Lysosomal alpha-glucosidase (EC 3.2.1.20) (Acid maltase) (Aglucosidase alfa) [Cleaved into: 76 kDa lysosomal alpha-glucosidase; 70 kDa lysosomal alpha-glucosidase]
1_MGVRH 6_ PPCSH 11_ RLLAV 16_ CALVS 21_ LATAA 26_ LLGHI 31_ LLHDF 36_ LLVPR 41_ ELSGS 46_ SPVLE 51_ ETHPA 56_ HQQGA 61_ SRPGP 66_ RDAQA 71_ HPGRP 76_ RAVPT 81_ QCDVP 86_ PNSRF 91_ DCAPD 96_ KAITQ 101_ EQCEA 106_ RGCCY 111_ IPAKQ 116_ GLQGA 121_ QMGQP 126_ WCFFP 131_ PSYPS 136_ YKLEN 141_ LSSSE 146_ MGYTA 151_ TLTRT 156_ TPTFF 161_ PKDIL 166_ TLRLD 171_ VMMET 176_ ENRLH 181_ FTIKD 186_ PANRR 191_ YEVPL 196_ ETPHV 201_ HSRAP 206_ SPLYS 211_ VEFSE 216_ EPFGV 221_ IVRRQ 226_ LDGRV 231_ LLNTT 236_ VAPLF 241_ FADQF 246_ LQLST 251_ SLPSQ 256_ YITGL 261_ AEHLS 266_ PLMLS 271_ TSWTR 276_ ITLWN 281_ RDLAP 286_ TPGAN 291_ LYGSH 296_ PFYLA 301_ LEDGG 306_ SAHGV 311_ FLLNS 316_ NAMDV 321_ VLQPS 326_ PALSW 331_ RSTGG 336_ ILDVY 341_ IFLGP 346_ EPKSV 351_ VQQYL 356_ DVVGY 361_ PFMPP 366_ YWGLG 371_ FHLCR 376_ WGYSS 381_ TAITR 386_ QVVEN 391_ MTRAH 396_ FPLDV 401_ QWNDL 406_ DYMDS 411_ RRDFT 416_ FNKDG 421_ FRDFP 426_ AMVQE 431_ LHQGG 436_ RRYMM 441_ IVDPA 446_ ISSSG 451_ PAGSY 456_ RPYDE 461_ GLRRG 466_ VFITN 471_ ETGQP 476_ LIGKV 481_ WPGST 486_ AFPDF 491_ TNPTA 496_ LAWWE 501_ DMVAE 506_ FHDQV 511_ PFDGM 516_ WIDMN 521_ EPSNF 526_ IRGSE 531_ DGCPN 536_ NELEN 541_ PPYVP 546_ GVVGG 551_ TLQAA 556_ TICAS 561_ SHQFL 566_ STHYN 571_ LHNLY 576_ GLTEA 581_ IASHR 586_ ALVKA 591_ RGTRP 596_ FVISR 601_ STFAG 606_ HGRYA 611_ GHWTG 616_ DVWSS 621_ WEQLA 626_ SSVPE 631_ ILQFN 636_ LLGVP 641_ LVGAD 646_ VCGFL 651_ GNTSE 656_ ELCVR 661_ WTQLG 666_ AFYPF 671_ MRNHN 676_ SLLSL 681_ PQEPY 686_ SFSEP 691_ AQQAM 696_ RKALT 701_ LRYAL 706_ LPHLY 711_ TLFHQ 716_ AHVAG 721_ ETVAR 726_ PLFLE 731_ FPKDS 736_ STWTV 741_ DHQLL 746_ WGEAL 751_ LITPV 756_ LQAGK 761_ AEVTG 766_ YFPLG 771_ TWYDL 776_ QTVPV 781_ EALGS 786_ LPPPP 791_ AAPRE 796_ PAIHS 801_ EGQWV 806_ TLPAP 811_ LDTIN 816_ VHLRA 821_ GYIIP 826_ LQGPG 831_ LTTTE 836_ SRQQP 841_ MALAV 846_ ALTKG 851_ GEARG 856_ ELFWD 861_ DGESL 866_ EVLER 871_ GAYTQ 876_ VIFLA 881_ RNNTI 886_ VNELV 891_ RVTSE 896_ GAGLQ 901_ LQKVT 906_ VLGVA 911_ TAPQQ 916_ VLSNG 921_ VPVSN 926_ FTYSP 931_ DTKVL 936_ DICVS 941_ LLMGE 946_QFLVS
1: Essential for the degradation of glycogen in lysosomes (PubMed:14695532, PubMed:18429042, PubMed:1856189, PubMed:7717400). Has highest activity on alpha-1,4-linked glycosidic linkages, but can also hydrolyze alpha-1,6-linked glucans (PubMed:29061980)