3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (EC 3.1.2.4) (3-hydroxyisobutyryl-coenzyme A hydrolase) (HIB-CoA hydrolase) (HIBYL-CoA-H)
1_MGQRE 6_ MWRLM 11_ SRFNA 16_ FKRTN 21_ TILHH 26_ LRMSK 31_ HTDAA 36_ EEVLL 41_ EKKGC 46_ TGVIT 51_ LNRPK 56_ FLNAL 61_ TLNMI 66_ RQIYP 71_ QLKKW 76_ EQDPE 81_ TFLII 86_ IKGAG 91_ GKAFC 96_ AGGDI 101_ RVISE 106_ AEKAK 111_ QKIAP 116_ VFFRE 121_ EYMLN 126_ NAVGS 131_ CQKPY 136_ VALIH 141_ GITMG 146_ GGVGL 151_ SVHGQ 156_ FRVAT 161_ EKCLF 166_ AMPET 171_ AIGLF 176_ PDVGG 181_ GYFLP 186_ RLQGK 191_ LGYFL 196_ ALTGF 201_ RLKGR 206_ DVYRA 211_ GIATH 216_ FVDSE 221_ KLAML 226_ EEDLL 231_ ALKSP 236_ SKENI 241_ ASVLE 246_ NYHTE 251_ SKIDR 256_ DKSFI 261_ LEEHM 266_ DKINS 271_ CFSAN 276_ TVEEI 281_ IENLQ 286_ QDGSS 291_ FALEQ 296_ LKVIN 301_ KMSPT 306_ SLKIT 311_ LRQLM 316_ EGSSK 321_ TLQEV 326_ LTMEY 331_ RLSQA 336_ CMRGH 341_ DFHEG 346_ VRAVL 351_ IDKDQ 356_ SPKWK 361_ PADLK 366_ EVTEE 371_ DLNNH 376_ FKSLG 381_SSDLK
1: Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA