5-aminolevulinate synthase, non-specific, mitochondrial (ALAS-H) (EC 2.3.1.37) (5-aminolevulinic acid synthase 1) (Delta-ALA synthase 1) (Delta-aminolevulinate synthase 1)
1_MESVV 6_ RRCPF 11_ LSRVP 16_ QAFLQ 21_ KAGKS 26_ LLFYA 31_ QNCPK 36_ MMEVG 41_ AKPAP 46_ RALST 51_ AAVHY 56_ QQIKE 61_ TPPAS 66_ EKDKT 71_ AKAKV 76_ QQTPD 81_ GSQQS 86_ PDGTQ 91_ LPSGH 96_ PLPAT 101_ SQGTA 106_ SKCPF 111_ LAAQM 116_ NQRGS 121_ SVFCK 126_ ASLEL 131_ QEDVQ 136_ EMNAV 141_ RKEVA 146_ ETSAG 151_ PSVVS 156_ VKTDG 161_ GDPSG 166_ LLKNF 171_ QDIMQ 176_ KQRPE 181_ RVSHL 186_ LQDNL 191_ PKSVS 196_ TFQYD 201_ RFFEK 206_ KIDEK 211_ KNDHT 216_ YRVFK 221_ TVNRR 226_ AHIFP 231_ MADDY 236_ SDSLI 241_ TKKQV 246_ SVWCS 251_ NDYLG 256_ MSRHP 261_ RVCGA 266_ VMDTL 271_ KQHGA 276_ GAGGT 281_ RNISG 286_ TSKFH 291_ VDLER 296_ ELADL 301_ HGKDA 306_ ALLFS 311_ SCFVA 316_ NDSTL 321_ FTLAK 326_ MMPGC 331_ EIYSD 336_ SGNHA 341_ SMIQG 346_ IRNSR 351_ VPKYI 356_ FRHND 361_ VSHLR 366_ ELLQR 371_ SDPSV 376_ PKIVA 381_ FETVH 386_ SMDGA 391_ VCPLE 396_ ELCDV 401_ AHEFG 406_ AITFV 411_ DEVHA 416_ VGLYG 421_ ARGGG 426_ IGDRD 431_ GVMPK 436_ MDIIS 441_ GTLGK 446_ AFGCV 451_ GGYIA 456_ STSSL 461_ IDTVR 466_ SYAAG 471_ FIFTT 476_ SLPPM 481_ LLAGA 486_ LESVR 491_ ILKSA 496_ EGRVL 501_ RRQHQ 506_ RNVKL 511_ MRQML 516_ MDAGL 521_ PVVHC 526_ PSHII 531_ PVRVA 536_ DAAKN 541_ TEVCD 546_ ELMSR 551_ HNIYV 556_ QAINY 561_ PTVPR 566_ GEELL 571_ RIAPT 576_ PHHTP 581_ QMMNY 586_ FLENL 591_ LVTWK 596_ QVGLE 601_ LKPHS 606_ SAECN 611_ FCRRP 616_ LHFEV 621_ MSERE 626_ KSYFS 631_GLSKL
1: Catalyzes the pyridoxal 5'-phosphate (PLP)-dependent condensation of succinyl-CoA and glycine to form aminolevulinic acid (ALA), with CoA and CO2 as by-products