Procollagen-lysine,2-oxoglutarate 5-dioxygenase 1 (EC 1.14.11.4) (Lysyl hydroxylase 1) (LH1)
1_MRPLL 6_ LLALL 11_ GWLLL 16_ AEAKG 21_ DAKPE 26_ DNLLV 31_ LTVAT 36_ KETEG 41_ FRRFK 46_ RSAQF 51_ FNYKI 56_ QALGL 61_ GEDWN 66_ VEKGT 71_ SAGGG 76_ QKVRL 81_ LKKAL 86_ EKHAD 91_ KEDLV 96_ ILFAD 101_ SYDVL 106_ FASGP 111_ RELLK 116_ KFRQA 121_ RSQVV 126_ FSAEE 131_ LIYPD 136_ RRLET 141_ KYPVV 146_ SDGKR 151_ FLGSG 156_ GFIGY 161_ APNLS 166_ KLVAE 171_ WEGQD 176_ SDSDQ 181_ LFYTK 186_ IFLDP 191_ EKREQ 196_ INITL 201_ DHRCR 206_ IFQNL 211_ DGALD 216_ EVVLK 221_ FEMGH 226_ VRARN 231_ LAYDT 236_ LPVLI 241_ HGNGP 246_ TKLQL 251_ NYLGN 256_ YIPRF 261_ WTFET 266_ GCTVC 271_ DEGLR 276_ SLKGI 281_ GDEAL 286_ PTVLV 291_ GVFIE 296_ QPTPF 301_ VSLFF 306_ QRLLR 311_ LHYPQ 316_ KHMRL 321_ FIHNH 326_ EQHHK 331_ AQVEE 336_ FLAQH 341_ GSEYQ 346_ SVKLV 351_ GPEVR 356_ MANAD 361_ ARNMG 366_ ADLCR 371_ QDRSC 376_ TYYFS 381_ VDADV 386_ ALTEP 391_ NSLRL 396_ LIQQN 401_ KNVIA 406_ PLMTR 411_ HGRLW 416_ SNFWG 421_ ALSAD 426_ GYYAR 431_ SEDYV 436_ DIVQG 441_ RRVGV 446_ WNVPY 451_ ISNIY 456_ LIKGS 461_ ALRGE 466_ LQSSD 471_ LFHHS 476_ KLDPD 481_ MAFCA 486_ NIRQQ 491_ DVFMF 496_ LTNRH 501_ TLGHL 506_ LSLDS 511_ YRTTH 516_ LHNDL 521_ WEVFS 526_ NPEDW 531_ KEKYI 536_ HQNYT 541_ KALAG 546_ KLVET 551_ PCPDV 556_ YWFPI 561_ FTEVA 566_ CDELV 571_ EEMEH 576_ FGQWS 581_ LGNNK 586_ DNRIQ 591_ GGYEN 596_ VPTID 601_ IHMNQ 606_ IGFER 611_ EWHKF 616_ LLEYI 621_ APMTE 626_ KLYPG 631_ YYTRA 636_ QFDLA 641_ FVVRY 646_ KPDEQ 651_ PSLMP 656_ HHDAS 661_ TFTIN 666_ IALNR 671_ VGVDY 676_ EGGGC 681_ RFLRY 686_ NCSIR 691_ APRKG 696_ WTLMH 701_ PGRLT 706_ HYHEG 711_ LPTTR 716_ GTRYI 721_AVSFV
1: Part of a complex composed of PLOD1, P3H3 and P3H4 that catalyzes hydroxylation of lysine residues in collagen alpha chains and is required for normal assembly and cross-linkling of collagen fibrils (By similarity). Forms hydroxylysine residues in -Xaa-Lys-Gly- sequences in collagens (PubMed:10686424, PubMed:15854030, PubMed:8621606). These hydroxylysines serve as sites of attachment for carbohydrate units and are essential for the stability of the intermolecular collagen cross-links (Probable)