Pyruvate carboxylase, mitochondrial (EC 6.4.1.1) (Pyruvic carboxylase) (PCB)
1_MLKFR 6_ TVHGG 11_ LRLLG 16_ IRRTS 21_ TAPAA 26_ SPNVR 31_ RLEYK 36_ PIKKV 41_ MVANR 46_ GEIAI 51_ RVFRA 56_ CTELG 61_ IRTVA 66_ IYSEQ 71_ DTGQM 76_ HRQKA 81_ DEAYL 86_ IGRGL 91_ APVQA 96_ YLHIP 101_ DIIKV 106_ AKENN 111_ VDAVH 116_ PGYGF 121_ LSERA 126_ DFAQA 131_ CQDAG 136_ VRFIG 141_ PSPEV 146_ VRKMG 151_ DKVEA 156_ RAIAI 161_ AAGVP 166_ VVPGT 171_ DAPIT 176_ SLHEA 181_ HEFSN 186_ TYGFP 191_ IIFKA 196_ AYGGG 201_ GRGMR 206_ VVHSY 211_ EELEE 216_ NYTRA 221_ YSEAL 226_ AAFGN 231_ GALFV 236_ EKFIE 241_ KPRHI 246_ EVQIL 251_ GDQYG 256_ NILHL 261_ YERDC 266_ SIQRR 271_ HQKVV 276_ EIAPA 281_ AHLDP 286_ QLRTR 291_ LTSDS 296_ VKLAK 301_ QVGYE 306_ NAGTV 311_ EFLVD 316_ RHGKH 321_ YFIEV 326_ NSRLQ 331_ VEHTV 336_ TEEIT 341_ DVDLV 346_ HAQIH 351_ VAEGR 356_ SLPDL 361_ GLRQE 366_ NIRIN 371_ GCAIQ 376_ CRVTT 381_ EDPAR 386_ SFQPD 391_ TGRIE 396_ VFRSG 401_ EGMGI 406_ RLDNA 411_ SAFQG 416_ AVISP 421_ HYDSL 426_ LVKVI 431_ AHGKD 436_ HPTAA 441_ TKMSR 446_ ALAEF 451_ RVRGV 456_ KTNIA 461_ FLQNV 466_ LNNQQ 471_ FLAGT 476_ VDTQF 481_ IDENP 486_ ELFQL 491_ RPAQN 496_ RAQKL 501_ LHYLG 506_ HVMVN 511_ GPTTP 516_ IPVKA 521_ SPSPT 526_ DPVVP 531_ AVPIG 536_ PPPAG 541_ FRDIL 546_ LREGP 551_ EGFAR 556_ AVRNH 561_ PGLLL 566_ MDTTF 571_ RDAHQ 576_ SLLAT 581_ RVRTH 586_ DLKKI 591_ APYVA 596_ HNFSK 601_ LFSME 606_ NWGGA 611_ TFDVA 616_ MRFLY 621_ ECPWR 626_ RLQEL 631_ RELIP 636_ NIPFQ 641_ MLLRG 646_ ANAVG 651_ YTNYP 656_ DNVVF 661_ KFCEV 666_ AKENG 671_ MDVFR 676_ VFDSL 681_ NYLPN 686_ MLLGM 691_ EAAGS 696_ AGGVV 701_ EAAIS 706_ YTGDV 711_ ADPSR 716_ TKYSL 721_ QYYMG 726_ LAEEL 731_ VRAGT 736_ HILCI 741_ KDMAG 746_ LLKPT 751_ ACTML 756_ VSSLR 761_ DRFPD 766_ LPLHI 771_ HTHDT 776_ SGAGV 781_ AAMLA 786_ CAQAG 791_ ADVVD 796_ VAADS 801_ MSGMT 806_ SQPSM 811_ GALVA 816_ CTRGT 821_ PLDTE 826_ VPMER 831_ VFDYS 836_ EYWEG 841_ ARGLY 846_ AAFDC 851_ TATMK 856_ SGNSD 861_ VYENE 866_ IPGGQ 871_ YTNLH 876_ FQAHS 881_ MGLGS 886_ KFKEV 891_ KKAYV 896_ EANQM 901_ LGDLI 906_ KVTPS 911_ SKIVG 916_ DLAQF 921_ MVQNG 926_ LSRAE 931_ AEAQA 936_ EELSF 941_ PRSVV 946_ EFLQG 951_ YIGVP 956_ HGGFP 961_ EPFRS 966_ KVLKD 971_ LPRVE 976_ GRPGA 981_ SLPPL 986_ DLQAL 991_ EKELV 996_ DRHGE 1001_ EVTPE 1006_ DVLSA 1011_ AMYPD 1016_ VFAHF 1021_ KDFTA 1026_ TFGPL 1031_ DSLNT 1036_ RLFLQ 1041_ GPKIA 1046_ EEFEV 1051_ ELERG 1056_ KTLHI 1061_ KALAV 1066_ SDLNR 1071_ AGQRQ 1076_ VFFEL 1081_ NGQLR 1086_ SILVK 1091_ DTQAM 1096_ KEMHF 1101_ HPKAL 1106_ KDVKG 1111_ QIGAP 1116_ MPGKV 1121_ IDIKV 1126_ VAGAK 1131_ VAKGQ 1136_ PLCVL 1141_ SAMKM 1146_ ETVVT 1151_ SPMEG 1156_ TVRKV 1161_ HVTKD 1166_ MTLEG 1171_DDLIL
1: Pyruvate carboxylase catalyzes a 2-step reaction, involving the ATP-dependent carboxylation of the covalently attached biotin in the first step and the transfer of the carboxyl group to pyruvate in the second. Catalyzes in a tissue specific manner, the initial reactions of glucose (liver, kidney) and lipid (adipose tissue, liver, brain) synthesis from pyruvate