Carbamoyl-phosphate synthase [ammonia], mitochondrial (EC 6.3.4.16) (Carbamoyl-phosphate synthetase I) (CPSase I)
1_MTRIL 6_ TAFKV 11_ VRTLK 16_ TGFGF 21_ TNVTA 26_ HQKWK 31_ FSRPG 36_ IRLLS 41_ VKAQT 46_ AHIVL 51_ EDGTK 56_ MKGYS 61_ FGHPS 66_ SVAGE 71_ VVFNT 76_ GLGGY 81_ PEAIT 86_ DPAYK 91_ GQILT 96_ MANPI 101_ IGNGG 106_ APDTT 111_ ALDEL 116_ GLSKY 121_ LESNG 126_ IKVSG 131_ LLVLD 136_ YSKDY 141_ NHWLA 146_ TKSLG 151_ QWLQE 156_ EKVPA 161_ IYGVD 166_ TRMLT 171_ KIIRD 176_ KGTML 181_ GKIEF 186_ EGQPV 191_ DFVDP 196_ NKQNL 201_ IAEVS 206_ TKDVK 211_ VYGKG 216_ NPTKV 221_ VAVDC 226_ GIKNN 231_ VIRLL 236_ VKRGA 241_ EVHLV 246_ PWNHD 251_ FTKME 256_ YDGIL 261_ IAGGP 266_ GNPAL 271_ AEPLI 276_ QNVRK 281_ ILESD 286_ RKEPL 291_ FGIST 296_ GNLIT 301_ GLAAG 306_ AKTYK 311_ MSMAN 316_ RGQNQ 321_ PVLNI 326_ TNKQA 331_ FITAQ 336_ NHGYA 341_ LDNTL 346_ PAGWK 351_ PLFVN 356_ VNDQT 361_ NEGIM 366_ HESKP 371_ FFAVQ 376_ FHPEV 381_ TPGPI 386_ DTEYL 391_ FDSFF 396_ SLIKK 401_ GKATT 406_ ITSVL 411_ PKPAL 416_ VASRV 421_ EVSKV 426_ LILGS 431_ GGLSI 436_ GQAGE 441_ FDYSG 446_ SQAVK 451_ AMKEE 456_ NVKTV 461_ LMNPN 466_ IASVQ 471_ TNEVG 476_ LKQAD 481_ TVYFL 486_ PITPQ 491_ FVTEV 496_ IKAEQ 501_ PDGLI 506_ LGMGG 511_ QTALN 516_ CGVEL 521_ FKRGV 526_ LKEYG 531_ VKVLG 536_ TSVES 541_ IMATE 546_ DRQLF 551_ SDKLN 556_ EINEK 561_ IAPSF 566_ AVESI 571_ EDALK 576_ AADTI 581_ GYPVM 586_ IRSAY 591_ ALGGL 596_ GSGIC 601_ PNRET 606_ LMDLS 611_ TKAFA 616_ MTNQI 621_ LVEKS 626_ VTGWK 631_ EIEYE 636_ VVRDA 641_ DDNCV 646_ TVCNM 651_ ENVDA 656_ MGVHT 661_ GDSVV 666_ VAPAQ 671_ TLSNA 676_ EFQML 681_ RRTSI 686_ NVVRH 691_ LGIVG 696_ ECNIQ 701_ FALHP 706_ TSMEY 711_ CIIEV 716_ NARLS 721_ RSSAL 726_ ASKAT 731_ GYPLA 736_ FIAAK 741_ IALGI 746_ PLPEI 751_ KNVVS 756_ GKTSA 761_ CFEPS 766_ LDYMV 771_ TKIPR 776_ WDLDR 781_ FHGTS 786_ SRIGS 791_ SMKSV 796_ GEVMA 801_ IGRTF 806_ EESFQ 811_ KALRM 816_ CHPSI 821_ EGFTP 826_ RLPMN 831_ KEWPS 836_ NLDLR 841_ KELSE 846_ PSSTR 851_ IYAIA 856_ KAIDD 861_ NMSLD 866_ EIEKL 871_ TYIDK 876_ WFLYK 881_ MRDIL 886_ NMEKT 891_ LKGLN 896_ SESMT 901_ EETLK 906_ RAKEI 911_ GFSDK 916_ QISKC 921_ LGLTE 926_ AQTRE 931_ LRLKK 936_ NIHPW 941_ VKQID 946_ TLAAE 951_ YPSVT 956_ NYLYV 961_ TYNGQ 966_ EHDVN 971_ FDDHG 976_ MMVLG 981_ CGPYH 986_ IGSSV 991_ EFDWC 996_ AVSSI 1001_ RTLRQ 1006_ LGKKT 1011_ VVVNC 1016_ NPETV 1021_ STDFD 1026_ ECDKL 1031_ YFEEL 1036_ SLERI 1041_ LDIYH 1046_ QEACG 1051_ GCIIS 1056_ VGGQI 1061_ PNNLA 1066_ VPLYK 1071_ NGVKI 1076_ MGTSP 1081_ LQIDR 1086_ AEDRS 1091_ IFSAV 1096_ LDELK 1101_ VAQAP 1106_ WKAVN 1111_ TLNEA 1116_ LEFAK 1121_ SVDYP 1126_ CLLRP 1131_ SYVLS 1136_ GSAMN 1141_ VVFSE 1146_ DEMKK 1151_ FLEEA 1156_ TRVSQ 1161_ EHPVV 1166_ LTKFV 1171_ EGARE 1176_ VEMDA 1181_ VGKDG 1186_ RVISH 1191_ AISEH 1196_ VEDAG 1201_ VHSGD 1206_ ATLML 1211_ PTQTI 1216_ SQGAI 1221_ EKVKD 1226_ ATRKI 1231_ AKAFA 1236_ ISGPF 1241_ NVQFL 1246_ VKGND 1251_ VLVIE 1256_ CNLRA 1261_ SRSFP 1266_ FVSKT 1271_ LGVDF 1276_ IDVAT 1281_ KVMIG 1286_ ENVDE 1291_ KHLPT 1296_ LDHPI 1301_ IPADY 1306_ VAIKA 1311_ PMFSW 1316_ PRLRD 1321_ ADPIL 1326_ RCEMA 1331_ STGEV 1336_ ACFGE 1341_ GIHTA 1346_ FLKAM 1351_ LSTGF 1356_ KIPQK 1361_ GILIG 1366_ IQQSF 1371_ RPRFL 1376_ GVAEQ 1381_ LHNEG 1386_ FKLFA 1391_ TEATS 1396_ DWLNA 1401_ NNVPA 1406_ TPVAW 1411_ PSQEG 1416_ QNPSL 1421_ SSIRK 1426_ LIRDG 1431_ SIDLV 1436_ INLPN 1441_ NNTKF 1446_ VHDNY 1451_ VIRRT 1456_ AVDSG 1461_ IPLLT 1466_ NFQVT 1471_ KLFAE 1476_ AVQKS 1481_ RKVDS 1486_ KSLFH 1491_YRQYS
1: Involved in the urea cycle of ureotelic animals where the enzyme plays an important role in removing excess ammonia from the cell