Isovaleryl-CoA dehydrogenase, mitochondrial (IVD) (EC 1.3.8.4) (Butyryl-CoA dehydrogenase) (EC 1.3.8.1)
1_MAEMA 6_ TATRL 11_ LGWRV 16_ ASWRL 21_ RPPLA 26_ GFVSQ 31_ RAHSL 36_ LPVDD 41_ AINGL 46_ SEEQR 51_ QLRQT 56_ MAKFL 61_ QEHLA 66_ PKAQE 71_ IDRSN 76_ EFKNL 81_ REFWK 86_ QLGNL 91_ GVLGI 96_ TAPVQ 101_ YGGSG 106_ LGYLE 111_ HVLVM 116_ EEISR 121_ ASGAV 126_ GLSYG 131_ AHSNL 136_ CINQL 141_ VRNGN 146_ EAQKE 151_ KYLPK 156_ LISGE 161_ YIGAL 166_ AMSEP 171_ NAGSD 176_ VVSMK 181_ LKAEK 186_ KGNHY 191_ ILNGN 196_ KFWIT 201_ NGPDA 206_ DVLIV 211_ YAKTD 216_ LAAVP 221_ ASRGI 226_ TAFIV 231_ EKGMP 236_ GFSTS 241_ KKLDK 246_ LGMRG 251_ SNTCE 256_ LIFED 261_ CKIPA 266_ ANILG 271_ HENKG 276_ VYVLM 281_ SGLDL 286_ ERLVL 291_ AGGPL 296_ GLMQA 301_ VLDHT 306_ IPYLH 311_ VREAF 316_ GQKIG 321_ HFQLM 326_ QGKMA 331_ DMYTR 336_ LMACR 341_ QYVYN 346_ VAKAC 351_ DEGHC 356_ TAKDC 361_ AGVIL 366_ YSAEC 371_ ATQVA 376_ LDGIQ 381_ CFGGN 386_ GYIND 391_ FPMGR 396_ FLRDA 401_ KLYEI 406_ GAGTS 411_ EVRRL 416_ VIGRA 421_FNADF
1: Catalyzes the conversion of isovaleryl-CoA/3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA as an intermediate step in the leucine (Leu) catabolic pathway (PubMed:7640268). To a lesser extent, is also able to catalyze the oxidation of other saturated short-chain acyl-CoA thioesters as pentanoyl-CoA, hexenoyl-CoA and butenoyl-CoA (PubMed:7640268)