Gene name: CFP

Uniprot entry:

P27918

Protein names:

Properdin (Complement factor P)

Protein sequence:

1_MITEG 6_ AQAPR 11_ LLLPP 16_ LLLLL 21_ TLPAT 26_ GSDPV 31_ LCFTQ 36_ YEESS 41_ GKCKG 46_ LLGGG 51_ VSVED 56_ CCLNT 61_ AFAYQ 66_ KRSGG 71_ LCQPC 76_ RSPRW 81_ SLWST 86_ WAPCS 91_ VTCSE 96_ GSQLR 101_ YRRCV 106_ GWNGQ 111_ CSGKV 116_ APGTL 121_ EWQLQ 126_ ACEDQ 131_ QCCPE 136_ MGGWS 141_ GWGPW 146_ EPCSV 151_ TCSKG 156_ TRTRR 161_ RACNH 166_ PAPKC 171_ GGHCP 176_ GQAQE 181_ SEACD 186_ TQQVC 191_ PTHGA 196_ WATWG 201_ PWTPC 206_ SASCH 211_ GGPHE 216_ PKETR 221_ SRKCS 226_ APEPS 231_ QKPPG 236_ KPCPG 241_ LAYEQ 246_ RRCTG 251_ LPPCP 256_ VAGGW 261_ GPWGP 266_ VSPCP 271_ VTCGL 276_ GQTME 281_ QRTCN 286_ HPVPQ 291_ HGGPF 296_ CAGDA 301_ TRTHI 306_ CNTAV 311_ PCPVD 316_ GEWDS 321_ WGEWS 326_ PCIRR 331_ NMKSI 336_ SCQEI 341_ PGQQS 346_ RGRTC 351_ RGRKF 356_ DGHRC 361_ AGQQQ 366_ DIRHC 371_ YSIQH 376_ CPLKG 381_ SWSEW 386_ STWGL 391_ CMPPC 396_ GPNPT 401_ RARQR 406_ LCTPL 411_ LPKYP 416_ PTVSM 421_ VEGQG 426_ EKNVT 431_ FWGRP 436_ LPRCE 441_ ELQGQ 446_ KLVVE 451_ EKRPC 456_ LHVPA 461_CKDPE

Protein annotations

Protein functions:

1: A positive regulator of the alternate pathway (AP) of complement (PubMed:16301317, PubMed:20382442, PubMed:28264884, PubMed:9748277). It binds to and stabilizes the C3- and C5-convertase enzyme complexes (PubMed:16301317, PubMed:20382442, PubMed:28264884, PubMed:9748277). Inhibits CFI-CFH mediated degradation of Complement C3 beta chain (C3b) (PubMed:31507604)