Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial (EC 2.3.1.12) (70 kDa mitochondrial autoantigen of primary biliary cirrhosis) (PBC) (Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex) (M2 antigen complex 70 kDa subunit) (Pyruvate dehydrogenase complex component E2) (PDC-E2) (PDCE2)
1_MWRVC 6_ ARRAQ 11_ NVAPW 16_ AGLEA 21_ RWTAL 26_ QEVPG 31_ TPRVT 36_ SRSGP 41_ APARR 46_ NSVTT 51_ GYGGV 56_ RALCG 61_ WTPSS 66_ GATPR 71_ NRLLL 76_ QLLGS 81_ PGRRY 86_ YSLPP 91_ HQKVP 96_ LPSLS 101_ PTMQA 106_ GTIAR 111_ WEKKE 116_ GDKIN 121_ EGDLI 126_ AEVET 131_ DKATV 136_ GFESL 141_ EECYM 146_ AKILV 151_ AEGTR 156_ DVPIG 161_ AIICI 166_ TVGKP 171_ EDIEA 176_ FKNYT 181_ LDSSA 186_ APTPQ 191_ AAPAP 196_ TPAAT 201_ ASPPT 206_ PSAQA 211_ PGSSY 216_ PPHMQ 221_ VLLPA 226_ LSPTM 231_ TMGTV 236_ QRWEK 241_ KVGEK 246_ LSEGD 251_ LLAEI 256_ ETDKA 261_ TIGFE 266_ VQEEG 271_ YLAKI 276_ LVPEG 281_ TRDVP 286_ LGTPL 291_ CIIVE 296_ KEADI 301_ SAFAD 306_ YRPTE 311_ VTDLK 316_ PQVPP 321_ PTPPP 326_ VAAVP 331_ PTPQP 336_ LAPTP 341_ SAPCP 346_ ATPAG 351_ PKGRV 356_ FVSPL 361_ AKKLA 366_ VEKGI 371_ DLTQV 376_ KGTGP 381_ DGRIT 386_ KKDID 391_ SFVPS 396_ KVAPA 401_ PAAVV 406_ PPTGP 411_ GMAPV 416_ PTGVF 421_ TDIPI 426_ SNIRR 431_ VIAQR 436_ LMQSK 441_ QTIPH 446_ YYLSI 451_ DVNMG 456_ EVLLV 461_ RKELN 466_ KILEG 471_ RSKIS 476_ VNDFI 481_ IKASA 486_ LACLK 491_ VPEAN 496_ SSWMD 501_ TVIRQ 506_ NHVVD 511_ VSVAV 516_ STPAG 521_ LITPI 526_ VFNAH 531_ IKGVE 536_ TIAND 541_ VVSLA 546_ TKARE 551_ GKLQP 556_ HEFQG 561_ GTFTI 566_ SNLGM 571_ FGIKN 576_ FSAII 581_ NPPQA 586_ CILAI 591_ GASED 596_ KLVPA 601_ DNEKG 606_ FDVAS 611_ MMSVT 616_ LSCDH 621_ RVVDG 626_ AVGAQ 631_ WLAEF 636_ RKYLE 641_KPITM
1: As part of the pyruvate dehydrogenase complex, catalyzes the transfers of an acetyl group to a lipoic acid moiety (Probable). The pyruvate dehydrogenase complex, catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2), and thereby links cytoplasmic glycolysis and the mitochondrial tricarboxylic acid (TCA) cycle (Probable)