Gene name: TIMM50

Uniprot entry:

Q3ZCQ8

Protein names:

Mitochondrial import inner membrane translocase subunit TIM50

Protein sequence:

1_MAASA 6_ AVFSR 11_ LRSGL 16_ RLGSR 21_ GLCTR 26_ LATPP 31_ RRAPD 36_ QAAEI 41_ GSRGS 46_ TKAQG 51_ PQQQP 56_ GSEGP 61_ SYAKK 66_ VALWL 71_ AGLLG 76_ AGGTV 81_ SVVYI 86_ FGNNP 91_ VDENG 96_ AKIPD 101_ EFDND 106_ PILVQ 111_ QLRRT 116_ YKYFK 121_ DYRQM 126_ IIEPT 131_ SPCLL 136_ PDPLQ 141_ EPYYQ 146_ PPYTL 151_ VLELT 156_ GVLLH 161_ PEWSL 166_ ATGWR 171_ FKKRP 176_ GIETL 181_ FQQLA 186_ PLYEI 191_ VIFTS 196_ ETGMT 201_ AFPLI 206_ DSVDP 211_ HGFIS 216_ YRLFR 221_ DATRY 226_ MDGHH 231_ VKDIS 236_ CLNRD 241_ PARVV 246_ VVDCK 251_ KEAFR 256_ LQPYN 261_ GVALR 266_ PWDGN 271_ SDDRV 276_ LLDLS 281_ AFLKT 286_ IALNG 291_ VEDVR 296_ TVLEH 301_ YALED 306_ DPLAA 311_ FKQRQ 316_ SRLEQ 321_ EEQQR 326_ LAELS 331_ KSNKQ 336_ NLFLG 341_ SLTSR 346_LWPRS

Protein annotations

Protein functions:

1: Essential component of the TIM23 complex, a complex that mediates the translocation of transit peptide-containing proteins across the mitochondrial inner membrane (PubMed:30190335, PubMed:38828998). Has some phosphatase activity in vitro; however such activity may not be relevant in vivo

2: May participate in the release of snRNPs and SMN from the Cajal body