4-aminobutyrate aminotransferase, mitochondrial (EC 2.6.1.19) ((S)-3-amino-2-methylpropionate transaminase) (EC 2.6.1.22) (GABA aminotransferase) (GABA-AT) (Gamma-amino-N-butyrate transaminase) (GABA transaminase) (GABA-T) (L-AIBAT)
1_MASML 6_ LAQRL 11_ ACSFQ 16_ HSYRL 21_ LVPGS 26_ RHISQ 31_ AAAKV 36_ DVEFD 41_ YDGPL 46_ MKTEV 51_ PGPRS 56_ QELMK 61_ QLNII 66_ QNAEA 71_ VHFFC 76_ NYEES 81_ RGNYL 86_ VDVDG 91_ NRMLD 96_ LYSQI 101_ SSVPI 106_ GYSHP 111_ ALLKL 116_ IQQPQ 121_ NASMF 126_ VNRPA 131_ LGILP 136_ PENFV 141_ EKLRQ 146_ SLLSV 151_ APKGM 156_ SQLIT 161_ MACGS 166_ CSNEN 171_ ALKTI 176_ FMWYR 181_ SKERG 186_ QRGFS 191_ QEELE 196_ TCMIN 201_ QAPGC 206_ PDYSI 211_ LSFMG 216_ AFHGR 221_ TMGCL 226_ ATTHS 231_ KAIHK 236_ IDIPS 241_ FDWPI 246_ APFPR 251_ LKYPL 256_ EEFVK 261_ ENQQE 266_ EARCL 271_ EEVED 276_ LIVKY 281_ RKKKK 286_ TVAGI 291_ IVEPI 296_ QSEGG 301_ DNHAS 306_ DDFFR 311_ KLRDI 316_ ARKHG 321_ CAFLV 326_ DEVQT 331_ GGGCT 336_ GKFWA 341_ HEHWG 346_ LDDPA 351_ DVMTF 356_ SKKMM 361_ TGGFF 366_ HKEEF 371_ RPNAP 376_ YRIFN 381_ TWLGD 386_ PSKNL 391_ LLAEV 396_ INIIK 401_ REDLL 406_ NNAAH 411_ AGKAL 416_ LTGLL 421_ DLQAR 426_ YPQFI 431_ SRVRG 436_ RGTFC 441_ SFDTP 446_ DDSIR 451_ NKLIL 456_ IARNK 461_ GVVLG 466_ GCGDK 471_ SIRFR 476_ PTLVF 481_ RDHHA 486_ HLFLN 491_IFSDI
1: Catalyzes the conversion of gamma-aminobutyrate and L-beta-aminoisobutyrate to succinate semialdehyde and methylmalonate semialdehyde, respectively (PubMed:10407778, PubMed:15528998). Can also convert delta-aminovalerate and beta-alanine (By similarity)