Phenylalanine--tRNA ligase, mitochondrial (EC 6.1.1.20) (Phenylalanyl-tRNA synthetase) (PheRS)
1_MVGSA 6_ LRRGA 11_ HAYVY 16_ LVSKA 21_ SHISR 26_ GHQHQ 31_ AWGSR 36_ PPAAE 41_ CATQR 46_ APGSV 51_ VELLG 56_ KSYPQ 61_ DDHSN 66_ LTRKV 71_ LTRVG 76_ RNLHN 81_ QQHHP 86_ LWLIK 91_ ERVKE 96_ HFYKQ 101_ YVGRF 106_ GTPLF 111_ SVYDN 116_ LSPVV 121_ TTWQN 126_ FDSLL 131_ IPADH 136_ PSRKK 141_ GDNYY 146_ LNRTH 151_ MLRAH 156_ TSAHQ 161_ WDLLH 166_ AGLDA 171_ FLVVG 176_ DVYRR 181_ DQIDS 186_ QHYPI 191_ FHQLE 196_ AVRLF 201_ SKHEL 206_ FAGIK 211_ DGESL 216_ QLFEQ 221_ SSRSA 226_ HKQET 231_ HTMEA 236_ VKLVE 241_ FDLKQ 246_ TLTRL 251_ MAHLF 256_ GDELE 261_ IRWVD 266_ CYFPF 271_ THPSF 276_ EMEIN 281_ FHGEW 286_ LEVLG 291_ CGVME 296_ QQLVN 301_ SAGAQ 306_ DRIGW 311_ AFGLG 316_ LERLA 321_ MILYD 326_ IPDIR 331_ LFWCE 336_ DERFL 341_ KQFCV 346_ SNINQ 351_ KVKFQ 356_ PLSKY 361_ PAVIN 366_ DISFW 371_ LPSEN 376_ YAEND 381_ FYDLV 386_ RTIGG 391_ DLVEK 396_ VDLID 401_ KFVHP 406_ KTHKT 411_ SHCYR 416_ ITYRH 421_ MERTL 426_ SQREV 431_ RHIHQ 436_ ALQEA 441_ AVQLL 446_GVEGR
1: Is responsible for the charging of tRNA(Phe) with phenylalanine in mitochondrial translation. To a lesser extent, also catalyzes direct attachment of m-Tyr (an oxidized version of Phe) to tRNA(Phe), thereby opening the way for delivery of the misacylated tRNA to the ribosome and incorporation of ROS-damaged amino acid into proteins