Carbonic anhydrase 5A, mitochondrial (EC 4.2.1.1) (Carbonate dehydratase VA) (Carbonic anhydrase VA) (CA-VA)
1_MLGRN 6_ TWKTS 11_ AFSFL 16_ VEQMW 21_ APLWS 26_ RSMRP 31_ GRWCS 36_ QRSCA 41_ WQTSN 46_ NTLHP 51_ LWTVP 56_ VSVPG 61_ GTRQS 66_ PINIQ 71_ WRDSV 76_ YDPQL 81_ KPLRV 86_ SYEAA 91_ SCLYI 96_ WNTGY 101_ LFQVE 106_ FDDAT 111_ EASGI 116_ SGGPL 121_ ENHYR 126_ LKQFH 131_ FHWGA 136_ VNEGG 141_ SEHTV 146_ DGHAY 151_ PAELH 156_ LVHWN 161_ SVKYQ 166_ NYKEA 171_ VVGEN 176_ GLAVI 181_ GVFLK 186_ LGAHH 191_ QTLQR 196_ LVDIL 201_ PEIKH 206_ KDARA 211_ AMRPF 216_ DPSTL 221_ LPTCW 226_ DYWTY 231_ AGSLT 236_ TPPLT 241_ ESVTW 246_ IIQKE 251_ PVEVA 256_ PSQLS 261_ AFRTL 266_ LFSAL 271_ GEEEK 276_ MMVNN 281_ YRPLQ 286_ PLMNR 291_ KVWAS 296_FQATN
1: Mitochondrial carbonic anhydrase that catalyzes the reversible conversion of carbon dioxide to bicarbonate/HCO3 (PubMed:24530203, PubMed:8356065). Mitochondria are impermeable to HCO3, and thus this intramitochondrial carbonic anhydrase is pivotal in providing HCO3 for multiple mitochondrial enzymes that catalyze the formation of essential metabolites of intermediary metabolism in the urea and Krebs cycles (PubMed:24530203)