Gene name: GANAB

Uniprot entry:

Q14697

Protein names:

Neutral alpha-glucosidase AB (EC 3.2.1.207) (Alpha-glucosidase 2) (Glucosidase II subunit alpha)

Protein sequence:

1_MAAVA 6_ AVAAR 11_ RRRSW 16_ ASLVL 21_ AFLGV 26_ CLGIT 31_ LAVDR 36_ SNFKT 41_ CEESS 46_ FCKRQ 51_ RSIRP 56_ GLSPY 61_ RALLD 66_ SLQLG 71_ PDSLT 76_ VHLIH 81_ EVTKV 86_ LLVLE 91_ LQGLQ 96_ KNMTR 101_ FRIDE 106_ LEPRR 111_ PRYRV 116_ PDVLV 121_ ADPPI 126_ ARLSV 131_ SGRDE 136_ NSVEL 141_ TMAEG 146_ PYKII 151_ LTARP 156_ FRLDL 161_ LEDRS 166_ LLLSV 171_ NARGL 176_ LEFEH 181_ QRAPR 186_ VSQGS 191_ KDPAE 196_ GDGAQ 201_ PEETP 206_ RDGDK 211_ PEETQ 216_ GKAEK 221_ DEPGA 226_ WEETF 231_ KTHSD 236_ SKPYG 241_ PMSVG 246_ LDFSL 251_ PGMEH 256_ VYGIP 261_ EHADN 266_ LRLKV 271_ TEGGE 276_ PYRLY 281_ NLDVF 286_ QYELY 291_ NPMAL 296_ YGSVP 301_ VLLAH 306_ NPHRD 311_ LGIFW 316_ LNAAE 321_ TWVDI 326_ SSNTA 331_ GKTLF 336_ GKMMD 341_ YLQGS 346_ GETPQ 351_ TDVRW 356_ MSETG 361_ IIDVF 366_ LLLGP 371_ SISDV 376_ FRQYA 381_ SLTGT 386_ QALPP 391_ LFSLG 396_ YHQSR 401_ WNYRD 406_ EADVL 411_ EVDQG 416_ FDDHN 421_ LPCDV 426_ IWLDI 431_ EHADG 436_ KRYFT 441_ WDPSR 446_ FPQPR 451_ TMLER 456_ LASKR 461_ RKLVA 466_ IVDPH 471_ IKVDS 476_ GYRVH 481_ EELRN 486_ LGLYV 491_ KTRDG 496_ SDYEG 501_ WCWPG 506_ SAGYP 511_ DFTNP 516_ TMRAW 521_ WANMF 526_ SYDNY 531_ EGSAP 536_ NLFVW 541_ NDMNE 546_ PSVFN 551_ GPEVT 556_ MLKDA 561_ QHYGG 566_ WEHRD 571_ VHNIY 576_ GLYVH 581_ MATAD 586_ GLRQR 591_ SGGME 596_ RPFVL 601_ ARAFF 606_ AGSQR 611_ FGAVW 616_ TGDNT 621_ AEWDH 626_ LKISI 631_ PMCLS 636_ LGLVG 641_ LSFCG 646_ ADVGG 651_ FFKNP 656_ EPELL 661_ VRWYQ 666_ MGAYQ 671_ PFFRA 676_ HAHLD 681_ TGRRE 686_ PWLLP 691_ SQHND 696_ IIRDA 701_ LGQRY 706_ SLLPF 711_ WYTLL 716_ YQAHR 721_ EGIPV 726_ MRPLW 731_ VQYPQ 736_ DVTTF 741_ NIDDQ 746_ YLLGD 751_ ALLVH 756_ PVSDS 761_ GAHGV 766_ QVYLP 771_ GQGEV 776_ WYDIQ 781_ SYQKH 786_ HGPQT 791_ LYLPV 796_ TLSSI 801_ PVFQR 806_ GGTIV 811_ PRWMR 816_ VRRSS 821_ ECMKD 826_ DPITL 831_ FVALS 836_ PQGTA 841_ QGELF 846_ LDDGH 851_ TFNYQ 856_ TRQEF 861_ LLRRF 866_ SFSGN 871_ TLVSS 876_ SADPE 881_ GHFET 886_ PIWIE 891_ RVVII 896_ GAGKP 901_ AAVVL 906_ QTKGS 911_ PESRL 916_ SFQHD 921_ PETSV 926_ LVLRK 931_ PGINV 936_ASDWS

Protein annotations

Protein functions:

1: Catalytic subunit of glucosidase II that cleaves sequentially the 2 innermost alpha-1,3-linked glucose residues from the Glc(2)Man(9)GlcNAc(2) oligosaccharide precursor of immature glycoproteins (PubMed:10929008). Required for PKD1/Polycystin-1 and PKD2/Polycystin-2 maturation and localization to the cell surface and cilia (PubMed:27259053)