Electron transfer flavoprotein subunit alpha, mitochondrial (Alpha-ETF)
1_MFRAA 6_ APGQL 11_ RRAAS 16_ LLRFQ 21_ STLVI 26_ AEHAN 31_ DSLAP 36_ ITLNT 41_ ITAAT 46_ RLGGE 51_ VSCLV 56_ AGTKC 61_ DKVAQ 66_ DLCKV 71_ AGIAK 76_ VLVAQ 81_ HDVYK 86_ GLLPE 91_ ELTPL 96_ ILATQ 101_ KQFNY 106_ THICA 111_ GASAF 116_ GKNLL 121_ PRVAA 126_ KLEVA 131_ PISDI 136_ IAIKS 141_ PDTFV 146_ RTIYA 151_ GNALC 156_ TVKCD 161_ EKVKV 166_ FSVRG 171_ TSFDA 176_ AATSG 181_ GSASS 186_ EKASS 191_ TSPVE 196_ ISEWL 201_ DQKLT 206_ KSDRP 211_ ELTGA 216_ KVVVS 221_ GGRGL 226_ KSGEN 231_ FKLLY 236_ DLADQ 241_ LHAAV 246_ GASRA 251_ AVDAG 256_ FVPND 261_ MQVGQ 266_ TGKIV 271_ APELY 276_ IAVGI 281_ SGAIQ 286_ HLAGM 291_ KDSKT 296_ IVAIN 301_ KDPEA 306_ PIFQV 311_ ADYGI 316_ VADLF 321_ KVVPE 326_MTEIL
1: Heterodimeric electron transfer flavoprotein that accepts electrons from several mitochondrial dehydrogenases, including acyl-CoA dehydrogenases, glutaryl-CoA and sarcosine dehydrogenase (PubMed:10356313, PubMed:15159392, PubMed:15975918, PubMed:27499296, PubMed:9334218). It transfers the electrons to the main mitochondrial respiratory chain via ETF-ubiquinone oxidoreductase (ETF dehydrogenase) (PubMed:9334218). Required for normal mitochondrial fatty acid oxidation and normal amino acid metabolism (PubMed:12815589, PubMed:1430199, PubMed:1882842)