Gene name: ATN1

Uniprot entry:

P54259

Protein names:

Atrophin-1 (Dentatorubral-pallidoluysian atrophy protein)

Protein sequence:

1_MKTRQ 6_ NKDSM 11_ SMRSG 16_ RKKEA 21_ PGPRE 26_ ELRSR 31_ GRASP 36_ GGVST 41_ SSSDG 46_ KAEKS 51_ RQTAK 56_ KARVE 61_ EASTP 66_ KVNKQ 71_ GRSEE 76_ ISESE 81_ SEETN 86_ APKKT 91_ KTEQE 96_ LPRPQ 101_ SPSDL 106_ DSLDG 111_ RSLND 116_ DGSSD 121_ PRDID 126_ QDNRS 131_ TSPSI 136_ YSPGS 141_ VENDS 146_ DSSSG 151_ LSQGP 156_ ARPYH 161_ PPPLF 166_ PPSPQ 171_ PPDST 176_ PRQPE 181_ ASFEP 186_ HPSVT 191_ PTGYH 196_ APMEP 201_ PTSRM 206_ FQAPP 211_ GAPPP 216_ HPQLY 221_ PGGTG 226_ GVLSG 231_ PPMGP 236_ KGGGA 241_ ASSVG 246_ GPNGG 251_ KQHPP 256_ PTTPI 261_ SVSSS 266_ GASGA 271_ PPTKP 276_ PTTPV 281_ GGGNL 286_ PSAPP 291_ PANFP 296_ HVTPN 301_ LPPPP 306_ ALRPL 311_ NNASA 316_ SPPGL 321_ GAQPL 326_ PGHLP 331_ SPHAM 336_ GQGMG 341_ GLPPG 346_ PEKGP 351_ TLAPS 356_ PHSLP 361_ PASSS 366_ APAPP 371_ MRFPY 376_ SSSSS 381_ SSAAA 386_ SSSSS 391_ SSSSS 396_ ASPFP 401_ ASQAL 406_ PSYPH 411_ SFPPP 416_ TSLSV 421_ SNQPP 426_ KYTQP 431_ SLPSQ 436_ AVWSQ 441_ GPPPP 446_ PPYGR 451_ LLANS 456_ NAHPG 461_ PFPPS 466_ TGAQS 471_ TAHPP 476_ VSTHH 481_ HHHQQ 486_ QQQQQ 491_ QQQQQ 496_ QQQQQ 501_ QQHHG 506_ NSGPP 511_ PPGAF 516_ PHPLE 521_ GGSSH 526_ HAHPY 531_ AMSPS 536_ LGSLR 541_ PYPPG 546_ PAHLP 551_ PPHSQ 556_ VSYSQ 561_ AGPNG 566_ PPVSS 571_ SSNSS 576_ SSTSQ 581_ GSYPC 586_ SHPSP 591_ SQGPQ 596_ GAPYP 601_ FPPVP 606_ TVTTS 611_ SATLS 616_ TVIAT 621_ VASSP 626_ AGYKT 631_ ASPPG 636_ PPPYG 641_ KRAPS 646_ PGAYK 651_ TATPP 656_ GYKPG 661_ SPPSF 666_ RTGTP 671_ PGYRG 676_ TSPPA 681_ GPGTF 686_ KPGSP 691_ TVGPG 696_ PLPPA 701_ GPSGL 706_ PSLPP 711_ PPAAP 716_ ASGPP 721_ LSATQ 726_ IKQEP 731_ AEEYE 736_ TPESP 741_ VPPAR 746_ SPSPP 751_ PKVVD 756_ VPSHA 761_ SQSAR 766_ FNKHL 771_ DRGFN 776_ SCARS 781_ DLYFV 786_ PLEGS 791_ KLAKK 796_ RADLV 801_ EKVRR 806_ EAEQR 811_ AREEK 816_ ERERE 821_ REREK 826_ ERERE 831_ KEREL 836_ ERSVK 841_ LAQEG 846_ RAPVE 851_ CPSLG 856_ PVPHR 861_ PPFEP 866_ GSAVA 871_ TVPPY 876_ LGPDT 881_ PALRT 886_ LSEYA 891_ RPHVM 896_ SPGNR 901_ NHPFY 906_ VPLGA 911_ VDPGL 916_ LGYNV 921_ PALYS 926_ SDPAA 931_ RERER 936_ EARER 941_ DLRDR 946_ LKPGF 951_ EVKPS 956_ ELEPL 961_ HGVPG 966_ PGLDP 971_ FPRHG 976_ GLALQ 981_ PGPPG 986_ LHPFP 991_ FHPSL 996_ GPLER 1001_ ERLAL 1006_ AAGPA 1011_ LRPDM 1016_ SYAER 1021_ LAAER 1026_ QHAER 1031_ VAALG 1036_ NDPLA 1041_ RLQML 1046_ NVTPH 1051_ HHQHS 1056_ HIHSH 1061_ LHLHQ 1066_ QDAIH 1071_ AASAS 1076_ VHPLI 1081_ DPLAS 1086_ GSHLT 1091_ RIPYP 1096_ AGTLP 1101_ NPLLP 1106_ HPLHE 1111_ NEVLR 1116_ HQLFA 1121_ APYRD 1126_ LPASL 1131_ SAPMS 1136_ AAHQL 1141_ QAMHA 1146_ QSAEL 1151_ QRLAL 1156_ EQQQW 1161_ LHAHH 1166_ PLHSV 1171_ PLPAQ 1176_ EDYYS 1181_HLKKE

Protein annotations

Protein functions:

1: Transcriptional corepressor. Recruits NR2E1 to repress transcription. Promotes vascular smooth cell (VSMC) migration and orientation (By similarity). Corepressor of MTG8 transcriptional repression. Has some intrinsic repression activity which is independent of the number of poly-Gln (polyQ) repeats