Gene name: IDS

Uniprot entry:

P22304

Protein names:

Iduronate 2-sulfatase (EC 3.1.6.13) (Alpha-L-iduronate sulfate sulfatase) (Idursulfase) [Cleaved into: Iduronate 2-sulfatase 42 kDa chain; Iduronate 2-sulfatase 14 kDa chain]

Protein sequence:

1_MPPPR 6_ TGRGL 11_ LWLGL 16_ VLSSV 21_ CVALG 26_ SETQA 31_ NSTTD 36_ ALNVL 41_ LIIVD 46_ DLRPS 51_ LGCYG 56_ DKLVR 61_ SPNID 66_ QLASH 71_ SLLFQ 76_ NAFAQ 81_ QAVCA 86_ PSRVS 91_ FLTGR 96_ RPDTT 101_ RLYDF 106_ NSYWR 111_ VHAGN 116_ FSTIP 121_ QYFKE 126_ NGYVT 131_ MSVGK 136_ VFHPG 141_ ISSNH 146_ TDDSP 151_ YSWSF 156_ PPYHP 161_ SSEKY 166_ ENTKT 171_ CRGPD 176_ GELHA 181_ NLLCP 186_ VDVLD 191_ VPEGT 196_ LPDKQ 201_ STEQA 206_ IQLLE 211_ KMKTS 216_ ASPFF 221_ LAVGY 226_ HKPHI 231_ PFRYP 236_ KEFQK 241_ LYPLE 246_ NITLA 251_ PDPEV 256_ PDGLP 261_ PVAYN 266_ PWMDI 271_ RQRED 276_ VQALN 281_ ISVPY 286_ GPIPV 291_ DFQRK 296_ IRQSY 301_ FASVS 306_ YLDTQ 311_ VGRLL 316_ SALDD 321_ LQLAN 326_ STIIA 331_ FTSDH 336_ GWALG 341_ EHGEW 346_ AKYSN 351_ FDVAT 356_ HVPLI 361_ FYVPG 366_ RTASL 371_ PEAGE 376_ KLFPY 381_ LDPFD 386_ SASQL 391_ MEPGR 396_ QSMDL 401_ VELVS 406_ LFPTL 411_ AGLAG 416_ LQVPP 421_ RCPVP 426_ SFHVE 431_ LCREG 436_ KNLLK 441_ HFRFR 446_ DLEED 451_ PYLPG 456_ NPREL 461_ IAYSQ 466_ YPRPS 471_ DIPQW 476_ NSDKP 481_ SLKDI 486_ KIMGY 491_ SIRTI 496_ DYRYT 501_ VWVGF 506_ NPDEF 511_ LANFS 516_ DIHAG 521_ ELYFV 526_ DSDPL 531_ QDHNM 536_ YNDSQ 541_GGDLF

Protein annotations

Protein functions:

1: Lysosomal enzyme involved in the degradation pathway of dermatan sulfate and heparan sulfate