Gene name: PRORP

Uniprot entry:

O15091

Protein names:

Mitochondrial ribonuclease P catalytic subunit (EC 3.1.26.5) (Mitochondrial ribonuclease P protein 3) (Mitochondrial RNase P protein 3) (Protein only RNase P catalytic subunit)

Protein sequence:

1_MTFYL 6_ FGIRS 11_ FPKLW 16_ KSPYL 21_ GLGPG 26_ HSYVS 31_ LFLAD 36_ RCGIR 41_ NQQRL 46_ FSLKT 51_ MSPQN 56_ TKATN 61_ LIAKA 66_ RYLRK 71_ DEGSN 76_ KQVYS 81_ VPHFF 86_ LAGAA 91_ KERSQ 96_ MNSQT 101_ EDHAL 106_ APVRN 111_ TIQLP 116_ TQPLN 121_ SEEWD 126_ KLKED 131_ LKENT 136_ GKTSF 141_ ESWII 146_ SQMAG 151_ CHSSI 156_ DVAKS 161_ LLAWV 166_ AAKNN 171_ GIVSY 176_ DLLVK 181_ YLYLC 186_ VFHMQ 191_ TSEVI 196_ DVFEI 201_ MKARY 206_ KTLEP 211_ RGYSL 216_ LIRGL 221_ IHSDR 226_ WREAL 231_ LLLED 236_ IKKVI 241_ TPSKK 246_ NYNDC 251_ IQGAL 256_ LHQDV 261_ NTAWN 266_ LYQEL 271_ LGHDI 276_ VPMLE 281_ TLKAF 286_ FDFGK 291_ DIKDD 296_ NYSNK 301_ LLDIL 306_ SYLRN 311_ NQLYP 316_ GESFA 321_ HSIKT 326_ WFESV 331_ PGKQW 336_ KGQFT 341_ TVRKS 346_ GQCSG 351_ CGKTI 356_ ESIQL 361_ SPEEY 366_ ECLKG 371_ KIMRD 376_ VIDGG 381_ DQYRK 386_ TTPQE 391_ LKRFE 396_ NFIKS 401_ RPPFD 406_ VVIDG 411_ LNVAK 416_ MFPKV 421_ RESQL 426_ LLNVV 431_ SQLAK 436_ RNLRL 441_ LVLGR 446_ KHMLR 451_ RSSQW 456_ SRDEM 461_ EEVQK 466_ QASCF 471_ FADDI 476_ SEDDP 481_ FLLYA 486_ TLHSG 491_ NHCRF 496_ ITRDL 501_ MRDHK 506_ ACLPD 511_ AKTQR 516_ LFFKW 521_ QQGHQ 526_ LAIVN 531_ RFPGS 536_ KLTFQ 541_ RILSY 546_ DTVVQ 551_ TTGDS 556_ WHIPY 561_ DEDLV 566_ ERCSC 571_ EVPTK 576_WLCLH

Protein annotations

Protein functions:

1: Catalytic ribonuclease component of mitochondrial ribonuclease P, a complex composed of TRMT10C/MRPP1, HSD17B10/MRPP2 and PRORP/MRPP3, which cleaves tRNA molecules in their 5'-ends (PubMed:18984158, PubMed:25953853, PubMed:34715011). The presence of TRMT10C/MRPP1, HSD17B10/MRPP2 is required to catalyze tRNA molecules in their 5'-ends (PubMed:25953853)