New insights with focus on the paradigm of opposing phenotypes for both FBN1 and FBN2.

FBN1 FBN2

2.83e-06259235419902
Pubmed

Fibrillin genes map to regions of conserved mouse/human synteny on mouse chromosomes 2 and 18.

FBN1 FBN2

2.83e-0625928307578
Pubmed

Fibrillin assembly: dimer formation mediated by amino-terminal sequences.

FBN1 FBN2

2.83e-06259210504303
Pubmed

Three novel mutations of the fibrillin-1 gene and ten single nucleotide polymorphisms of the fibrillin-3 gene in Marfan syndrome patients.

FBN1 FBN3

2.83e-06259215221638
Pubmed

Developmental expression of fibrillin genes suggests heterogeneity of extracellular microfibrils.

FBN1 FBN2

2.83e-0625927744963
Pubmed

Fibrillin microfibrils in bone physiology.

FBN1 FBN2

2.83e-06259226408953
Pubmed

Arg-Gly-Asp-containing domains of fibrillins-1 and -2 distinctly regulate lung fibroblast migration.

FBN1 FBN2

2.83e-06259218006876
Pubmed

Rare variants in FBN1 and FBN2 are associated with severe adolescent idiopathic scoliosis.

FBN1 FBN2

2.83e-06259224833718
Pubmed

Exome sequencing identified new mutations in a Marfan syndrome family.

FBN1 LRP1

2.83e-06259224484584
Pubmed

The Fbn1 gene variant governs passive ascending aortic mechanics in the mgΔlpn mouse model of Marfan syndrome when superimposed to perlecan haploinsufficiency.

HSPG2 FBN1

2.83e-06259238545339
Pubmed

Nonselective assembly of fibrillin 1 and fibrillin 2 in the rodent ocular zonule and in cultured cells: implications for Marfan syndrome.

FBN1 FBN2

2.83e-06259224265020
Pubmed

In vivo studies of mutant fibrillin-1 microfibrils.

FBN1 FBN2

2.83e-06259220529844
Pubmed

Immunohistochemical expression of fibrillin-1 and fibrillin-2 during tooth development.

FBN1 FBN2

2.83e-06259225524144
Pubmed

Agrin binds to the nerve-muscle basal lamina via laminin.

LAMB1 AGRN

2.83e-0625929151673
Pubmed

Fibrillin-1 mutations causing Weill-Marchesani syndrome and acromicric and geleophysic dysplasias disrupt heparan sulfate interactions.

FBN1 FBN2

2.83e-06259223133647
Pubmed

Absence of LTBP-3 attenuates the aneurysmal phenotype but not spinal effects on the aorta in Marfan syndrome.

FBN1 LTBP3

2.83e-06259230306291
Pubmed

Fibrillins 1 and 2 perform partially overlapping functions during aortic development.

FBN1 FBN2

2.83e-06259216407178
Pubmed

Is HSPG2 a modifier gene for Marfan syndrome?

HSPG2 FBN1

2.83e-06259232514132
Pubmed

Linkage of Marfan syndrome and a phenotypically related disorder to two different fibrillin genes.

FBN1 FBN2

2.83e-0625921852206
Pubmed

N-terminal domains of fibrillin 1 and fibrillin 2 direct the formation of homodimers: a possible first step in microfibril assembly.

FBN1 FBN2

2.83e-06259210359653
Pubmed

Microfibrils at basement membrane zones interact with perlecan via fibrillin-1.

HSPG2 FBN1

2.83e-06259215657057
Pubmed

ADAMTS18-fibronectin interaction regulates the morphology of liver sinusoidal endothelial cells.

FBN1 FBN2 LAMB1

3.72e-061859339040056
Pubmed

Human plasma N-glycoproteome analysis by immunoaffinity subtraction, hydrazide chemistry, and mass spectrometry.

ATRN HSPG2 MEGF8 LRP1 LAMB1 ADAMTS13

4.99e-0625759616335952
Pubmed

Renal collecting system growth and function depend upon embryonic γ1 laminin expression.

HSPG2 LAMB1 AGRN

8.02e-062359321903675
Pubmed

Interaction of tropoelastin with the amino-terminal domains of fibrillin-1 and fibrillin-2 suggests a role for the fibrillins in elastic fiber assembly.

FBN1 FBN2

8.48e-06359210825173
Pubmed

A Pkd1-Fbn1 genetic interaction implicates TGF-β signaling in the pathogenesis of vascular complications in autosomal dominant polycystic kidney disease.

FBN1 PKD1

8.48e-06359224071006
Pubmed

A forward genetic screen in mice identifies Sema3A(K108N), which binds to neuropilin-1 but cannot signal.

ERBB3 MEGF8

8.48e-06359220410128
Pubmed

Adamts10 inactivation in mice leads to persistence of ocular microfibrils subsequent to reduced fibrillin-2 cleavage.

FBN1 FBN2

8.48e-06359230201140
Pubmed

An mTurq2-Col4a1 mouse model allows for live visualization of mammalian basement membrane development.

HSPG2 LAMB1

8.48e-06359238051393
Pubmed

The flamingo-related mouse Celsr family (Celsr1-3) genes exhibit distinct patterns of expression during embryonic development.

CELSR1 CELSR3

8.48e-06359211677057
Pubmed

Geleophysic Dysplasia

FBN1 LTBP3

8.48e-06359220301776
Pubmed

Fibrillin-1 and -2 differentially modulate endogenous TGF-β and BMP bioavailability during bone formation.

FBN1 FBN2

8.48e-06359220855508
Pubmed

TGFβ attenuates cartilage extracellular matrix degradation via enhancing FBXO6-mediated MMP14 ubiquitination.

HSPG2 LRP1 LAMB1 LAMB3 AGRN

8.94e-0616459532409323
Pubmed

Transcriptome-based systematic identification of extracellular matrix proteins.

HSPG2 LAMB1 LAMB3 AGRN

1.02e-057959418757743
Pubmed

ERp57 is essential for efficient folding of glycoproteins sharing common structural domains.

LAMB1 LAMB3 AGRN

1.04e-052559317170699
Pubmed

Adamts18 modulates the development of the aortic arch and common carotid artery.

FBN1 FBN2 LAMB1

1.17e-052659334189436
Pubmed

ETS2 overexpression ameliorates cartilage injury in osteoarthritis by the ETS2/miR-155/STAT1/DNMT1 feedback loop pathway.

STAT1 DNMT1

1.69e-05459237524226
Pubmed

Human eye development is characterized by coordinated expression of fibrillin isoforms.

FBN1 FBN2

1.69e-05459225406291
Pubmed

Latent transforming growth factor-beta (TGF-beta) binding proteins: orchestrators of TGF-beta availability.

LTBP3 LTBP4

1.69e-05459215611103
Pubmed

Extracellular microfibrils control osteoblast-supported osteoclastogenesis by restricting TGF{beta} stimulation of RANKL production.

FBN1 FBN2

1.69e-05459220729550
Pubmed

Disabled-2 is essential for endodermal cell positioning and structure formation during mouse embryogenesis.

LRP1 LRP2

1.69e-05459212413896
Pubmed

Comprehensive genetic analysis of relevant four genes in 49 patients with Marfan syndrome or Marfan-related phenotypes.

FBN1 FBN2

1.69e-05459216835936
Pubmed

The adhesion GPCRs CELSR1-3 and LPHN3 engage G proteins via distinct activation mechanisms.

CELSR1 CELSR3

1.69e-05459237224017
Pubmed

Identification of the low density lipoprotein receptor-related protein (LRP) as an endocytic receptor for thrombospondin-1.

LRP1 LRP2

1.69e-0545927775583
Pubmed

Role of apolipoprotein E receptors in regulating the differential in vivo neurotrophic effects of apolipoprotein E.

LRP1 LRP2

1.69e-05459211421580
Pubmed

Conjugation of LG domains of agrins and perlecan to polymerizing laminin-2 promotes acetylcholine receptor clustering.

HSPG2 AGRN

1.69e-05459216219760
Pubmed

Evaluation of the ARMD1 locus on 1q25-31 in patients with age-related maculopathy: genetic variation in laminin genes and in exon 104 of HEMICENTIN-1.

HMCN1 LAMB3

1.69e-05459215370542
Pubmed

Spatial and temporal deletion reveals a latent effect of Megf8 on the left-right patterning and heart development.

MEGF8 MESP1

1.69e-05459232203821
Pubmed

Association analysis of genes involved in the maintenance of the integrity of the extracellular matrix with intracranial aneurysms in a Japanese cohort.

HSPG2 FBN2

1.69e-05459219506372
Pubmed

Developmental expression profiles of Celsr (Flamingo) genes in the mouse.

CELSR1 CELSR3

1.69e-05459211850187
Pubmed

The latent transforming growth factor beta binding protein (LTBP) family.

LTBP3 LTBP4

1.69e-05459211104663
InteractionCACNA1A interactions

HSPG2 MEGF6 MEGF8 TSPOAP1 LRP1 LAMB1 LTBP3 LTBP4 AGRN

7.23e-11123589int:CACNA1A
InteractionFBXO2 interactions

ATRN SNED1 HSPG2 FBN1 FBN2 CELSR3 MEGF8 LRP2 TMEM131L LAMB1 LAMB3 LTBP4 AGRN

1.20e-104115813int:FBXO2
InteractionZFP41 interactions

FBN1 FBN2 LRP1 LRP2 LTBP4 AGRN

1.41e-0857586int:ZFP41
InteractionATXN7 interactions

FBN1 ATXN7L2 MEGF6 MEGF8 LAMB1 LTBP4 AGRN

2.67e-08109587int:ATXN7
InteractionCFC1 interactions

DGCR2 CELSR1 MEGF8 LAMB1 LAMB3 LTBP4 AGRN

7.29e-08126587int:CFC1
InteractionGFI1B interactions

HSPG2 MEGF6 MEGF8 LAMB1 EGFL7 LTBP4 AGRN

1.23e-07136587int:GFI1B
InteractionBTNL2 interactions

ATRN DGCR2 CELSR1 MEGF8 TMEM131L LAMB1 LAMB3

3.01e-07155587int:BTNL2
InteractionMFAP5 interactions

FBN1 FBN2 MEGF6 EGFL7 LTBP4

3.88e-0752585int:MFAP5
InteractionNTN5 interactions

FBN1 FBN2 LRP2 LTBP4

6.29e-0724584int:NTN5
InteractionEDN3 interactions

ATRN HSPG2 CELSR1 MEGF8 LAMB3 AGRN

6.65e-07108586int:EDN3
InteractionATN1 interactions

HSPG2 MEGF6 MEGF8 LRP2 LTBP4 SSPOP AGRN

1.07e-06187587int:ATN1
InteractionZDHHC15 interactions

FBN1 FBN2 LRP1 LRP2 LTBP3 SSPOP

1.57e-06125586int:ZDHHC15
InteractionIGFL3 interactions

ATRN FBN2 LRP2 LAMB1 AGRN

2.45e-0675585int:IGFL3
InteractionZNF408 interactions

ATRN HSPG2 FBN1 FBN2 LRP2 LTBP4

3.72e-06145586int:ZNF408
InteractionSDF2L1 interactions

ATRN DGCR2 HSPG2 CELSR1 MEGF8 LAMB1 LAMB3 AGRN

3.73e-06322588int:SDF2L1
InteractionFBXO6 interactions

ATRN HSPG2 FBN2 MEGF8 LRP1 TMEM131L LAMB1 LAMB3 LTBP3 LTBP4 AGRN

5.30e-067175811int:FBXO6
InteractionHOXA1 interactions

FBN1 MEGF6 MEGF8 KRT83 LTBP3 EGFL7 LTBP4 AGRN

7.78e-06356588int:HOXA1
InteractionC1orf54 interactions

CELSR1 CELSR3 PKD1 LAMB1 LAMB3 AGRN

8.39e-06167586int:C1orf54
InteractionPRG2 interactions

HSPG2 CELSR1 FBN2 LAMB3 LTBP3 EGFL7 LTBP4

1.71e-05285587int:PRG2
InteractionLYPD1 interactions

ATRN CELSR1 MEGF8 LAMB1

2.33e-0558584int:LYPD1
InteractionNUFIP2 interactions

COMP MEGF6 LTBP3 EGFL7 LTBP4 AGRN PEAR1 STAB1

2.44e-05417588int:NUFIP2
InteractionDYRK1A interactions

ATRN SNED1 ERBB3 RNF169 FBN1 LRP2 LAMB1 LTBP3 STAB1

2.62e-05552589int:DYRK1A
InteractionLY86 interactions

ATRN CELSR1 TMEM131L LAMB1 LAMB3 EGFL7

3.69e-05217586int:LY86
InteractionSFTPC interactions

ATRN DGCR2 CELSR1 MEGF8 TMEM131L SYNE4

4.19e-05222586int:SFTPC
InteractionTOP3B interactions

ZXDC DGCR2 HSPG2 CELSR1 CELSR3 MEGF6 MEGF8 PKD1 LAMB3 LTBP3 LTBP4 ZDHHC8 AGRN SYNE4

5.46e-0514705814int:TOP3B
InteractionSLURP1 interactions

ATRN MEGF8 LAMB1 LAMB3 EGFL7

5.87e-05144585int:SLURP1
InteractionNTF3 interactions

LRP1 LAMB1 LAMB3

6.30e-0527583int:NTF3
InteractionGGH interactions

ATRN CELSR1 MEGF8 LAMB1 LAMB3 STAT1

6.92e-05243586int:GGH
InteractionMBD1 interactions

MEGF6 LTBP3 LTBP4 STAT1

7.15e-0577584int:MBD1
InteractionELN interactions

HSPG2 FBN1 FBN2

7.84e-0529583int:ELN
InteractionSIRPD interactions

DGCR2 HSPG2 CELSR1 MEGF8

1.10e-0486584int:SIRPD
InteractionWDR76 interactions

HSPG2 FBN1 FBN2 LRP1 LAMB1 EGFL7 AGRN

1.11e-04383587int:WDR76
InteractionELSPBP1 interactions

ATRN MEGF8 LAMB3 AGRN

1.43e-0492584int:ELSPBP1
InteractionCCN2 interactions

HSPG2 LRP1 LRP2

2.07e-0440583int:CCN2
InteractionCRISP2 interactions

ATRN CELSR1 LAMB3

2.07e-0440583int:CRISP2
InteractionXAGE1A interactions

CELSR1 CELSR3 ZNF574

2.23e-0441583int:XAGE1A
InteractionPSG8 interactions

CELSR3 MEGF8 LAMB1

2.23e-0441583int:PSG8
InteractionMEPE interactions

ZXDC LRP2

2.25e-048582int:MEPE
InteractionBRICD5 interactions

DGCR2 HSPG2 CELSR1 TMEM131L SYNE4

2.38e-04194585int:BRICD5
InteractionDNAJB9 interactions

DGCR2 CELSR1 LAMB1 LAMB3 AGRN

2.87e-04202585int:DNAJB9
InteractionST14 interactions

ATRN FBN1 FBN2 LAMB1 EGFL7

3.21e-04207585int:ST14
InteractionBTNL8 interactions

ATRN TMEM131L TFF1

3.35e-0447583int:BTNL8
InteractionRNF180 interactions

AGRN DNMT1

3.61e-0410582int:RNF180
InteractionLYZL1 interactions

ATRN DGCR2 CELSR1 LAMB3

3.71e-04118584int:LYZL1
InteractionHLA-G interactions

DGCR2 MEGF8 TMEM131L LAMB3

3.71e-04118584int:HLA-G
InteractionFBN1 interactions

HSPG2 FBN1 FBN2

4.27e-0451583int:FBN1
InteractionNELL2 interactions

LTBP3 EGFL7 LTBP4

4.78e-0453583int:NELL2
InteractionTHBS1 interactions

FBN2 LRP1 LRP2 LAMB3

4.90e-04127584int:THBS1
InteractionMFAP2 interactions

FBN1 FBN2

5.27e-0412582int:MFAP2
InteractionSCGB1A1 interactions

LRP2 AGRN

5.27e-0412582int:SCGB1A1
InteractionLBHD1 interactions

ERBB3 CTU2

6.22e-0413582int:LBHD1
InteractionLRRC7 interactions

ERBB3 OTUD7A ADGRB1

6.24e-0458583int:LRRC7
InteractionMANEA interactions

ATRN LAMB1 AGRN

6.89e-0460583int:MANEA
InteractionHRG interactions

FBN1 FBN2 LTBP4

7.95e-0463583int:HRG
InteractionVWCE interactions

FBN2 EGFL7 LTBP4

8.32e-0464583int:VWCE
InteractionCUBN interactions

LRP1 LRP2

8.34e-0415582int:CUBN
InteractionLAMA1 interactions

HSPG2 LAMB1 LAMB3

9.10e-0466583int:LAMA1
InteractionRPS6KA6 interactions

SYNE4 FBN3 DNMT1

9.51e-0467583int:RPS6KA6
InteractionSCN3A interactions

LRP1 LRP2

9.52e-0416582int:SCN3A
InteractionFCRL4 interactions

ZNF76 TFF1

9.52e-0416582int:FCRL4
Cytoband12q13

ATF7 ERBB3 KRT83

1.08e-047159312q13
CytobandEnsembl 112 genes in cytogenetic band chr12q13

ATF7 ERBB3 KRT83 FIGNL2 LRP1

2.16e-04423595chr12q13
GeneFamilyHyalectan proteoglycans|V-set domain containing|Sushi domain containing|C-type lectin domain containing

ATRN DGCR2 THBD PKD1

2.63e-06414341298
GeneFamilyAdhesion G protein-coupled receptors, subfamily C|CELSR cadherins

CELSR1 CELSR3

1.66e-053432913
GeneFamilyAdhesion G protein-coupled receptors, subfamily C|CELSR cadherins

CELSR1 CELSR3

1.66e-0534321189
GeneFamilyLatent transforming growth factor beta binding proteins

LTBP3 LTBP4

3.31e-054432628
GeneFamilyBlood group antigens|CD molecules|Proteoglycans

HSPG2 AGRN

1.15e-047432570
GeneFamilyLaminin subunits

LAMB1 LAMB3

3.59e-0412432626
GeneFamilyLow density lipoprotein receptors

LRP1 LRP2

4.24e-0413432634
CoexpressionNABA_ECM_GLYCOPROTEINS

SNED1 FBN1 FBN2 COMP HMCN1 LAMB1 LAMB3 LTBP3 LTBP4 SSPOP AGRN FBN3

1.79e-141965912M3008
CoexpressionNABA_CORE_MATRISOME

SNED1 HSPG2 FBN1 FBN2 COMP HMCN1 LAMB1 LAMB3 LTBP3 LTBP4 SSPOP AGRN FBN3

3.70e-142755913M5884
CoexpressionNABA_ECM_GLYCOPROTEINS

SNED1 FBN1 FBN2 COMP HMCN1 LAMB1 LAMB3 LTBP3 LTBP4 SSPOP AGRN

4.75e-131915911MM17059
CoexpressionNABA_MATRISOME

SNED1 HSPG2 FBN1 FBN2 COMP HMCN1 MEGF6 MEGF8 SEMA5B LAMB1 LAMB3 ADAMTS13 LTBP3 EGFL7 LTBP4 SSPOP AGRN FBN3 PSPN

4.90e-1310265919M5889
CoexpressionNABA_CORE_MATRISOME

SNED1 HSPG2 FBN1 FBN2 COMP HMCN1 LAMB1 LAMB3 LTBP3 LTBP4 SSPOP AGRN

8.14e-132705912MM17057
CoexpressionNABA_MATRISOME

SNED1 HSPG2 FBN1 FBN2 COMP HMCN1 MEGF6 MEGF8 SEMA5B LAMB1 LAMB3 ADAMTS13 LTBP3 EGFL7 LTBP4 SSPOP AGRN PSPN

4.25e-1210085918MM17056
CoexpressionNABA_BASEMENT_MEMBRANES

HSPG2 HMCN1 LAMB1 LAMB3 AGRN

3.01e-0840595M5887
CoexpressionHU_FETAL_RETINA_FIBROBLAST

SNED1 FBN1 FBN2 HMCN1 LAMB1 EGFL7 LTBP4 PEAR1

2.32e-06385598M39264
CoexpressionHEBERT_MATRISOME_TNBC_BRAIN_METASTASIS

HMCN1 EGFL7 AGRN

2.71e-0526593M47999
CoexpressionBRUINS_UVC_RESPONSE_VIA_TP53_GROUP_B

THBD CELSR3 PKD1 LRP1 LAMB3 LTBP3 LTBP4 AGRN

3.26e-05554598M2244
CoexpressionNABA_MATRISOME_HIGHLY_METASTATIC_BREAST_CANCER_TUMOR_CELL_DERIVED

SNED1 LTBP3 AGRN

3.80e-0529593M47987
CoexpressionNABA_MATRISOME_METASTATIC_COLORECTAL_LIVER_METASTASIS

COMP HMCN1 AGRN

4.21e-0530593M47990
CoexpressionGSE33162_HDAC3_KO_VS_HDAC3_KO_MACROPHAGE_UP

ERBB3 NUBP1 AGRN STAT1 ZNF574

8.61e-05199595M9038
CoexpressionGSE25123_CTRL_VS_IL4_AND_ROSIGLITAZONE_STIM_PPARG_KO_MACROPHAGE_UP

ATRN RNF169 TSPOAP1 LTBP3 SYNE4

8.82e-05200595M7980
CoexpressionNABA_MATRISOME_HIGHLY_METASTATIC_BREAST_CANCER

SNED1 LTBP3 AGRN

1.09e-0441593M47988
CoexpressionGAO_LARGE_INTESTINE_ADULT_CJ_IMMUNE_CELLS

SNED1 THBD FBN1 LRP1 EGFL7 NOTCH4 PEAR1

1.36e-04505597M39167
CoexpressionCUI_DEVELOPING_HEART_C3_FIBROBLAST_LIKE_CELL

FBN1 LRP1 LAMB1 LTBP4

1.42e-04117594M39300
CoexpressionZHANG_UTERUS_C14_ENDOTHELIAL_MMRN1_HIGH_CELL

EGFL7 LTBP4 STAB1

1.85e-0449593MM16620
CoexpressionPOOLA_INVASIVE_BREAST_CANCER_DN

CELSR1 LAMB3 LTBP3 LTBP4

2.32e-04133594M6767
CoexpressionDESCARTES_FETAL_THYMUS_STROMAL_CELLS

FBN1 FBN2 LRP1 LTBP4

2.60e-04137594M40313
CoexpressionPURWIN_A375_SOX10_TARGETS

ERBB3 NOTCH4 DNMT1

2.62e-0455593M48227
CoexpressionHALLMARK_COAGULATION

THBD FBN1 COMP LRP1

2.67e-04138594M5946
CoexpressionHOLLERN_EMT_BREAST_TUMOR_UP

HSPG2 PKD1 LRP1 LAMB1

2.83e-04140594M617
CoexpressionDESCARTES_FETAL_LIVER_VASCULAR_ENDOTHELIAL_CELLS

HSPG2 EGFL7 NOTCH4 STAB1

3.14e-04144594M40230
CoexpressionNABA_MATRISOME_PRIMARY_METASTATIC_COLORECTAL_TUMOR

HMCN1 MEGF8 AGRN

3.22e-0459593M47989
CoexpressionHEBERT_MATRISOME_TNBC_BRAIN_METASTASIS_TUMOR_CELL_DERIVED

HMCN1 AGRN

3.24e-0412592M47998
CoexpressionHOLLERN_EMT_BREAST_TUMOR_UP

HSPG2 PKD1 LRP1 LAMB1

3.31e-04146594MM964
CoexpressionAtlasStromal Cells, LEC.MLN, gp38+ CD31+, Lymph Node, avg-4

HSPG2 THBD FBN1 HMCN1 LAMB1 EGFL7 LTBP4 AGRN PEAR1 STAB1

2.77e-074395810GSM777059_500
CoexpressionAtlasdev gonad_e13.5_M_InterstitFLeydig_MafB_k-means-cluster#3_top-relative-expression-ranked_200

THBD FBN1 HMCN1 LRP1 LTBP4

2.96e-0682585gudmap_dev gonad_e13.5_M_InterstitFLeydig_MafB_k3_200
CoexpressionAtlasStromal Cells, LEC.SLN, gp38+ CD31+, Lymph Node, avg-4

HSPG2 THBD FBN1 HMCN1 LAMB1 EGFL7 LTBP4 AGRN STAB1

3.38e-06450589GSM777063_500
CoexpressionAtlasgeo_heart_top-relative-expression-ranked_2500_k-means-cluster#3

HSPG2 ITGBL1 EGFL7 ZDHHC8 NOTCH4 STAB1

1.05e-05183586geo_heart_2500_K3
CoexpressionAtlasStromal Cells, Fi.Sk, gp38+ CD140a+, Skin, avg-4

SNED1 HSPG2 ITGBL1 FBN1 HMCN1 LRP1 LAMB1 LTBP4

2.35e-05437588GSM777046_500
CoexpressionAtlasDevelopingGonad_e16.5_testes_emap-8444_k-means-cluster#2_top-relative-expression-ranked_500

THBD FBN1 SEMA5B LAMB1 LTBP4

2.71e-05129585gudmap_developingGonad_e16.5_testes_500_k2
CoexpressionAtlasStromal Cells, FRC.MLN, gp38+ CD31- CD140a+, Lymph Node, avg-5

HSPG2 THBD FBN1 HMCN1 LRP1 LAMB1 LTBP3 LTBP4

3.71e-05466588GSM777050_500
CoexpressionAtlasdev gonad_e13.5_M_InterstitFLeydig_MafB_top-relative-expression-ranked_200

THBD FBN1 HMCN1 LRP1 LTBP4

4.90e-05146585gudmap_dev gonad_e13.5_M_InterstitFLeydig_MafB_200
CoexpressionAtlasdev gonad_e13.5_M_InterstitTestis_Sma_k-means-cluster#1_top-relative-expression-ranked_500

THBD FBN1 HMCN1 LRP1 LTBP4

6.72e-05156585gudmap_dev gonad_e13.5_M_InterstitTestis_Sma_k1_500
CoexpressionAtlasdev gonad_e12.5_M_InterstitLeydig_MafB_k-means-cluster#2_top-relative-expression-ranked_500

THBD FBN1 HMCN1 LRP1 LTBP4

8.76e-05165585gudmap_dev gonad_e12.5_M_InterstitLeydig_MafB_k2_500
CoexpressionAtlasdev gonad_e13.5_F_VascAssocMesenchStromOvary_Sma_k-means-cluster#4_top-relative-expression-ranked_1000

FBN1 HMCN1 LRP1 LAMB1 LTBP4

9.54e-05168585gudmap_dev gonad_e13.5_F_VascAssocMesenchStromOvary_Sma_k4_1000
CoexpressionAtlasStromal Cells, LEC.MLN, gp38+ CD31+, Lymph Node, avg-4

FBN1 EGFL7 LTBP4 STAB1

1.12e-0491584GSM777059_100
CoexpressionAtlaskidney_adult_RenalCapsule_top-relative-expression-ranked_500

ITGBL1 FBN1 HMCN1 LRP1 LRP2 LTBP4 STAT1

1.19e-04408587gudmap_kidney_adult_RenalCapsule_500
CoexpressionAtlasDevelopingGonad_e14.5_ testes_emap-6710_k-means-cluster#2_top-relative-expression-ranked_1000

THBD FBN1 SEMA5B LAMB1 LTBP4

1.35e-04181585gudmap_developingGonad_e14.5_ testes_1000_k2
CoexpressionAtlasStromal Cells, Fi.MTS15+.Th, CD45- PDGFRa+ MTS15+, Thymus, avg-3

HSPG2 FBN1 LAMB1 LTBP4

1.44e-0497584GSM777043_100
CoexpressionAtlasDevelopingGonad_e14.5_ testes_emap-6710_k-means-cluster#5_top-relative-expression-ranked_500

THBD FBN1 SEMA5B LAMB1

1.50e-0498584gudmap_developingGonad_e14.5_ testes_500_k5
CoexpressionAtlasdev gonad_e12.5_M_InterstitTestis_Sma_k-means-cluster#4_top-relative-expression-ranked_1000

THBD FBN1 HMCN1 LAMB1 LTBP4

1.74e-04191585gudmap_dev gonad_e12.5_M_InterstitTestis_Sma_k4_1000
CoexpressionAtlasdev gonad_e12.5_M_InterstitLeydig_MafB_k-means-cluster#1_top-relative-expression-ranked_1000

THBD FBN1 FBN2 HMCN1 LRP1 LTBP4

1.97e-04310586gudmap_dev gonad_e12.5_M_InterstitLeydig_MafB_k1_1000
CoexpressionAtlasJC_hmvEC_top-relative-expression-ranked_2500_k-means-cluster#1

SNED1 HSPG2 ITGBL1 CTU2 LAMB1 EGFL7 STAT1 NOTCH4 PEAR1 STAB1

2.01e-049365810JC_hmvEC_2500_K1
CoexpressionAtlasdev gonad_e12.5_M_InterstitTestis_Sma_k-means-cluster#4_top-relative-expression-ranked_200

FBN1 HMCN1 LRP1

2.06e-0442583gudmap_dev gonad_e12.5_M_InterstitTestis_Sma_k4_200
CoexpressionAtlasgudmap_RNAseq_e15.5_Podocytes_2500_K0

SNED1 HSPG2 THBD CELSR1 FBN1 SEMA5B EGFL7 LTBP4 NOTCH4 ZNF513 STAB1

2.31e-0411435811gudmap_RNAseq_e15.5_Podocytes_2500_K0
CoexpressionAtlasStromal Cells, FRC.SLN, gp38+ CD31- CD140a+, Lymph Node, avg-4

SNED1 HSPG2 THBD FBN1 LRP1 LAMB1 LTBP4

2.32e-04455587GSM777055_500
CoexpressionAtlasStromal Cells, BEC.MLN, gp38- CD31+, Lymph Node, avg-5

HSPG2 THBD LAMB1 EGFL7 LTBP4 NOTCH4 STAB1

2.35e-04456587GSM777032_500
CoexpressionAtlaskidney_adult_RenalCapsule_top-relative-expression-ranked_1000

ITGBL1 THBD FBN1 HMCN1 LRP1 LRP2 LTBP3 LTBP4 STAT1

2.42e-04778589gudmap_kidney_adult_RenalCapsule_1000
CoexpressionAtlasStromal Cells, BEC.SLN, gp38- CD31+, Lymph Node, avg-4

HSPG2 THBD LAMB1 EGFL7 LTBP4 NOTCH4 STAB1

2.45e-04459587GSM777037_500
CoexpressionAtlasDevelopingKidney_e15.5_Endothelial cells_emap-29977_k-means-cluster#3_top-relative-expression-ranked_100

EGFL7 NOTCH4 STAB1

2.70e-0446583DevelopingKidney_e15.5_Endothelial cells_emap-29977_k3_100
CoexpressionAtlasDevelopingGonad_e16.5_testes_emap-8444_k-means-cluster#5_top-relative-expression-ranked_1000

THBD FBN1 SEMA5B LAMB1 LTBP4

2.95e-04214585gudmap_developingGonad_e16.5_testes_1000_k5
CoexpressionAtlasdev gonad_e13.5_M_InterstitFLeydig_MafB_k-means-cluster#3_top-relative-expression-ranked_1000

THBD FBN1 HMCN1 LRP1 LAMB1 LTBP4

3.04e-04336586gudmap_dev gonad_e13.5_M_InterstitFLeydig_MafB_k3_1000
CoexpressionAtlasDevelopingGonad_P2_testes_emap-30171_k-means-cluster#1_top-relative-expression-ranked_500

THBD FBN1 SEMA5B LAMB1

3.15e-04119584gudmap_developingGonad_P2_testes_500_k1
CoexpressionAtlasJC_hmvEC_top-relative-expression-ranked_1000

SNED1 HSPG2 ITGBL1 THBD LAMB3 EGFL7 STAT1 NOTCH4 PEAR1 STAB1

3.15e-049905810JC_hmvEC_1000
CoexpressionAtlasdev gonad_e13.5_F_VascAssocMesenchStromOvary_MafB_k-means-cluster#3_top-relative-expression-ranked_500

FBN1 FBN2 HMCN1 LRP1

3.46e-04122584gudmap_dev gonad_e13.5_F_VascAssocMesenchStromOvary_MafB_k3_500
CoexpressionAtlasdev gonad_e13.5_M_InterstitFLeydig_MafB_top-relative-expression-ranked_500

THBD FBN1 FBN2 HMCN1 LRP1 LTBP4

4.13e-04356586gudmap_dev gonad_e13.5_M_InterstitFLeydig_MafB_500
CoexpressionAtlasDevelopingGonad_e18.5_testes_emap-11164_k-means-cluster#5_top-relative-expression-ranked_500

THBD FBN1 SEMA5B LAMB1

4.15e-04128584gudmap_developingGonad_e18.5_testes_500_k5
CoexpressionAtlasfacebase_RNAseq_e14.5_palate_poster_nasal_Tgfbr2_WT_2500_K2

SNED1 ATF7 HSPG2 THBD FBN1 FBN2 HMCN1 PKD1 LRP1 LTBP3 LTBP4

4.27e-0412285811facebase_RNAseq_e14.5_palate_poster_nasal_Tgfbr2_WT_2500_K2
CoexpressionAtlasdev gonad_e12.5_F_VasAssocMesStromOvary_Sma_k-means-cluster#2_top-relative-expression-ranked_500

FBN1 HMCN1 LRP1

4.35e-0454583gudmap_dev gonad_e12.5_F_VasAssocMesStromOvary_Sma_k2_500
CoexpressionAtlasdev gonad_e12.5_M_InterstitTestis_Sma_k-means-cluster#2_top-relative-expression-ranked_500

FBN1 HMCN1 LRP1 LTBP4

4.41e-04130584gudmap_dev gonad_e12.5_M_InterstitTestis_Sma_k2_500
CoexpressionAtlasEctoderm Differentiated Cells_vs_Pluripotent Stem Cells-Confounder_removed-fold2.0_adjp0.05

ATF7 CELSR1 FBN1 FBN2 MEGF6 TSPOAP1 PKD1 LRP2 LAMB1 LTBP4 AGRN FBN3

5.11e-0414665812PCBC_ratio_ECTO_vs_SC_cfr-2X-p05
CoexpressionAtlasdev gonad_e12.5_F_VasAssMesen_MafB_k-means-cluster#4_top-relative-expression-ranked_500

FBN1 FBN2 HMCN1 LRP1

6.82e-04146584gudmap_dev gonad_e12.5_F_VasAssMesen_MafB_k4_500
CoexpressionAtlasdev gonad_e13.5_M_DevVasTestis_Flk_k-means-cluster#4_top-relative-expression-ranked_1000

THBD HMCN1 LAMB1 LTBP4

7.18e-04148584gudmap_dev gonad_e13.5_M_gudmap_devVasTestis_Flk_k4_1000
CoexpressionAtlasdev gonad_e13.5_F_VascAssocMesenchStromOvary_MafB_k-means-cluster#2_top-relative-expression-ranked_1000

FBN1 FBN2 HMCN1 LRP1 LTBP4

7.79e-04265585gudmap_dev gonad_e13.5_F_VascAssocMesenchStromOvary_MafB_k2_1000
CoexpressionAtlasJC_hmvEC_top-relative-expression-ranked_1000_k-means-cluster#4

SNED1 HSPG2 EGFL7 NOTCH4 PEAR1 STAB1

1.08e-03428586JC_hmvEC_1000_K4
ToppCellfacs-Lung-nan|Lung / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

SNED1 HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP3 LTBP4

2.06e-10196598b05f77f3990b662682ffeaf0e4c2fb190e0a6e65
ToppCellfacs-Lung-nan-3m|Lung / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

SNED1 HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP3 LTBP4

2.06e-10196598787c6cd92035e0b1108c2c086c42a229016e476b
ToppCell10x3'2.3-week_17-19-Endothelial-stroma-sinusoidal_EC|week_17-19 / cell types per 3 fetal stages;per 3',per 5'

HSPG2 THBD HMCN1 LAMB1 EGFL7 NOTCH4 PEAR1 STAB1

2.15e-101975984e58bbf3ecb30b4c8199adcc04d2eb134d90de56
ToppCell5'-Parenchyma_lung-Mesenchymal-Mesenchymal_Myocytic-myocytic_fibroblast-Myofibroblasts-Myofibroblasts_L.2.3.2.2|5' / 5'-vs-3', Tissue groups, Lineages, Lineage subclass, Cell_type2, Cell_subtype2_L4.5

ITGBL1 FBN1 COMP HMCN1 LAMB1 ADAMTS13 LTBP4

4.34e-09181597b116c68393d8836bac080f81a8fcbeb52e0403e7
ToppCellfacs-Heart-LA-24m-Endothelial-endothelial_cell_of_endocardium|Heart / Tongue_Heart_Limb_Muscle_Aorta_Diaphragm - method, tissue, subtissue, age, lineage, cell ontology and free annotation

THBD CELSR1 COMP HMCN1 MEGF6 EGFL7 STAB1

5.44e-09187597d9943e65eedab73d141eae524e2411653a751705
ToppCellfacs-Heart-LA-24m-Endothelial-endocardial_cell|Heart / Tongue_Heart_Limb_Muscle_Aorta_Diaphragm - method, tissue, subtissue, age, lineage, cell ontology and free annotation

THBD CELSR1 COMP HMCN1 MEGF6 EGFL7 STAB1

5.44e-091875977b13c3b67d66f3afb410141d5471c9e78a4d8623
ToppCell3'-GW_trimst-2-LargeIntestine-Endothelial-blood_vessel_EC-Fetal_venous_EC|GW_trimst-2 / Celltypes from developing, pediatric, Crohn's, & adult GI tract

HSPG2 THBD FBN1 HMCN1 ACR EGFL7 AGRN

5.86e-09189597fccadf8efbef17b7f12291b069c71060a71b04e2
ToppCellfacs-Lung-nan-3m-Mesenchymal-Adventitial_Fibroblast|Lung / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP3 LTBP4

6.53e-09192597a2c31390da4962bda9a936470b0b68fa1f5d47d1
ToppCellPND28-Mesenchymal-Mesenchymal_structural-Fibroblastic-AF2-AF2_mature|PND28 / Age_group by Lineage, Lineage_subclass, Cell_type, subtypes-by-prolif

SNED1 HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP4

6.53e-0919259729bee88b45e23f16543ffc7cc361bc5da5d16a2b
ToppCellfacs-Lung-nan-3m-Mesenchymal-adventitial_cell|Lung / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP3 LTBP4

6.53e-09192597eeab1cef7c36ae824381952c5b2c982368c379fd
ToppCellfacs-Lung-3m-Mesenchymal-fibroblast-adventitial_fibroblast|3m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP3 LTBP4

6.53e-0919259732acd89617934016cd135d2cc797e8e79ae1b37f
ToppCellPND28-Mesenchymal-Mesenchymal_structural-Fibroblastic-AF2|PND28 / Age_group by Lineage, Lineage_subclass, Cell_type, subtypes-by-prolif

SNED1 HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP4

6.53e-09192597cdc652dbfabe41b324fd85c1ed933d29fb73a49f
ToppCell15-Trachea-Endothelial-Endothelial|Trachea / Age, Tissue, Lineage and Cell class

HSPG2 THBD FBN1 HMCN1 EGFL7 PEAR1 STAB1

6.77e-091935976ea0444fc3dc156997129387184e6418947f4b12
ToppCellfacs-Lung-nan-3m-Mesenchymal|Lung / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP3 LTBP4

6.77e-09193597d9c20a092b507c43fcf7ccb04073fecd27d1749c
ToppCell15-Trachea-Endothelial|Trachea / Age, Tissue, Lineage and Cell class

HSPG2 THBD FBN1 HMCN1 EGFL7 PEAR1 STAB1

6.77e-09193597b1ebf8df2d55e2938e5a495ea68b80c4ac216dc0
ToppCellfacs-Thymus-Thymus_Epithelium|Thymus / Spleen_Marrow_Thymus - method, tissue, subtissue, age, lineage, cell ontology and free annotation

THBD FBN1 HMCN1 LRP1 LRP2 LAMB1 LTBP4

7.53e-091965976bc1187dfc4860a4e09032d7ea87ba3d9fe9f363
ToppCellfacs-Thymus-Thymus_Epithelium-18m|Thymus / Spleen_Marrow_Thymus - method, tissue, subtissue, age, lineage, cell ontology and free annotation

THBD FBN1 HMCN1 LRP1 LRP2 LAMB1 LTBP4

7.53e-09196597c8c89e469402e11aa2a9561e859b6fd1fb66c39b
ToppCellTracheal-10x5prime-Stromal-Peri/Epineurial_|10x5prime / Cell types per location group and 10X technology with lineage, and cell group designations

SNED1 FBN1 FBN2 LRP1 LAMB1 LTBP4 PEAR1

7.80e-091975972cb1f557ce1400398975de94638126b4522567f3
ToppCellFibroblasts|World / Immune cells in Rheumatoid Arthritis Joint Synovial Tissues

SNED1 HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP3

8.37e-0919959740de6d4a31cf22efa2864f79e4ec8e2b7bfc9d4a
ToppCell10x_3'_v2v3-Non-neoplastic-Endothelial-Endothelial_mature-Endo_arterial|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

HSPG2 HMCN1 LAMB1 EGFL7 AGRN NOTCH4 PEAR1

8.37e-091995970602e2b2aa56d106da63bd342a38bef437b4d496
ToppCell10x_3'_v2v3-Non-neoplastic-Endothelial-Endothelial_mature-Endo_arterial-F|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

HSPG2 HMCN1 LAMB1 EGFL7 AGRN NOTCH4 PEAR1

8.37e-09199597463ba77dc4c85eebb343f29a42c7ac889b0497c9
ToppCellTracheal-10x5prime-Stromal-Fibroblastic-Fibro_peribronchial|10x5prime / Cell types per location group and 10X technology with lineage, and cell group designations

ITGBL1 FBN1 COMP HMCN1 LRP1 LAMB1 LTBP4

8.66e-092005978ab0051544ea32eb8b3f7f8ba7582deaf8bf26c0
ToppCell3'-Parenchyma_lung-Mesenchymal-Mesenchymal_Myocytic-myocytic_fibroblast-Myofibroblasts-Myofibroblasts_L.2.3.2.2|3' / 5'-vs-3', Tissue groups, Lineages, Lineage subclass, Cell_type2, Cell_subtype2_L4.5

ITGBL1 FBN1 COMP HMCN1 LAMB1 LTBP4

1.21e-071755961799a7be623dc3bf53ba580a7c47d2619969d708
ToppCelldroplet-Heart-HEART_(LV+RV_ONLY)-30m-Endothelial-endocardial_cell|Heart / Tongue_Heart_Limb_Muscle_Aorta_Diaphragm - method, tissue, subtissue, age, lineage, cell ontology and free annotation

THBD CELSR1 HMCN1 MEGF6 EGFL7 STAB1

1.47e-07181596cef034030e6b029a49ae56be37ea1fac1a5c350e
ToppCellmetastatic_Brain-Fibroblasts-Myofibroblasts|metastatic_Brain / Location, Cell class and cell subclass

ITGBL1 FBN1 FBN2 COMP HMCN1 LAMB1

1.47e-07181596bd0b5f74f9c81ec0f1592710774a4fdf33d9d5a9
ToppCelldroplet-Liver-Npc-21m-Endothelial|Liver / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 EGFL7 LTBP4 NOTCH4 PEAR1 STAB1

1.52e-07182596dc55de945c6f78f32eb3a1b3520835eb8417e068
ToppCelldroplet-Liver-Npc-21m-Endothelial-endothelial_cell_of_hepatic_sinusoid|Liver / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 EGFL7 LTBP4 NOTCH4 PEAR1 STAB1

1.52e-07182596010a7364da46101cb5068891fd7bc712ea8f13bd
ToppCelldroplet-Liver-Npc-21m-Endothelial-endothelial_cell_of_hepatic_sinusoid|Liver / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 EGFL7 LTBP4 NOTCH4 PEAR1 STAB1

1.52e-07182596b1ec2015aad1181eac1bbf8d48ad6f2f7ed24a01
ToppCellBasal|World / shred by cell class for mouse tongue

CELSR1 MEGF6 LAMB1 LAMB3 LTBP4 AGRN

1.57e-07183596c6729a207526ff4aa48176207b9353176f631fea
ToppCelldroplet-Heart-4Chambers-18m-Endothelial-endocardial_cell|Heart / Tongue_Heart_Limb_Muscle_Aorta_Diaphragm - method, tissue, subtissue, age, lineage, cell ontology and free annotation

CELSR1 COMP HMCN1 MEGF6 AGRN STAB1

1.57e-071835966c4a09c02e30e1f24dde39f8cb8c5b453826ee2e
ToppCelldroplet-Liver-HEPATOCYTES-1m-Endothelial-nan|Liver / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 ACR EGFL7 LTBP4 PEAR1 STAB1

1.68e-07185596742350093d90f96735dc73e3360cdd749bae63fd
ToppCelldroplet-Kidney-KIDNEY-1m-Mesenchymal-Stroma____fibroblast|Kidney / Skin_Bladder_Kidney_Mammary_Gland - method, tissue, subtissue, age, lineage, cell ontology and free annotation

ITGBL1 FBN1 FBN2 HMCN1 LRP1 LTBP4

1.68e-07185596785c55d39909fac74415f24427979691e7e694e6
ToppCelldroplet-Kidney-KIDNEY-1m-Mesenchymal|Kidney / Skin_Bladder_Kidney_Mammary_Gland - method, tissue, subtissue, age, lineage, cell ontology and free annotation

ITGBL1 FBN1 FBN2 HMCN1 LRP1 LTBP4

1.68e-0718559697a1dcacbc48dc3f41c26fbb59af35c935f894d4
ToppCelldroplet-Kidney-KIDNEY-1m-Mesenchymal-fibroblast|Kidney / Skin_Bladder_Kidney_Mammary_Gland - method, tissue, subtissue, age, lineage, cell ontology and free annotation

ITGBL1 FBN1 FBN2 HMCN1 LRP1 LTBP4

1.73e-0718659694d577dbb6bfacf50632e1fe8af041b35a1e6b23
ToppCelldroplet-Pancreas-Exocrine-24m-Endothelial|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD HMCN1 EGFL7 LTBP4 NOTCH4

1.78e-07187596a178b1fed80a0bf83aedb6262493ee17374734b5
ToppCelldroplet-Pancreas-Exocrine-18m-Mesenchymal-pancreatic_stellate_cell|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

ITGBL1 FBN1 FBN2 LRP2 LAMB1 LTBP4

1.78e-071875964e553721fa5598cb211f44e3226280b7e6885484
ToppCelldroplet-Pancreas-Exocrine-18m-Mesenchymal|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

ITGBL1 FBN1 FBN2 LRP2 LAMB1 LTBP4

1.78e-07187596d36e7fc6125e7a4310499365022d38f34b757a73
ToppCelldroplet-Pancreas-Exocrine-18m-Mesenchymal-pancreatic_stellate_cell|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

ITGBL1 FBN1 FBN2 LRP2 LAMB1 LTBP4

1.78e-07187596827eae63fabf6892a82ce7779b5f395958d3d628
ToppCelldroplet-Pancreas-Exocrine-24m-Endothelial-endothelial_cell|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD HMCN1 EGFL7 LTBP4 NOTCH4

1.78e-07187596e60cbccf5842f25123fd34b9475759b7424b32e9
ToppCelldroplet-Pancreas-Exocrine-24m-Endothelial-endothelial_cell|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD HMCN1 EGFL7 LTBP4 NOTCH4

1.78e-071875962b8eda2812be0be68a6f01aa4038925d3d5b1e65
ToppCelldroplet-Lung-nan-18m-Endothelial-Lymphatic_endothelial_cell|Lung / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

SNED1 CELSR1 ACR LTBP4 PEAR1 STAB1

1.84e-07188596a6ed43fdd42d681c9fbb2fb368947ab7e41d8d7c
ToppCellkidney_cells-Renal_AKI_(acute_kidney_injury)-Endothelial-lymphatic_endothelial_cell|Renal_AKI_(acute_kidney_injury) / Celltypes from Cells and Nuclei per compartment and clinical group

HSPG2 THBD FBN1 MEGF6 EGFL7 PEAR1

1.84e-0718859626915db8863f4115b46a81982e187322e21600fd
ToppCelldroplet-Lung-nan-18m-Endothelial-endothelial_cell_of_lymphatic_vessel|Lung / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

SNED1 CELSR1 ACR LTBP4 PEAR1 STAB1

1.84e-0718859654550313db78b3b5b572fa1e67092c8f6f33aab5
ToppCellkidney_cells-Renal_AKI_(acute_kidney_injury)-Endothelial-lymphatic_endothelial_cell-lymphatic_endothelial_cell_of_renal_cortex|Renal_AKI_(acute_kidney_injury) / Celltypes from Cells and Nuclei per compartment and clinical group

HSPG2 THBD FBN1 MEGF6 EGFL7 PEAR1

1.84e-071885963f76c0f912f8f023ea425be7f43593b3d7f967e3
ToppCellkidney_cells-Renal_AKI_(acute_kidney_injury)-Endothelial-lymphatic_endothelial_cell-lymphatic_endothelial_cell_of_renal_cortex-lymphatic_endothelial_cell_of_renal_cortex|Renal_AKI_(acute_kidney_injury) / Celltypes from Cells and Nuclei per compartment and clinical group

HSPG2 THBD FBN1 MEGF6 EGFL7 PEAR1

1.84e-0718859661ee7b152745164293d8a44ef91ee2393efbdca5
ToppCellrenal_cortex_nuclei-Renal_AKI_(acute_kidney_injury)-Endothelial-blood_vessel_endothelial_cell_of_kidney-arteriolar_vasa-recta_endothelial-Afferent_/_Efferent_Arteriole_Endothelial_Cell|Renal_AKI_(acute_kidney_injury) / Celltypes from Cells and Nuclei per compartment and clinical group

HSPG2 THBD FBN1 EGFL7 LTBP4 NOTCH4

1.90e-0718959612b6f1c3bf526b90e112374bf937701f645c5780
ToppCellLPS_only-Endothelial-Endothelial-Artery|LPS_only / V2 postpublication: Rhesus Genome Updated; Treatment groups by lineage, cell_type_level1, cell_type_level2

HSPG2 FBN1 HMCN1 EGFL7 LTBP4 NOTCH4

1.90e-07189596b028466fcd36fdeceec752e55a24286a1cd62ae4
ToppCelldroplet-Pancreas-PANCREAS-30m-Endothelial-endothelial_cell|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD HMCN1 LAMB1 EGFL7 LTBP4

1.96e-071905969d5242759546be0089981ef1877e4ed5f81face5
ToppCelldroplet-Heart-nan-24m-Endothelial-endocardial_cell|Heart / Tongue_Heart_Limb_Muscle_Aorta_Diaphragm - method, tissue, subtissue, age, lineage, cell ontology and free annotation

CELSR1 COMP HMCN1 MEGF6 EGFL7 STAB1

1.96e-071905967068754c29f63a331e2b6c54715f3b26f37ad32b
ToppCellfacs-Pancreas-Exocrine-3m-Endothelial|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD HMCN1 EGFL7 LTBP4 NOTCH4

1.96e-07190596b7fc451e160e31dc898b122de844b501f587db67
ToppCell21-Trachea-Endothelial|Trachea / Age, Tissue, Lineage and Cell class

HSPG2 THBD EGFL7 NOTCH4 PEAR1 STAB1

1.96e-07190596bce09634acbc2cfd53666328e8aed8bf8835f845
ToppCelldroplet-Lung-21m-Endothelial-lymphatic_endothelial-lymphatic_endothelial_cell-lymphatic_endothelial_cell|21m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

HSPG2 CELSR1 COMP LTBP4 PEAR1 STAB1

1.96e-07190596f50b9814a1beac67dc042a8c27dfd085ceeda3a6
ToppCelldroplet-Lung-21m-Endothelial-lymphatic_endothelial-lymphatic_endothelial_cell|21m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

HSPG2 CELSR1 COMP LTBP4 PEAR1 STAB1

1.96e-07190596a22a510b4a257eb0eaf09c7ae7978d3d2f07a58c
ToppCellfacs-Pancreas-Exocrine-3m-Endothelial-endothelial_cell|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD HMCN1 EGFL7 LTBP4 NOTCH4

1.96e-0719059683cc851fb9f644b17a8ebf4d99a646003769a22f
ToppCelldroplet-Lung-21m-Endothelial-lymphatic_endothelial|21m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

HSPG2 CELSR1 COMP LTBP4 PEAR1 STAB1

1.96e-0719059657c136bf6d7feafb4a220877bed0cc8fdf314db2
ToppCellfacs-Pancreas-Exocrine-3m-Endothelial-nan|Pancreas / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD HMCN1 EGFL7 LTBP4 NOTCH4

1.96e-071905965f440d4b334d66d419c03bd828f7d93f16c1ce67
ToppCell21-Trachea-Endothelial-Endothelial|Trachea / Age, Tissue, Lineage and Cell class

HSPG2 THBD EGFL7 NOTCH4 PEAR1 STAB1

1.96e-0719059608437396a98ca9526f69c3a74bbf2929f3c68b8e
ToppCell10x5'v1-week_12-13-Endothelial-stroma-tip_EC|week_12-13 / cell types per 3 fetal stages;per 3',per 5'

HSPG2 THBD FBN1 LAMB1 AGRN NOTCH4

2.02e-07191596cf1a67b7c0d5c0dc5d4d59faf9d9b1a3a1fb00e0
ToppCell5'-Parenchyma_lung-Mesenchymal-Fibroblastic-fibroblastic_type_2-Peribronchial_fibroblasts|5' / 5'-vs-3', Tissue groups, Lineages, Lineage subclass, Cell_type2, Cell_subtype2_L4.5

ITGBL1 FBN1 COMP HMCN1 LAMB1 LTBP4

2.02e-071915960fae1c2ef9f83ac7721d0a9d69455bf97eed9257
ToppCellmetastatic_Lymph_Node-Fibroblasts-Myofibroblasts|metastatic_Lymph_Node / Location, Cell class and cell subclass

HSPG2 ITGBL1 FBN1 COMP HMCN1 LAMB1

2.02e-07191596aa43b472bc8362f79ae63f09f1ca764718bbf22c
ToppCelldroplet-Lung-1m-Endothelial-venous_endothelial|1m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

THBD HMCN1 MEGF6 ACR EGFL7 LTBP4

2.08e-071925961990dc8a81594018a5bf596be99d0b5f0af0f58f
ToppCellfacs-Lung-3m-Mesenchymal-fibroblast-adventitial_fibroblast-adventitial_fibroblast_l1|3m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

HSPG2 ITGBL1 FBN1 LRP1 LAMB1 LTBP4

2.08e-071925967b48df661f61ce494bf6f0b9a74b0422e29c24bf
ToppCelldroplet-Lung-1m-Endothelial-venous_endothelial-vein_endothelial_cell-vein_endothelial_cell|1m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

THBD HMCN1 MEGF6 ACR EGFL7 LTBP4

2.08e-07192596845cc9c18b4436b07dd3ce7980052683937546d2
ToppCelldroplet-Lung-1m-Endothelial-venous_endothelial-vein_endothelial_cell|1m / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

THBD HMCN1 MEGF6 ACR EGFL7 LTBP4

2.08e-07192596c72a082c93a8825adbfef37f889ba3a7052f201b
ToppCelldroplet-Liver-HEPATOCYTES-1m-Endothelial-endothelial_cell_of_hepatic_sinusoid|Liver / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 ACR EGFL7 LTBP4 PEAR1 STAB1

2.15e-071935964a8c97ff2dffc5c06351d1cb107e21e58250aa55
ToppCelldroplet-Liver-HEPATOCYTES-1m-Endothelial|Liver / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 ACR EGFL7 LTBP4 PEAR1 STAB1

2.15e-07193596d5f6d6e2c36d4e80af4d39cdfc0b18df295a587b
ToppCellCOVID-19-Fibroblasts-Other_FB|COVID-19 / group, cell type (main and fine annotations)

SNED1 ITGBL1 FBN1 COMP HMCN1 LAMB1

2.15e-07193596e6b75be08e33c1de079fb5c02f0b4468128b369c
ToppCellrenal_cortex_nuclei-Hypertensive_with+without-CKD-Endothelial-blood_vessel_endothelial_cell_of_kidney-arteriolar_vasa-recta_endothelial-Afferent_/_Efferent_Arteriole_Endothelial_Cell|Hypertensive_with+without-CKD / Celltypes from Cells and Nuclei per compartment and clinical group

HSPG2 THBD FBN1 EGFL7 LTBP4 NOTCH4

2.15e-071935960b328f725f6feba263783eaca60c142e80df90f3
ToppCelldroplet-Liver-LIVER-NPC-1m-Endothelial-nan|Liver / Large_Intestine_Pancreas_Liver - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 THBD EGFL7 LTBP4 PEAR1 STAB1

2.28e-07195596126f46dd15dddcf5701144718bb8ba1ce84b2d1d
ToppCell5'-Parenchyma_lung-Mesenchymal-Fibroblastic-fibroblastic_type_2-Alveolar_fibroblasts-Alveolar_fibroblasts_L.2.1.1.0|5' / 5'-vs-3', Tissue groups, Lineages, Lineage subclass, Cell_type2, Cell_subtype2_L4.5

ITGBL1 FBN1 HMCN1 LRP1 LAMB1 LTBP4

2.28e-07195596df409f94f4e83be89f7a608058ee07ce3ce3a149
ToppCell5'-Parenchyma_lung-Mesenchymal-Fibroblastic-fibroblastic_type_2-Alveolar_fibroblasts|5' / 5'-vs-3', Tissue groups, Lineages, Lineage subclass, Cell_type2, Cell_subtype2_L4.5

ITGBL1 FBN1 HMCN1 LRP1 LAMB1 LTBP4

2.28e-071955964243190ad291d56694e2155954dbaa879c9d3844
ToppCell3'-Parenchyma_lung-Mesenchymal-Fibroblastic-fibroblastic_type_2-Peribronchial_fibroblasts|3' / 5'-vs-3', Tissue groups, Lineages, Lineage subclass, Cell_type2, Cell_subtype2_L4.5

ITGBL1 FBN1 COMP LRP1 LAMB1 LTBP4

2.28e-071955961236dc60288c7dd91868e86e9174a2dacd3b11b3
ToppCellfacs-Lung-3m|Lung / method, tissue, age, lineage, sublineage, cell ontologies, cell type and subtype

SNED1 HSPG2 FBN1 LAMB1 LTBP3 LTBP4

2.28e-07195596c4648c0332c3826776f9ad3f5f803dbac2b4c0c0
ToppCellCOVID-19-kidney-VWF+PLVAP+VCAM1+EC|kidney / Disease (COVID-19 only), tissue and cell type

HSPG2 THBD FBN1 EGFL7 NOTCH4 STAB1

2.35e-07196596ac2c4a325efa8497a755cd31fb6a9d94d8e3bf42
ToppCell5'-Parenchyma_lung-Mesenchymal-Fibroblastic-fibroblastic_type_2|5' / 5'-vs-3', Tissue groups, Lineages, Lineage subclass, Cell_type2, Cell_subtype2_L4.5

ITGBL1 FBN1 HMCN1 LRP1 LAMB1 LTBP4

2.35e-0719659642e9828222a9663525d571633e8a454c30bfa7f8
ToppCellmetastatic_Lymph_Node-Fibroblasts|metastatic_Lymph_Node / Location, Cell class and cell subclass

HSPG2 ITGBL1 FBN1 COMP HMCN1 LAMB1

2.35e-07196596275e153347caf94edc0c50021bbab49c8696fecb
ToppCell10x_3'_v2v3-Non-neoplastic-Endothelial-Endothelial_immature|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

SNED1 HSPG2 HMCN1 EGFL7 NOTCH4 PEAR1

2.43e-0719759662c0a90869431e582bb7bb329e0b0cc59123d3d1
ToppCell10x_3'_v2v3-Non-neoplastic-Endothelial-Endothelial_immature-Tip-like-A|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

SNED1 HSPG2 HMCN1 EGFL7 NOTCH4 PEAR1

2.43e-071975969e948b2e0f7e426f1e6f95bbbf4282fbddc2b99d
ToppCell10x_3'_v2v3-Non-neoplastic-Endothelial-Endothelial_immature-Tip-like|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

SNED1 HSPG2 HMCN1 EGFL7 NOTCH4 PEAR1

2.43e-0719759616f0eb047df9d702518f82ee99c6e7dc1350b2fb
ToppCellCOVID-19-lung-Fibroblast|COVID-19 / Disease (COVID-19 only), tissue and cell type

SNED1 ITGBL1 FBN1 HMCN1 LRP1 LAMB1

2.50e-071985963ec01a55ade5e1627258cc3cfebb2c3207a4cb43
ToppCellSmart-start-Cell-Wel_seq-Non-neoplastic-Endothelial-Endothelial_immature-Tip-like-A|Smart-start-Cell-Wel_seq / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

HSPG2 HMCN1 LAMB1 EGFL7 NOTCH4 PEAR1

2.50e-0719859672e8b9cccb7b0a2ea9d415218fff4fa2f09728f4
ToppCellSmart-start-Cell-Wel_seq-Non-neoplastic-Endothelial|Smart-start-Cell-Wel_seq / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

HSPG2 HMCN1 LAMB1 EGFL7 NOTCH4 PEAR1

2.50e-07198596e1fa02184ce93c4f8aa5cf04b70949cd4c425ff0
ToppCellfacs-Trachea-nan-3m-Mesenchymal-fibroblast|Trachea / Lung_Trachea - method, tissue, subtissue, age, lineage, cell ontology and free annotation

HSPG2 FBN1 LRP1 LAMB1 LTBP3 LTBP4

2.50e-071985960dc7d59a07428a7b7e8bdc81f0e2417dd4ce3cf2
ToppCellwk_20-22-Endothelial-Blood_vessel_endothelial-Venous_endo|wk_20-22 / Celltypes from embryonic and fetal-stage human lung

HSPG2 THBD FBN1 HMCN1 EGFL7 AGRN

2.57e-0719959670e05d7c0c68c28754ce0e72434b205aed6287ae
ToppCellSmart-start-Cell-Wel_seq-Non-neoplastic-Endothelial-Endothelial_immature|Smart-start-Cell-Wel_seq / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

HSPG2 HMCN1 LAMB1 EGFL7 NOTCH4 PEAR1

2.57e-071995969c40b3ee39860e9d8edafd007daec11abdd95435
ToppCell10x_3'_v2v3-Non-neoplastic-Vascular-Mural_cell-Scavenging_endothelial|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

SNED1 HSPG2 HMCN1 EGFL7 NOTCH4 PEAR1

2.57e-07199596d95d78b2ebc9a20532466e4d4be579b4faf6776f
ToppCellkidney_cells-Renal_AKI_(acute_kidney_injury)-Endothelial-blood_vessel_endothelial_cell_of_kidney-arteriolar_vasa-recta_endothelial|Renal_AKI_(acute_kidney_injury) / Celltypes from Cells and Nuclei per compartment and clinical group

HSPG2 THBD EGFL7 LTBP4 NOTCH4 STAB1

2.57e-07199596f35e9c05d0a0339ff691b38564da7aad8e9218aa
ToppCell10x_3'_v2v3-Non-neoplastic-Vascular-Mural_cell-Scavenging_endothelial-F|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

SNED1 HSPG2 HMCN1 EGFL7 NOTCH4 PEAR1

2.57e-07199596cdcfca94baba66e213cc3ffb0cfb4c75d6ab44ec
ToppCellSmart-start-Cell-Wel_seq-Non-neoplastic-Endothelial-Endothelial_immature-Tip-like|Smart-start-Cell-Wel_seq / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

HSPG2 HMCN1 LAMB1 EGFL7 NOTCH4 PEAR1

2.57e-0719959672b34bce8157abe389e95cd3ed8ba578dce0cbf6
ToppCellLPS_anti-TNF-Mesenchymal_myocytic-Myofibroblastic-MatrixFB_->_Myofibroblast|LPS_anti-TNF / Treatment groups by lineage, cell group, cell type

FBN1 LRP1 LAMB1 ADAMTS13 LTBP3 LTBP4

2.57e-0719959638cfd367ee8c074c11ba54edeb7a001e375e2687
ToppCellBronchial-10x5prime-Stromal-Fibroblastic-Fibro_peribronchial|10x5prime / Cell types per location group and 10X technology with lineage, and cell group designations

ITGBL1 FBN1 COMP HMCN1 LAMB1 LTBP4

2.57e-07199596e1f1950d6f840485e263b83dc81b98910be3ae7a
ToppCell10x_3'_v2v3-Non-neoplastic-Endothelial-Endothelial_immature-Tip-like-G|10x_3'_v2v3 / Platform, Oncotype, Lineage, Cell_class, celltype (level4), mutation group

HSPG2 HMCN1 EGFL7 AGRN NOTCH4 PEAR1

2.57e-071995961295f34a350bf48987e2fad411aaac3630efd3f1
ToppCellBiopsy_Other_PF-Mesenchymal-Myofibroblasts|Biopsy_Other_PF / Sample group, Lineage and Cell type

ITGBL1 FBN1 COMP HMCN1 LAMB1 LTBP4

2.65e-07200596e504570fd7eec1524c401b1cfa9d10822d80d994
ToppCell10x5'v1-week_14-16-Endothelial-stroma|week_14-16 / cell types per 3 fetal stages;per 3',per 5'

HSPG2 THBD LAMB1 EGFL7 NOTCH4 STAB1

2.65e-072005962488aa12970a43a5af352e2c36c73884d73a1cc5
ToppCellTracheal-NucSeq-Stromal-Fibroblastic-Fibro_perichondrial|NucSeq / Cell types per location group and 10X technology with lineage, and cell group designations

SNED1 ITGBL1 FBN1 COMP LRP1 LAMB1

2.65e-07200596a4ec0e80f5422b91b85264a9bb74568dd577e285
ToppCellBronchial-10x5prime-Endothelial-Endothelia_vascular-VE_pulmonary_arterial|10x5prime / Cell types per location group and 10X technology with lineage, and cell group designations

HSPG2 THBD HMCN1 EGFL7 LTBP4 NOTCH4

2.65e-072005967547d6339f9380d031cfd2cce21ac9a12491e085
ToppCellkidney_cells-Hypertensive_with+without-CKD-Endothelial-blood_vessel_endothelial_cell_of_kidney-capillary-immature_endothelial_cell-Peritubular_Capilary_Endothelial_Cell_|Hypertensive_with+without-CKD / Celltypes from Cells and Nuclei per compartment and clinical group

SNED1 HSPG2 THBD EGFL7 NOTCH4 STAB1

2.65e-07200596b1be27d134a8633e3e7862c6a0d7be2001d387f0
ToppCellLPS_IL1RA_TNF-Mesenchymal_myocytic-Myofibroblastic-MatrixFB_->_Myofibroblast|LPS_IL1RA_TNF / Treatment groups by lineage, cell group, cell type

FBN1 LRP1 LAMB1 ADAMTS13 LTBP3 LTBP4

2.65e-0720059609537dc25f8b8b4654a7c183827ee1522a41a4e0
ToppCellcellseq2-Mesenchymal-Fibroblastic-Fibroblastic_1-AF2|cellseq2 / Celltype signatures by Technology, Lineage, Lineage_subclass, Celltype_group, Cell_type2

SNED1 FBN1 HMCN1 LRP1 LAMB1 LTBP4

2.65e-0720059644317fbf4d1480a37b50ab2777bf1a3e4fc0c05f
ToppCellTracheal-NucSeq-Stromal-Fibroblastic|NucSeq / Cell types per location group and 10X technology with lineage, and cell group designations

SNED1 ITGBL1 FBN1 HMCN1 LRP1 LAMB1

2.65e-07200596b4ccffdd79526c85e5273d27b668dbddcddba1ee
ComputationalAdhesion molecules.

DGCR2 ITGBL1 FBN1 FBN2 COMP LAMB1 LAMB3

4.27e-07141377MODULE_122
ComputationalMetal / Ca ion binding.

THBD FBN1 FBN2 COMP LRP1

8.53e-05133375MODULE_324
ComputationalImmune / stress response genes.

HSPG2 COMP ACR PKD1 LRP1 TFF1 STAB1

2.82e-04383377MODULE_33
ComputationalGenes upregulated in subsets of cells of a given type within various tumors

ITGBL1 FBN1 COMP

6.58e-0450373GAVISH_3CA_METAPROGRAM_FIBROBLASTS_CAF_1
ComputationalGenes upregulated in subsets of cells of a given type within various tumors

HSPG2 EGFL7 NOTCH4

6.58e-0450373GAVISH_3CA_METAPROGRAM_ENDOTHELIAL_ENDO_3
Drugfuniferine N-oxide

FBN1 FBN2 LTBP3 LTBP4 AGRN

1.72e-0749595CID000191631
DrugVerteporfin [129497-78-5]; Down 200; 2.8uM; MCF7; HT_HG-U133A

ATRN DGCR2 THBD TMEM131L LAMB1 AGRN

3.76e-061615963556_DN
Diseaseconnective tissue disease (implicated_via_orthology)

FBN1 FBN2 FBN3

7.21e-093583DOID:65 (implicated_via_orthology)
DiseaseCongenital Thrombotic Thrombocytopenic Purpura

THBD ADAMTS13

2.27e-054582C1268935
DiseaseFamilial Thrombotic Thrombocytopenic Purpura

THBD ADAMTS13

2.27e-054582C1956258
Diseasescoliosis (is_implicated_in)

FBN1 FBN2

2.27e-054582DOID:0060249 (is_implicated_in)
DiseasePurpura, Thrombotic Thrombocytopenic

THBD ADAMTS13

2.27e-054582C0034155
DiseaseGeleophysic dysplasia

FBN1 LTBP3

3.78e-055582C3489726
DiseaseAcromicric Dysplasia

FBN1 LTBP3

3.78e-055582C0265287
Diseasesystemic lupus erythematosus (is_marker_for)

THBD ADAMTS13 DNMT1

1.10e-0447583DOID:9074 (is_marker_for)
DiseaseFamilial thoracic aortic aneurysm and aortic dissection

FBN1 FBN2 PKD1

1.57e-0453583C4707243
Diseaseaortic aneurysm

FBN1 LRP1

1.69e-0410582EFO_0001666
Diseasecortical thickness

HSPG2 ERBB3 CELSR1 FBN1 FBN2 PKD1 LRP1 STAT1 STAB1

3.02e-041113589EFO_0004840
DiseaseSchizophrenia

DGCR2 ERBB3 MCHR1 LRP1 LRP2 ZDHHC8 NOTCH4 DNMT1

3.18e-04883588C0036341
Diseaselung non-small cell carcinoma (is_marker_for)

THBD ERBB3 LAMB3 DNMT1

3.46e-04169584DOID:3908 (is_marker_for)
Diseaseanorexia nervosa

ERBB3 CELSR3 LRP2

3.59e-0470583MONDO_0005351
Diseaseglycerate measurement

HMCN1 AGRN

3.92e-0415582EFO_0021029
Diseaseendoplasmic reticulum resident protein 29 measurement

EGFL7 NOTCH4

4.48e-0416582EFO_0020346
DiseaseDisproportionate short stature

HSPG2 FBN1 COMP

4.75e-0477583C0878659
Diseaseosteochondrodysplasia (is_implicated_in)

HSPG2 COMP

6.36e-0419582DOID:2256 (is_implicated_in)
DiseaseOsteoarthritis of hip

COMP LTBP3

7.05e-0420582C0029410
DiseaseStomach Carcinoma

ERBB3 TFF1

7.78e-0421582C0699791
DiseaseCarcinoma, Pancreatic Ductal

NOTCH4 DNMT1

1.02e-0324582C0887833
Diseasesystemic scleroderma (is_implicated_in)

FBN1 NOTCH4

1.02e-0324582DOID:418 (is_implicated_in)
Diseasemonocyte count

ATRN ATF7 TSPOAP1 PKD1 TMEM131L EGFL7 NOTCH4 DNMT1 PEAR1

1.03e-031320589EFO_0005091
Diseasemyeloperoxidase measurement

TSPOAP1 NOTCH4

1.20e-0326582EFO_0005243
Diseaseurinary bladder cancer (is_marker_for)

ERBB3 TFF1 DNMT1

1.24e-03107583DOID:11054 (is_marker_for)
Diseasechronic obstructive pulmonary disease (biomarker_via_orthology)

ERBB3 STAT1

1.39e-0328582DOID:3083 (biomarker_via_orthology)
Diseaseaortic measurement

FBN1 HMCN1 LRP1 LTBP4

1.51e-03251584EFO_0020865
Diseasespontaneous coronary artery dissection

FBN1 LRP1

1.70e-0331582EFO_0010820

Protein segments in the cluster

PeptideGeneStartEntry
GPGPGQCLSCRNYSR

ERBB3

511

P21860
ACGAAICQPPCRNGG

EGFL7

101

Q9UHF1
CGGPPCQGFSGMNRF

DNMT1

1221

P26358
GRQCNREACGPAGRT

ADGRB1

306

O14514
DGPCGLRFRQNPQGG

ACR

26

P10323
RGSFQCGPCQPGFVG

COMP

201

P49747
NLEAGRFHCQCPPGR

AGRN

1566

O00468
PFVCNAPGCGQRFTN

ATF7

6

P17544
PGVIGRQCNRCDNPF

CELSR1

2026

Q9NYQ6
FPGVCPNGRCVNTAG

FBN3

876

Q75N90
CHVVNGQGPACRAPG

ATXN7L2

126

Q5T6C5
CNNPRPAFGGRACVG

ADAMTS13

411

Q76LX8
GPQEAACRNGHCIPR

HSPG2

286

P98160
CLPGFSGPRCQQGSG

HSPG2

4166

P98160
GLGCDSGQPRRPGQC

TSPOAP1

1366

O95153
AGRGASCQGCPNQRL

NUBP1

16

P53384
QGNQPQCRCLPGFLG

LRP1

4286

Q07954
CDRPCVNGGRCNPGT

ATRN

101

O75882
ACFFPGRCSGGQQPL

HPS5

221

Q9UPZ3
ENGNCVCAPGFRGPS

PEAR1

591

Q5VY43
RGCRPCQCNGHGDPR

MEGF8

1206

Q7Z7M0
RTCNRCAPGTFGFGP

LAMB1

801

P07942
RPGQFRCANGRCIPQ

LRP2

3636

P98164
GGPGPVQRRCQRENC

OTUD7A

881

Q8TE49
TRCNVQACPGGPQRA

HMCN1

4861

Q96RW7
RAGGPPQVAGAQAAC

CENPH

21

Q9H3R5
ESGCLNGGRCVAPNR

FBN1

151

P35555
PELRCNPGQFACRSG

DGCR2

26

P98153
RPGGAVCECPGGFQL

LTBP3

1231

Q9NS15
PNCGACAPGQGGRRW

MCHR1

31

Q99705
RCVCGPGFRAGPRAA

LTBP4

611

Q8N2S1
RPGLTGPRCDQCQRG

LAMB3

556

Q13751
NGECRGNGFRAKPPG

FIGNL2

301

A6NMB9
ENGCQNGGRCIGPNR

FBN2

181

P35556
SNPCRNGGACARREG

CELSR3

1441

Q9NYQ7
TDAPNGGFRCQCPAG

CELSR3

1491

Q9NYQ7
QCPAGGAFEGPRCEV

CELSR3

1501

Q9NYQ7
QPPGAALCHGRGRCD

ITGBL1

56

O95965
PGVGWAQRCGQGACR

CTU2

436

Q2VPK5
GFRPGNFSCVSACGP

KRT83

11

P78385
PAPGAACRVNCSGRG

PKD1

41

P98161
PGFVGSRCQDVCPAG

MEGF6

806

O75095
PGRAGVRCERGCPQN

MEGF6

1281

O75095
GAPRCQCPAGAALQA

THBD

261

P07204
RRQQSACIGGPPNAC

STAT1

241

P42224
AGCPAGRLYRECQPG

SSPOP

3696

A2VEC9
RTCEGGPGVAPCQAQ

SSPOP

4791

A2VEC9
GCVCQPGHFRSQAGP

SSPOP

4966

A2VEC9
FQVLLPCCRPGGAQG

TMEM131L

26

A2VDJ0
VPCELCGQRGPQGRG

SYNE4

271

Q8N205
CAQRAADAAGPGCPR

RNF169

91

Q8NCN4
CRQRGDAGSPRGCPL

MESP1

151

Q9BRJ9
GSFQCLCPVGQEGPR

NOTCH4

216

Q99466
NSFRCQCPAGFGGPT

SNED1

331

Q8TER0
CTVAPRERQNCGFPG

TFF1

31

P04155
QNGGRSSAQPCPRCI

C10orf143

81

A0A1B0GUT2
ARGERPGPACQLCGG

ZNF513

111

Q8N8E2
GGQGRRPFKCPLEGC

ZXDC

201

Q2QGD7
AGRQPHRCPSCGAAF

ZNF574

631

Q6ZN55
AVGGGQRVCTCPPGF

STAB1

966

Q9NY15
CSNPAPRHGGRICVG

SEMA5B

691

Q9P283
RGGVNPFTRGCCGNV

ZDHHC8

226

Q9ULC8
RLQGQGRAHGGPCCR

PSPN

111

O60542
GERPFQCPFEGCGRS

ZNF76

251

P36508
QGGVYACPQCRGPFR

TRIM58

51

Q8NG06