Treacle protein (Treacher Collins syndrome protein)
1_MAEAR 6_ KRREL 11_ LPLIY 16_ HHLLR 21_ AGYVR 26_ AAREV 31_ KEQSG 36_ QKCFL 41_ AQPVT 46_ LLDIY 51_ THWQQ 56_ TSELG 61_ RKRKA 66_ EEDAA 71_ LQAKK 76_ TRVSD 81_ PISTS 86_ ESSEE 91_ EEEAE 96_ AETAK 101_ ATPRL 106_ ASTNS 111_ SVLGA 116_ DLPSS 121_ MKEKA 126_ KAETE 131_ KAGKT 136_ GNSMP 141_ HPATG 146_ KTVAN 151_ LLSGK 156_ SPRKS 161_ AEPSA 166_ NTTLV 171_ SETEE 176_ EGSVP 181_ AFGAA 186_ AKPGM 191_ VSAGQ 196_ ADSSS 201_ EDTSS 206_ SSDET 211_ DVEGK 216_ PSVKP 221_ AQVKA 226_ SSVST 231_ KESPA 236_ RKAAP 241_ APGKV 246_ GDVTP 251_ QVKGG 256_ ALPPA 261_ KRAKK 266_ PEEES 271_ ESSEE 276_ GSESE 281_ EEAPA 286_ GTRSQ 291_ VKASE 296_ KILQV 301_ RAASA 306_ PAKGT 311_ PGKGA 316_ TPAPP 321_ GKAGA 326_ VASQT 331_ KAGKP 336_ EEDSE 341_ SSSEE 346_ SSDSE 351_ EETPA 356_ AKALL 361_ QAKAS 366_ GKTSQ 371_ VGAAS 376_ APAKE 381_ SPRKG 386_ AAPAP 391_ PGKTG 396_ PAVAK 401_ AQAGK 406_ REEDS 411_ QSSSE 416_ ESDSE 421_ EEAPA 426_ QAKPS 431_ GKAPQ 436_ VRAAS 441_ APAKE 446_ SPRKG 451_ AAPAP 456_ PRKTG 461_ PAAAQ 466_ VQVGK 471_ QEEDS 476_ RSSSE 481_ ESDSD 486_ REALA 491_ AMNAA 496_ QVKPL 501_ GKSPQ 506_ VKPAS 511_ TMGMG 516_ PLGKG 521_ AGPVP 526_ PGKVG 531_ PATPS 536_ AQVGK 541_ WEEDS 546_ ESSSE 551_ ESSDS 556_ SDGEV 561_ PTAVA 566_ PAQEK 571_ SLGNI 576_ LQAKP 581_ TSSPA 586_ KGPPQ 591_ KAGPV 596_ AVQVK 601_ AEKPM 606_ DNSES 611_ SEESS 616_ DSADS 621_ EEAPA 626_ AMTAA 631_ QAKPA 636_ LKIPQ 641_ TKACP 646_ KKTNT 651_ TASAK 656_ VAPVR 661_ VGTQA 666_ PRKAG 671_ TATSP 676_ AGSSP 681_ AVAGG 686_ TQRPA 691_ EDSSS 696_ SEESD 701_ SEEEK 706_ TGLAV 711_ TVGQA 716_ KSVGK 721_ GLQVK 726_ AASVP 731_ VKGSL 736_ GQGTA 741_ PVLPG 746_ KTGPT 751_ VTQVK 756_ AEKQE 761_ DSESS 766_ EEESD 771_ SEEAA 776_ ASPAQ 781_ VKTSV 786_ KKTQA 791_ KANPA 796_ AARAP 801_ SAKGT 806_ ISAPG 811_ KVVTA 816_ AAQAK 821_ QRSPS 826_ KVKPP 831_ VRNPQ 836_ NSTVL 841_ ARGPA 846_ SVPSV 851_ GKAVA 856_ TAAQA 861_ QTGPE 866_ EDSGS 871_ SEEES 876_ DSEEE 881_ AETLA 886_ QVKPS 891_ GKTHQ 896_ IRAAL 901_ APAKE 906_ SPRKG 911_ AAPTP 916_ PGKTG 921_ PSAAQ 926_ AGKQD 931_ DSGSS 936_ SEESD 941_ SDGEA 946_ PAAVT 951_ SAQVI 956_ KPPLI 961_ FVDPN 966_ RSPAG 971_ PAATP 976_ AQAQA 981_ ASTPR 986_ KARAS 991_ ESTAR 996_ SSSSE 1001_ SEDED 1006_ VIPAT 1011_ QCLTP 1016_ GIRTN 1021_ VVTMP 1026_ TAHPR 1031_ IAPKA 1036_ SMAGA 1041_ SSSKE 1046_ SSRIS 1051_ DGKKQ 1056_ EGPAT 1061_ QVSKK 1066_ NPASL 1071_ PLTQA 1076_ ALKVL 1081_ AQKAS 1086_ EAQPP 1091_ VARTQ 1096_ PSSGV 1101_ DSAVG 1106_ TLPAT 1111_ SPQST 1116_ SVQAK 1121_ GTNKL 1126_ RKPKL 1131_ PEVQQ 1136_ ATKAP 1141_ ESSDD 1146_ SEDSS 1151_ DSSSG 1156_ SEEDG 1161_ EGPQG 1166_ AKSAH 1171_ TLGPT 1176_ PSRTE 1181_ TLVEE 1186_ TAAES 1191_ SEDDV 1196_ VAPSQ 1201_ SLLSG 1206_ YMTPG 1211_ LTPAN 1216_ SQASK 1221_ ATPKL 1226_ DSSPS 1231_ VSSTL 1236_ AAKDD 1241_ PDGKQ 1246_ EAKPQ 1251_ QAAGM 1256_ LSPKT 1261_ GGKEA 1266_ ASGTT 1271_ PQKSR 1276_ KPKKG 1281_ AGNPQ 1286_ ASTLA 1291_ LQSNI 1296_ TQCLL 1301_ GQPWP 1306_ LNEAQ 1311_ VQASV 1316_ VKVLT 1321_ ELLEQ 1326_ ERKKV 1331_ VDTTK 1336_ ESSRK 1341_ GWESR 1346_ KRKLS 1351_ GDQPA 1356_ ARTPR 1361_ SKKKK 1366_ KLGAG 1371_ EGGEA 1376_ SVSPE 1381_ KTSTT 1386_ SKGKA 1391_ KRDKA 1396_ SGDVK 1401_ EKKGK 1406_ GSLGS 1411_ QGAKD 1416_ EPEEE 1421_ LQKGM 1426_ GTVEG 1431_ GDQSN 1436_ PKSKK 1441_ EKKKS 1446_ DKRKK 1451_ DKEKK 1456_ EKKKK 1461_ AKKAS 1466_ TKDSE 1471_ SPSQK 1476_ KKKKK 1481_KKTAE
1: Nucleolar protein that acts as a regulator of RNA polymerase I by connecting RNA polymerase I with enzymes responsible for ribosomal processing and modification (PubMed:12777385, PubMed:26399832). Required for neural crest specification: following monoubiquitination by the BCR(KBTBD8) complex, associates with NOLC1 and acts as a platform to connect RNA polymerase I with enzymes responsible for ribosomal processing and modification, leading to remodel the translational program of differentiating cells in favor of neural crest specification (PubMed:26399832)