Methylmalonyl-CoA mutase, mitochondrial (MCM) (EC 5.4.99.2) (Methylmalonyl-CoA isomerase)
1_MLRAK 6_ NQLFL 11_ LSPHY 16_ LRQVK 21_ ESSGS 26_ RLIQQ 31_ RLLHQ 36_ QQPLH 41_ PEWAA 46_ LAKKQ 51_ LKGKN 56_ PEDLI 61_ WHTPE 66_ GISIK 71_ PLYSK 76_ RDTMD 81_ LPEEL 86_ PGVKP 91_ FTRGP 96_ YPTMY 101_ TFRPW 106_ TIRQY 111_ AGFST 116_ VEESN 121_ KFYKD 126_ NIKAG 131_ QQGLS 136_ VAFDL 141_ ATHRG 146_ YDSDN 151_ PRVRG 156_ DVGMA 161_ GVAID 166_ TVEDT 171_ KILFD 176_ GIPLE 181_ KMSVS 186_ MTMNG 191_ AVIPV 196_ LANFI 201_ VTGEE 206_ QGVPK 211_ EKLTG 216_ TIQND 221_ ILKEF 226_ MVRNT 231_ YIFPP 236_ EPSMK 241_ IIADI 246_ FEYTA 251_ KHMPK 256_ FNSIS 261_ ISGYH 266_ MQEAG 271_ ADAIL 276_ ELAYT 281_ LADGL 286_ EYSRT 291_ GLQAG 296_ LTIDE 301_ FAPRL 306_ SFFWG 311_ IGMNF 316_ YMEIA 321_ KMRAG 326_ RRLWA 331_ HLIEK 336_ MFQPK 341_ NSKSL 346_ LLRAH 351_ CQTSG 356_ WSLTE 361_ QDPYN 366_ NIVRT 371_ AIEAM 376_ AAVFG 381_ GTQSL 386_ HTNSF 391_ DEALG 396_ LPTVK 401_ SARIA 406_ RNTQI 411_ IIQEE 416_ SGIPK 421_ VADPW 426_ GGSYM 431_ MECLT 436_ NDVYD 441_ AALKL 446_ INEIE 451_ EMGGM 456_ AKAVA 461_ EGIPK 466_ LRIEE 471_ CAARR 476_ QARID 481_ SGSEV 486_ IVGVN 491_ KYQLE 496_ KEDAV 501_ EVLAI 506_ DNTSV 511_ RNRQI 516_ EKLKK 521_ IKSSR 526_ DQALA 531_ ERCLA 536_ ALTEC 541_ AASGD 546_ GNILA 551_ LAVDA 556_ SRARC 561_ TVGEI 566_ TDALK 571_ KVFGE 576_ HKAND 581_ RMVSG 586_ AYRQE 591_ FGESK 596_ EITSA 601_ IKRVH 606_ KFMER 611_ EGRRP 616_ RLLVA 621_ KMGQD 626_ GHDRG 631_ AKVIA 636_ TGFAD 641_ LGFDV 646_ DIGPL 651_ FQTPR 656_ EVAQQ 661_ AVDAD 666_ VHAVG 671_ ISTLA 676_ AGHKT 681_ LVPEL 686_ IKELN 691_ SLGRP 696_ DILVM 701_ CGGVI 706_ PPQDY 711_ EFLFE 716_ VGVSN 721_ VFGPG 726_ TRIPK 731_ AAVQV 736_ LDDIE 741_KCLEK
1: Catalyzes the reversible isomerization of methylmalonyl-CoA (MMCoA) (generated from branched-chain amino acid metabolism and degradation of dietary odd chain fatty acids and cholesterol) to succinyl-CoA (3-carboxypropionyl-CoA), a key intermediate of the tricarboxylic acid cycle