Gene name: OXA1L

Uniprot entry:

Q15070

Protein names:

Mitochondrial inner membrane protein OXA1L (Hsa) (OXA1Hs) (Oxidase assembly 1-like protein) (OXA1-like protein)

Protein sequence:

1_MAMGL 6_ MCGRR 11_ ELLRL 16_ LQSGR 21_ RVHSV 26_ AGPSQ 31_ WLGKP 36_ LTTRL 41_ LFPVA 46_ PCCCR 51_ PHYLF 56_ LAASG 61_ PRSLS 66_ TSAIS 71_ FAEVQ 76_ VQAPP 81_ VVAAT 86_ PSPTA 91_ VPEVA 96_ SGETA 101_ DVVQT 106_ AAEQS 111_ FAELG 116_ LGSYT 121_ PVGLI 126_ QNLLE 131_ FMHVD 136_ LGLPW 141_ WGAIA 146_ ACTVF 151_ ARCLI 156_ FPLIV 161_ TGQRE 166_ AARIH 171_ NHLPE 176_ IQKFS 181_ SRIRE 186_ AKLAG 191_ DHIEY 196_ YKASS 201_ EMALY 206_ QKKHG 211_ IKLYK 216_ PLILP 221_ VTQAP 226_ IFISF 231_ FIALR 236_ EMANL 241_ PVPSL 246_ QTGGL 251_ WWFQD 256_ LTVSD 261_ PIYIL 266_ PLAVT 271_ ATMWA 276_ VLELG 281_ AETGV 286_ QSSDL 291_ QWMRN 296_ VIRMM 301_ PLITL 306_ PITMH 311_ FPTAV 316_ FMYWL 321_ SSNLF 326_ SLVQV 331_ SCLRI 336_ PAVRT 341_ VLKIP 346_ QRVVH 351_ DLDKL 356_ PPREG 361_ FLESF 366_ KKGWK 371_ NAEMT 376_ RQLRE 381_ REQRM 386_ RNQLE 391_ LAARG 396_ PLRQT 401_ FTHNP 406_ LLQPG 411_ KDNPP 416_ NIPSS 421_ SSKPK 426_SKYPW

Protein annotations

Protein functions:

1: Mitochondrial membrane insertase that mediates the cotranslational insertion of integral membrane proteins into the mitochondrial inner membrane (PubMed:17936786, PubMed:33602856, PubMed:7991568). Essential for the activity and assembly of cytochrome oxidase (PubMed:17936786, PubMed:7991568). Required for the correct biogenesis of ATP synthase and complex I in mitochondria (PubMed:17936786, PubMed:7991568)