Lysosomal cobalamin transporter ABCD4 (EC 7.6.2.8) (ATP-binding cassette sub-family D member 4) (PMP70-related protein) (P70R) (Peroxisomal membrane protein 1-like) (PXMP1-L) (Peroxisomal membrane protein 69) (PMP69)
1_MAVAG 6_ PAPGA 11_ GARPR 16_ LDLQF 21_ LQRFL 26_ QILKV 31_ LFPSW 36_ SSQNA 41_ LMFLT 46_ LLCLT 51_ LLEQF 56_ VIYQV 61_ GLIPS 66_ QYYGV 71_ LGNKD 76_ LEGFK 81_ TLTFL 86_ AVMLI 91_ VLNST 96_ LKSFD 101_ QFTCN 106_ LLYVS 111_ WRKDL 116_ TEHLH 121_ RLYFR 126_ GRAYY 131_ TLNVL 136_ RDDID 141_ NPDQR 146_ ISQDV 151_ ERFCR 156_ QLSSM 161_ ASKLI 166_ ISPFT 171_ LVYYT 176_ YQCFQ 181_ STGWL 186_ GPVSI 191_ FGYFI 196_ LGTVV 201_ NKTLM 206_ GPIVM 211_ KLVHQ 216_ EKLEG 221_ DFRFK 226_ HMQIR 231_ VNAEP 236_ AAFYR 241_ AGHVE 246_ HMRTD 251_ RRLQR 256_ LLQTQ 261_ RELMS 266_ KELWL 271_ YIGIN 276_ TFDYL 281_ GSILS 286_ YVVIA 291_ IPIFS 296_ GVYGD 301_ LSPAE 306_ LSTLV 311_ SKNAF 316_ VCIYL 321_ ISCFT 326_ QLIDL 331_ STTLS 336_ DVAGY 341_ THRIG 346_ QLRET 351_ LLDMS 356_ LKSQD 361_ CEILG 366_ ESEWG 371_ LDTPP 376_ GWPAA 381_ EPADT 386_ AFLLE 391_ RVSIS 396_ APSSD 401_ KPLIK 406_ DLSLK 411_ ISEGQ 416_ SLLIT 421_ GNTGT 426_ GKTSL 431_ LRVLG 436_ GLWTS 441_ TRGSV 446_ QMLTD 451_ FGPHG 456_ VLFLP 461_ QKPFF 466_ TDGTL 471_ REQVI 476_ YPLKE 481_ VYPDS 486_ GSADD 491_ ERILR 496_ FLELA 501_ GLSNL 506_ VARTE 511_ GLDQQ 516_ VDWNW 521_ YDVLS 526_ PGEMQ 531_ RLSFA 536_ RLFYL 541_ QPKYA 546_ VLDEA 551_ TSALT 556_ EEVES 561_ ELYRI 566_ GQQLG 571_ MTFIS 576_ VGHRQ 581_ SLEKF 586_ HSLVL 591_ KLCGG 596_ GRWEL 601_MRIKV
1: Lysosomal membrane protein that transports cobalamin (Vitamin B12) from the lysosomal lumen to the cytosol in an ATP-dependent manner (PubMed:22922874, PubMed:28572511, PubMed:31467407, PubMed:33845046). Targeted by LMBRD1 lysosomal chaperone from the endoplasmic reticulum to the lysosomal membrane (PubMed:27456980). Then forms a complex with lysosomal chaperone LMBRD1 and cytosolic MMACHC to transport cobalamin across the lysosomal membrane (PubMed:25535791)