Tetratricopeptide repeat protein 19, mitochondrial (TPR repeat protein 19)
1_MFRLL 6_ SWSLG 11_ RGFLR 16_ AAGRR 21_ CRGCS 26_ ARLLP 31_ GLAGG 36_ PGPEV 41_ QVPPS 46_ RVAPH 51_ GRGPG 56_ LLPLL 61_ AALAW 66_ FSRPA 71_ AAEEE 76_ EQQGA 81_ DGAAA 86_ EDGAD 91_ EAEAE 96_ IIQLL 101_ KRAKL 106_ SIMKD 111_ EPEEA 116_ ELILH 121_ DALRL 126_ AYQTD 131_ NKKAI 136_ TYTYD 141_ LMANL 146_ AFIRG 151_ QLENA 156_ EQLFK 161_ ATMSY 166_ LLGGG 171_ MKQED 176_ NAIIE 181_ ISLKL 186_ ASIYA 191_ AQNRQ 196_ EFAVA 201_ GYEFC 206_ ISTLE 211_ EKIER 216_ EKELA 221_ EDIMS 226_ VEEKA 231_ NTHLL 236_ LGMCL 241_ DACAR 246_ YLLFS 251_ KQPSQ 256_ AQRMY 261_ EKALQ 266_ ISEEI 271_ QGERH 276_ PQTIV 281_ LMSDL 286_ ATTLD 291_ AQGRF 296_ DEAYI 301_ YMQRA 306_ SDLAR 311_ QINHP 316_ ELHMV 321_ LSNLA 326_ AVLMH 331_ RERYT 336_ QAKEI 341_ YQEAL 346_ KQAKL 351_ KKDEI 356_ SVQHI 361_ REELA 366_ ELSKK 371_SRPLT
1: Required for the preservation of the structural and functional integrity of mitochondrial respiratory complex III by allowing the physiological turnover of the Rieske protein UQCRFS1 (PubMed:21278747, PubMed:28673544). Involved in the clearance of UQCRFS1 N-terminal fragments, which are produced upon incorporation of UQCRFS1 into the complex III and whose presence is detrimental for its catalytic activity (PubMed:28673544)