Polycystin-1 (PC1) (Autosomal dominant polycystic kidney disease 1 protein)
1_MPPAA 6_ PARLA 11_ LALGL 16_ GLWLG 21_ ALAGG 26_ PGRGC 31_ GPCEP 36_ PCLCG 41_ PAPGA 46_ ACRVN 51_ CSGRG 56_ LRTLG 61_ PALRI 66_ PADAT 71_ ALDVS 76_ HNLLR 81_ ALDVG 86_ LLANL 91_ SALAE 96_ LDISN 101_ NKIST 106_ LEEGI 111_ FANLF 116_ NLSEI 121_ NLSGN 126_ PFECD 131_ CGLAW 136_ LPRWA 141_ EEQQV 146_ RVVQP 151_ EAATC 156_ AGPGS 161_ LAGQP 166_ LLGIP 171_ LLDSG 176_ CGEEY 181_ VACLP 186_ DNSSG 191_ TVAAV 196_ SFSAA 201_ HEGLL 206_ QPEAC 211_ SAFCF 216_ STGQG 221_ LAALS 226_ EQGWC 231_ LCGAA 236_ QPSSA 241_ SFACL 246_ SLCSG 251_ PPPPP 256_ APTCR 261_ GPTLL 266_ QHVFP 271_ ASPGA 276_ TLVGP 281_ HGPLA 286_ SGQLA 291_ AFHIA 296_ APLPV 301_ TATRW 306_ DFGDG 311_ SAEVD 316_ AAGPA 321_ ASHRY 326_ VLPGR 331_ YHVTA 336_ VLALG 341_ AGSAL 346_ LGTDV 351_ QVEAA 356_ PAALE 361_ LVCPS 366_ SVQSD 371_ ESLDL 376_ SIQNR 381_ GGSGL 386_ EAAYS 391_ IVALG 396_ EEPAR 401_ AVHPL 406_ CPSDT 411_ EIFPG 416_ NGHCY 421_ RLVVE 426_ KAAWL 431_ QAQEQ 436_ CQAWA 441_ GAALA 446_ MVDSP 451_ AVQRF 456_ LVSRV 461_ TRSLD 466_ VWIGF 471_ STVQG 476_ VEVGP 481_ APQGE 486_ AFSLE 491_ SCQNW 496_ LPGEP 501_ HPATA 506_ EHCVR 511_ LGPTG 516_ WCNTD 521_ LCSAP 526_ HSYVC 531_ ELQPG 536_ GPVQD 541_ AENLL 546_ VGAPS 551_ GDLQG 556_ PLTPL 561_ AQQDG 566_ LSAPH 571_ EPVEV 576_ MVFPG 581_ LRLSR 586_ EAFLT 591_ TAEFG 596_ TQELR 601_ RPAQL 606_ RLQVY 611_ RLLST 616_ AGTPE 621_ NGSEP 626_ ESRSP 631_ DNRTQ 636_ LAPAC 641_ MPGGR 646_ WCPGA 651_ NICLP 656_ LDASC 661_ HPQAC 666_ ANGCT 671_ SGPGL 676_ PGAPY 681_ ALWRE 686_ FLFSV 691_ PAGPP 696_ AQYSV 701_ TLHGQ 706_ DVLML 711_ PGDLV 716_ GLQHD 721_ AGPGA 726_ LLHCS 731_ PAPGH 736_ PGPRA 741_ PYLSA 746_ NASSW 751_ LPHLP 756_ AQLEG 761_ TWACP 766_ ACALR 771_ LLAAT 776_ EQLTV 781_ LLGLR 786_ PNPGL 791_ RLPGR 796_ YEVRA 801_ EVGNG 806_ VSRHN 811_ LSCSF 816_ DVVSP 821_ VAGLR 826_ VIYPA 831_ PRDGR 836_ LYVPT 841_ NGSAL 846_ VLQVD 851_ SGANA 856_ TATAR 861_ WPGGS 866_ VSARF 871_ ENVCP 876_ ALVAT 881_ FVPGC 886_ PWETN 891_ DTLFS 896_ VVALP 901_ WLSEG 906_ EHVVD 911_ VVVEN 916_ SASRA 921_ NLSLR 926_ VTAEE 931_ PICGL 936_ RATPS 941_ PEARV 946_ LQGVL 951_ VRYSP 956_ VVEAG 961_ SDMVF 966_ RWTIN 971_ DKQSL 976_ TFQNV 981_ VFNVI 986_ YQSAA 991_ VFKLS 996_ LTASN 1001_ HVSNV 1006_ TVNYN 1011_ VTVER 1016_ MNRMQ 1021_ GLQVS 1026_ TVPAV 1031_ LSPNA 1036_ TLALT 1041_ AGVLV 1046_ DSAVE 1051_ VAFLW 1056_ TFGDG 1061_ EQALH 1066_ QFQPP 1071_ YNESF 1076_ PVPDP 1081_ SVAQV 1086_ LVEHN 1091_ VMHTY 1096_ AAPGE 1101_ YLLTV 1106_ LASNA 1111_ FENLT 1116_ QQVPV 1121_ SVRAS 1126_ LPSVA 1131_ VGVSD 1136_ GVLVA 1141_ GRPVT 1146_ FYPHP 1151_ LPSPG 1156_ GVLYT 1161_ WDFGD 1166_ GSPVL 1171_ TQSQP 1176_ AANHT 1181_ YASRG 1186_ TYHVR 1191_ LEVNN 1196_ TVSGA 1201_ AAQAD 1206_ VRVFE 1211_ ELRGL 1216_ SVDMS 1221_ LAVEQ 1226_ GAPVV 1231_ VSAAV 1236_ QTGDN 1241_ ITWTF 1246_ DMGDG 1251_ TVLSG 1256_ PEATV 1261_ EHVYL 1266_ RAQNC 1271_ TVTVG 1276_ AASPA 1281_ GHLAR 1286_ SLHVL 1291_ VFVLE 1296_ VLRVE 1301_ PAACI 1306_ PTQPD 1311_ ARLTA 1316_ YVTGN 1321_ PAHYL 1326_ FDWTF 1331_ GDGSS 1336_ NTTVR 1341_ GCPTV 1346_ THNFT 1351_ RSGTF 1356_ PLALV 1361_ LSSRV 1366_ NRAHY 1371_ FTSIC 1376_ VEPEV 1381_ GNVTL 1386_ QPERQ 1391_ FVQLG 1396_ DEAWL 1401_ VACAW 1406_ PPFPY 1411_ RYTWD 1416_ FGTEE 1421_ AAPTR 1426_ ARGPE 1431_ VTFIY 1436_ RDPGS 1441_ YLVTV 1446_ TASNN 1451_ ISAAN 1456_ DSALV 1461_ EVQEP 1466_ VLVTS 1471_ IKVNG 1476_ SLGLE 1481_ LQQPY 1486_ LFSAV 1491_ GRGRP 1496_ ASYLW 1501_ DLGDG 1506_ GWLEG 1511_ PEVTH 1516_ AYNST 1521_ GDFTV 1526_ RVAGW 1531_ NEVSR 1536_ SEAWL 1541_ NVTVK 1546_ RRVRG 1551_ LVVNA 1556_ SRTVV 1561_ PLNGS 1566_ VSFST 1571_ SLEAG 1576_ SDVRY 1581_ SWVLC 1586_ DRCTP 1591_ IPGGP 1596_ TISYT 1601_ FRSVG 1606_ TFNII 1611_ VTAEN 1616_ EVGSA 1621_ QDSIF 1626_ VYVLQ 1631_ LIEGL 1636_ QVVGG 1641_ GRYFP 1646_ TNHTV 1651_ QLQAV 1656_ VRDGT 1661_ NVSYS 1666_ WTAWR 1671_ DRGPA 1676_ LAGSG 1681_ KGFSL 1686_ TVLEA 1691_ GTYHV 1696_ QLRAT 1701_ NMLGS 1706_ AWADC 1711_ TMDFV 1716_ EPVGW 1721_ LMVAA 1726_ SPNPA 1731_ AVNTS 1736_ VTLSA 1741_ ELAGG 1746_ SGVVY 1751_ TWSLE 1756_ EGLSW 1761_ ETSEP 1766_ FTTHS 1771_ FPTPG 1776_ LHLVT 1781_ MTAGN 1786_ PLGSA 1791_ NATVE 1796_ VDVQV 1801_ PVSGL 1806_ SIRAS 1811_ EPGGS 1816_ FVAAG 1821_ SSVPF 1826_ WGQLA 1831_ TGTNV 1836_ SWCWA 1841_ VPGGS 1846_ SKRGP 1851_ HVTMV 1856_ FPDAG 1861_ TFSIR 1866_ LNASN 1871_ AVSWV 1876_ SATYN 1881_ LTAEE 1886_ PIVGL 1891_ VLWAS 1896_ SKVVA 1901_ PGQLV 1906_ HFQIL 1911_ LAAGS 1916_ AVTFR 1921_ LQVGG 1926_ ANPEV 1931_ LPGPR 1936_ FSHSF 1941_ PRVGD 1946_ HVVSV 1951_ RGKNH 1956_ VSWAQ 1961_ AQVRI 1966_ VVLEA 1971_ VSGLQ 1976_ VPNCC 1981_ EPGIA 1986_ TGTER 1991_ NFTAR 1996_ VQRGS 2001_ RVAYA 2006_ WYFSL 2011_ QKVQG 2016_ DSLVI 2021_ LSGRD 2026_ VTYTP 2031_ VAAGL 2036_ LEIQV 2041_ RAFNA 2046_ LGSEN 2051_ RTLVL 2056_ EVQDA 2061_ VQYVA 2066_ LQSGP 2071_ CFTNR 2076_ SAQFE 2081_ AATSP 2086_ SPRRV 2091_ AYHWD 2096_ FGDGS 2101_ PGQDT 2106_ DEPRA 2111_ EHSYL 2116_ RPGDY 2121_ RVQVN 2126_ ASNLV 2131_ SFFVA 2136_ QATVT 2141_ VQVLA 2146_ CREPE 2151_ VDVVL 2156_ PLQVL 2161_ MRRSQ 2166_ RNYLE 2171_ AHVDL 2176_ RDCVT 2181_ YQTEY 2186_ RWEVY 2191_ RTASC 2196_ QRPGR 2201_ PARVA 2206_ LPGVD 2211_ VSRPR 2216_ LVLPR 2221_ LALPV 2226_ GHYCF 2231_ VFVVS 2236_ FGDTP 2241_ LTQSI 2246_ QANVT 2251_ VAPER 2256_ LVPII 2261_ EGGSY 2266_ RVWSD 2271_ TRDLV 2276_ LDGSE 2281_ SYDPN 2286_ LEDGD 2291_ QTPLS 2296_ FHWAC 2301_ VASTQ 2306_ REAGG 2311_ CALNF 2316_ GPRGS 2321_ STVTI 2326_ PRERL 2331_ AAGVE 2336_ YTFSL 2341_ TVWKA 2346_ GRKEE 2351_ ATNQT 2356_ VLIRS 2361_ GRVPI 2366_ VSLEC 2371_ VSCKA 2376_ QAVYE 2381_ VSRSS 2386_ YVYLE 2391_ GRCLN 2396_ CSSGS 2401_ KRGRW 2406_ AARTF 2411_ SNKTL 2416_ VLDET 2421_ TTSTG 2426_ SAGMR 2431_ LVLRR 2436_ GVLRD 2441_ GEGYT 2446_ FTLTV 2451_ LGRSG 2456_ EEEGC 2461_ ASIRL 2466_ SPNRP 2471_ PLGGS 2476_ CRLFP 2481_ LGAVH 2486_ ALTTK 2491_ VHFEC 2496_ TGWHD 2501_ AEDAG 2506_ APLVY 2511_ ALLLR 2516_ RCRQG 2521_ HCEEF 2526_ CVYKG 2531_ SLSSY 2536_ GAVLP 2541_ PGFRP 2546_ HFEVG 2551_ LAVVV 2556_ QDQLG 2561_ AAVVA 2566_ LNRSL 2571_ AITLP 2576_ EPNGS 2581_ ATGLT 2586_ VWLHG 2591_ LTASV 2596_ LPGLL 2601_ RQADP 2606_ QHVIE 2611_ YSLAL 2616_ VTVLN 2621_ EYERA 2626_ LDVAA 2631_ EPKHE 2636_ RQHRA 2641_ QIRKN 2646_ ITETL 2651_ VSLRV 2656_ HTVDD 2661_ IQQIA 2666_ AALAQ 2671_ CMGPS 2676_ RELVC 2681_ RSCLK 2686_ QTLHK 2691_ LEAMM 2696_ LILQA 2701_ ETTAG 2706_ TVTPT 2711_ AIGDS 2716_ ILNIT 2721_ GDLIH 2726_ LASSD 2731_ VRAPQ 2736_ PSELG 2741_ AESPS 2746_ RMVAS 2751_ QAYNL 2756_ TSALM 2761_ RILMR 2766_ SRVLN 2771_ EEPLT 2776_ LAGEE 2781_ IVAQG 2786_ KRSDP 2791_ RSLLC 2796_ YGGAP 2801_ GPGCH 2806_ FSIPE 2811_ AFSGA 2816_ LANLS 2821_ DVVQL 2826_ IFLVD 2831_ SNPFP 2836_ FGYIS 2841_ NYTVS 2846_ TKVAS 2851_ MAFQT 2856_ QAGAQ 2861_ IPIER 2866_ LASER 2871_ AITVK 2876_ VPNNS 2881_ DWAAR 2886_ GHRSS 2891_ ANSAN 2896_ SVVVQ 2901_ PQASV 2906_ GAVVT 2911_ LDSSN 2916_ PAAGL 2921_ HLQLN 2926_ YTLLD 2931_ GHYLS 2936_ EEPEP 2941_ YLAVY 2946_ LHSEP 2951_ RPNEH 2956_ NCSAS 2961_ RRIRP 2966_ ESLQG 2971_ ADHRP 2976_ YTFFI 2981_ SPGSR 2986_ DPAGS 2991_ YHLNL 2996_ SSHFR 3001_ WSALQ 3006_ VSVGL 3011_ YTSLC 3016_ QYFSE 3021_ EDMVW 3026_ RTEGL 3031_ LPLEE 3036_ TSPRQ 3041_ AVCLT 3046_ RHLTA 3051_ FGASL 3056_ FVPPS 3061_ HVRFV 3066_ FPEPT 3071_ ADVNY 3076_ IVMLT 3081_ CAVCL 3086_ VTYMV 3091_ MAAIL 3096_ HKLDQ 3101_ LDASR 3106_ GRAIP 3111_ FCGQR 3116_ GRFKY 3121_ EILVK 3126_ TGWGR 3131_ GSGTT 3136_ AHVGI 3141_ MLYGV 3146_ DSRSG 3151_ HRHLD 3156_ GDRAF 3161_ HRNSL 3166_ DIFRI 3171_ ATPHS 3176_ LGSVW 3181_ KIRVW 3186_ HDNKG 3191_ LSPAW 3196_ FLQHV 3201_ IVRDL 3206_ QTARS 3211_ AFFLV 3216_ NDWLS 3221_ VETEA 3226_ NGGLV 3231_ EKEVL 3236_ AASDA 3241_ ALLRF 3246_ RRLLV 3251_ AELQR 3256_ GFFDK 3261_ HIWLS 3266_ IWDRP 3271_ PRSRF 3276_ TRIQR 3281_ ATCCV 3286_ LLICL 3291_ FLGAN 3296_ AVWYG 3301_ AVGDS 3306_ AYSTG 3311_ HVSRL 3316_ SPLSV 3321_ DTVAV 3326_ GLVSS 3331_ VVVYP 3336_ VYLAI 3341_ LFLFR 3346_ MSRSK 3351_ VAGSP 3356_ SPTPA 3361_ GQQVL 3366_ DIDSC 3371_ LDSSV 3376_ LDSSF 3381_ LTFSG 3386_ LHAEQ 3391_ AFVGQ 3396_ MKSDL 3401_ FLDDS 3406_ KSLVC 3411_ WPSGE 3416_ GTLSW 3421_ PDLLS 3426_ DPSIV 3431_ GSNLR 3436_ QLARG 3441_ QAGHG 3446_ LGPEE 3451_ DGFSL 3456_ ASPYS 3461_ PAKSF 3466_ SASDE 3471_ DLIQQ 3476_ VLAEG 3481_ VSSPA 3486_ PTQDT 3491_ HMETD 3496_ LLSSL 3501_ SSTPG 3506_ EKTET 3511_ LALQR 3516_ LGELG 3521_ PPSPG 3526_ LNWEQ 3531_ PQAAR 3536_ LSRTG 3541_ LVEGL 3546_ RKRLL 3551_ PAWCA 3556_ SLAHG 3561_ LSLLL 3566_ VAVAV 3571_ AVSGW 3576_ VGASF 3581_ PPGVS 3586_ VAWLL 3591_ SSSAS 3596_ FLASF 3601_ LGWEP 3606_ LKVLL 3611_ EALYF 3616_ SLVAK 3621_ RLHPD 3626_ EDDTL 3631_ VESPA 3636_ VTPVS 3641_ ARVPR 3646_ VRPPH 3651_ GFALF 3656_ LAKEE 3661_ ARKVK 3666_ RLHGM 3671_ LRSLL 3676_ VYMLF 3681_ LLVTL 3686_ LASYG 3691_ DASCH 3696_ GHAYR 3701_ LQSAI 3706_ KQELH 3711_ SRAFL 3716_ AITRS 3721_ EELWP 3726_ WMAHV 3731_ LLPYV 3736_ HGNQS 3741_ SPELG 3746_ PPRLR 3751_ QVRLQ 3756_ EALYP 3761_ DPPGP 3766_ RVHTC 3771_ SAAGG 3776_ FSTSD 3781_ YDVGW 3786_ ESPHN 3791_ GSGTW 3796_ AYSAP 3801_ DLLGA 3806_ WSWGS 3811_ CAVYD 3816_ SGGYV 3821_ QELGL 3826_ SLEES 3831_ RDRLR 3836_ FLQLH 3841_ NWLDN 3846_ RSRAV 3851_ FLELT 3856_ RYSPA 3861_ VGLHA 3866_ AVTLR 3871_ LEFPA 3876_ AGRAL 3881_ AALSV 3886_ RPFAL 3891_ RRLSA 3896_ GLSLP 3901_ LLTSV 3906_ CLLLF 3911_ AVHFA 3916_ VAEAR 3921_ TWHRE 3926_ GRWRV 3931_ LRLGA 3936_ WARWL 3941_ LVALT 3946_ AATAL 3951_ VRLAQ 3956_ LGAAD 3961_ RQWTR 3966_ FVRGR 3971_ PRRFT 3976_ SFDQV 3981_ AQLSS 3986_ AARGL 3991_ AASLL 3996_ FLLLV 4001_ KAAQQ 4006_ LRFVR 4011_ QWSVF 4016_ GKTLC 4021_ RALPE 4026_ LLGVT 4031_ LGLVV 4036_ LGVAY 4041_ AQLAI 4046_ LLVSS 4051_ CVDSL 4056_ WSVAQ 4061_ ALLVL 4066_ CPGTG 4071_ LSTLC 4076_ PAESW 4081_ HLSPL 4086_ LCVGL 4091_ WALRL 4096_ WGALR 4101_ LGAVI 4106_ LRWRY 4111_ HALRG 4116_ ELYRP 4121_ AWEPQ 4126_ DYEMV 4131_ ELFLR 4136_ RLRLW 4141_ MGLSK 4146_ VKEFR 4151_ HKVRF 4156_ EGMEP 4161_ LPSRS 4166_ SRGSK 4171_ VSPDV 4176_ PPPSA 4181_ GSDAS 4186_ HPSTS 4191_ SSQLD 4196_ GLSVS 4201_ LGRLG 4206_ TRCEP 4211_ EPSRL 4216_ QAVFE 4221_ ALLTQ 4226_ FDRLN 4231_ QATED 4236_ VYQLE 4241_ QQLHS 4246_ LQGRR 4251_ SSRAP 4256_ AGSSR 4261_ GPSPG 4266_ LRPAL 4271_ PSRLA 4276_ RASRG 4281_ VDLAT 4286_ GPSRT 4291_ PLRAK 4296_NKVHP
1: Component of a heteromeric calcium-permeable ion channel formed by PKD1 and PKD2 that is activated by interaction between PKD1 and a Wnt family member, such as WNT3A and WNT9B (PubMed:27214281). Both PKD1 and PKD2 are required for channel activity (PubMed:27214281). Involved in renal tubulogenesis (PubMed:12482949). Involved in fluid-flow mechanosensation by the primary cilium in renal epithelium (By similarity). Acts as a regulator of cilium length, together with PKD2 (By similarity). The dynamic control of cilium length is essential in the regulation of mechanotransductive signaling (By similarity). The cilium length response creates a negative feedback loop whereby fluid shear-mediated deflection of the primary cilium, which decreases intracellular cAMP, leads to cilium shortening and thus decreases flow-induced signaling (By similarity). May be an ion-channel regulator. Involved in adhesive protein-protein and protein-carbohydrate interactions. Likely to be involved with polycystin-1-interacting protein 1 in the detection, sequestration and exocytosis of senescent mitochondria (PubMed:37681898)