Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial (EC 1.2.4.1) (PDHE1-A type I)
1_MRKML 6_ AAVSR 11_ VLSGA 16_ SQKPA 21_ SRVLV 26_ ASRNF 31_ ANDAT 36_ FEIKK 41_ CDLHR 46_ LEEGP 51_ PVTTV 56_ LTRED 61_ GLKYY 66_ RMMQT 71_ VRRME 76_ LKADQ 81_ LYKQK 86_ IIRGF 91_ CHLCD 96_ GQEAC 101_ CVGLE 106_ AGINP 111_ TDHLI 116_ TAYRA 121_ HGFTF 126_ TRGLS 131_ VREIL 136_ AELTG 141_ RKGGC 146_ AKGKG 151_ GSMHM 156_ YAKNF 161_ YGGNG 166_ IVGAQ 171_ VPLGA 176_ GIALA 181_ CKYNG 186_ KDEVC 191_ LTLYG 196_ DGAAN 201_ QGQIF 206_ EAYNM 211_ AALWK 216_ LPCIF 221_ ICENN 226_ RYGMG 231_ TSVER 236_ AAAST 241_ DYYKR 246_ GDFIP 251_ GLRVD 256_ GMDIL 261_ CVREA 266_ TRFAA 271_ AYCRS 276_ GKGPI 281_ LMELQ 286_ TYRYH 291_ GHSMS 296_ DPGVS 301_ YRTRE 306_ EIQEV 311_ RSKSD 316_ PIMLL 321_ KDRMV 326_ NSNLA 331_ SVEEL 336_ KEIDV 341_ EVRKE 346_ IEDAA 351_ QFATA 356_ DPEPP 361_ LEELG 366_ YHIYS 371_ SDPPF 376_ EVRGA 381_NQWIK
1: The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2), and thereby links the glycolytic pathway to the tricarboxylic cycle