Gene name: GLA

Uniprot entry:

P06280

Protein names:

Alpha-galactosidase A (EC 3.2.1.22) (Alpha-D-galactosidase A) (Alpha-D-galactoside galactohydrolase) (Galactosylgalactosylglucosylceramidase GLA) (Melibiase) (Agalsidase)

Protein sequence:

1_MQLRN 6_ PELHL 11_ GCALA 16_ LRFLA 21_ LVSWD 26_ IPGAR 31_ ALDNG 36_ LARTP 41_ TMGWL 46_ HWERF 51_ MCNLD 56_ CQEEP 61_ DSCIS 66_ EKLFM 71_ EMAEL 76_ MVSEG 81_ WKDAG 86_ YEYLC 91_ IDDCW 96_ MAPQR 101_ DSEGR 106_ LQADP 111_ QRFPH 116_ GIRQL 121_ ANYVH 126_ SKGLK 131_ LGIYA 136_ DVGNK 141_ TCAGF 146_ PGSFG 151_ YYDID 156_ AQTFA 161_ DWGVD 166_ LLKFD 171_ GCYCD 176_ SLENL 181_ ADGYK 186_ HMSLA 191_ LNRTG 196_ RSIVY 201_ SCEWP 206_ LYMWP 211_ FQKPN 216_ YTEIR 221_ QYCNH 226_ WRNFA 231_ DIDDS 236_ WKSIK 241_ SILDW 246_ TSFNQ 251_ ERIVD 256_ VAGPG 261_ GWNDP 266_ DMLVI 271_ GNFGL 276_ SWNQQ 281_ VTQMA 286_ LWAIM 291_ AAPLF 296_ MSNDL 301_ RHISP 306_ QAKAL 311_ LQDKD 316_ VIAIN 321_ QDPLG 326_ KQGYQ 331_ LRQGD 336_ NFEVW 341_ ERPLS 346_ GLAWA 351_ VAMIN 356_ RQEIG 361_ GPRSY 366_ TIAVA 371_ SLGKG 376_ VACNP 381_ ACFIT 386_ QLLPV 391_ KRKLG 396_ FYEWT 401_ SRLRS 406_ HINPT 411_ GTVLL 416_ QLENT 421_MQMSL

Protein annotations

Protein functions:

1: Catalyzes the hydrolysis of glycosphingolipids and participates in their degradation in the lysosome