Pentatricopeptide repeat-containing protein 1, mitochondrial
1_MDFVR 6_ LARLF 11_ ARARP 16_ MGLFI 21_ LQHLD 26_ PCRAR 31_ WAGGR 36_ EGLMR 41_ PMWAP 46_ FSSSS 51_ SQLPL 56_ GQERQ 61_ ENTGS 66_ LGSDP 71_ SHSNS 76_ TATQE 81_ EDEEE 86_ EESFG 91_ TLSDK 96_ YSSRR 101_ LFRKS 106_ AAQFH 111_ NLRFG 116_ ERRDE 121_ QMEPE 126_ PKLWR 131_ GRRNT 136_ PYWYF 141_ LQCKH 146_ LIKEG 151_ KLVEA 156_ LDLFE 161_ RQMLK 166_ EERLQ 171_ PMESN 176_ YTVLI 181_ GGCGR 186_ VGYLK 191_ KAFNL 196_ YNQMK 201_ KRDLE 206_ PSDAT 211_ YTALF 216_ NVCAE 221_ SPWKD 226_ SALQS 231_ ALKLR 236_ QQLQA 241_ KNFEL 246_ NLKTY 251_ HALLK 256_ MAAKC 261_ ADLRM 266_ CLDVF 271_ KEIIH 276_ KGHVV 281_ TEETF 286_ SFLLM 291_ GCIQD 296_ KKTGF 301_ RYALQ 306_ VWRLM 311_ LSLGL 316_ QPSRD 321_ SYNLL 326_ LVAAR 331_ DCGLG 336_ DPQVA 341_ SELLL 346_ KPREE 351_ ATVLQ 356_ PPVSR 361_ QRPRR 366_ TAQAK 371_ AGNLM 376_ SAMLH 381_ VEALE 386_ RQLFL 391_ EPSQA 396_ LGPPE 401_ PPEAR 406_ VPGKA 411_ QPEVD 416_ TKAEP 421_ SHTAA 426_ LTAVA 431_ LKPPP 436_ VELEV 441_ NLLTP 446_ GAVPP 451_ TVVSF 456_ GTVTT 461_ PADRL 466_ ALIGG 471_ LEGFL 476_ SKMAE 481_ HRQQP 486_ DIRTL 491_ TLLAE 496_ VVESG 501_ SPAES 506_ LLLAL 511_ LDEHQ 516_ VEADL 521_ TFFNT 526_ LVRKK 531_ SKLGD 536_ LEGAK 541_ ALLPV 546_ LAKRG 551_ LVPNL 556_ QTFCN 561_ LAIGC 566_ HRPKD 571_ GLQLL 576_ TDMKK 581_ SQVTP 586_ NTHIY 591_ SALIN 596_ AAIRK 601_ LNYTY 606_ LISIL 611_ KDMKQ 616_ NRVPV 621_ NEVVI 626_ RQLEF 631_ AAQYP 636_ PTFDR 641_ YQGKN 646_ TYLEK 651_ IDGFR 656_ AYYKQ 661_ WLTVM 666_ PAEET 671_ PHPWQ 676_ KFRTK 681_ PQGDQ 686_ DTGKE 691_ADDGC
1: Mitochondrial protein implicated in negative regulation of leucine tRNA levels, as well as negative regulation of mitochondria-encoded proteins and COX activity. Also affects the 3'-processing of mitochondrial tRNAs