Gene name: PKHD1L1

Uniprot entry:

Q86WI1

Protein names:

Fibrocystin-L (Polycystic kidney and hepatic disease 1-like protein 1) (PKHD1-like protein 1)

Protein sequence:

1_MGHLW 6_ LLGIW 11_ GLCGL 16_ LLCAA 21_ DPSTD 26_ GSQII 31_ PKVTE 36_ IIPKY 41_ GSING 46_ ATRLT 51_ IRGEG 56_ FSQAN 61_ QFNYG 66_ VDNAE 71_ LGNSV 76_ QLISS 81_ FQSIT 86_ CDVEK 91_ DASHS 96_ TQITC 101_ YTRAM 106_ PEDSY 111_ TVRVS 116_ VDGVP 121_ VTENN 126_ TCKGH 131_ INSWE 136_ CTFNA 141_ KSFRT 146_ PTIRS 151_ ITPLS 156_ GTPGT 161_ LITIQ 166_ GRIFT 171_ DVYGS 176_ NIALS 181_ SNGKN 186_ VRILR 191_ VYIGG 196_ MPCEL 201_ LIPQS 206_ DNLYG 211_ LKLDH 216_ PNGDM 221_ GSMVC 226_ KTTGT 231_ FIGHH 236_ NVSFI 241_ LDNDY 246_ GRSFP 251_ QKMAY 256_ FVSSL 261_ NKIAM 266_ FQTYA 271_ EVTMI 276_ FPSQG 281_ SIRGG 286_ TTLTI 291_ SGRFF 296_ DQTDF 301_ PVRVL 306_ VGGEP 311_ CDILN 316_ VTENS 321_ ICCKT 326_ PPKPH 331_ ILKTV 336_ YPGGR 341_ GLKLE 346_ VWNNS 351_ RPIRL 356_ EEILE 361_ YNEKT 366_ PGYMG 371_ ASWVD 376_ SASYI 381_ WLMEQ 386_ DTFVA 391_ RFSGF 396_ LVAPD 401_ SDVYR 406_ FYIKG 411_ DDRYA 416_ IYFSQ 421_ TGLPE 426_ DKVRI 431_ AYHSA 436_ NANSY 441_ FSSPT 446_ QRSDD 451_ IHLQK 456_ GKEYY 461_ IEILL 466_ QEYRL 471_ SAFVD 476_ VGLYQ 481_ YRNVY 486_ TEQQT 491_ GDAVN 496_ EEQVI 501_ KSQST 506_ ILQEV 511_ QVITL 516_ ENWET 521_ TNAIN 526_ EVQKI 531_ KVTSP 536_ CVEAN 541_ SCSLY 546_ QYRLI 551_ YNMEK 556_ TVFLP 561_ ADASE 566_ FILQS 571_ ALNDL 576_ WSIKP 581_ DTVQV 586_ IRTQN 591_ PQSYV 596_ YMVTF 601_ ISTRG 606_ DFDLL 611_ GYEVV 616_ EGNNV 621_ TLDIT 626_ EQTKG 631_ KPNLE 636_ TFTLN 641_ WDGIA 646_ SKPLT 651_ LWSSE 656_ AEFQG 661_ AVEEM 666_ VSTKC 671_ PPQIA 676_ NFEEG 681_ FVVKY 686_ FRDYE 691_ TDFNL 696_ EHINR 701_ GQKTA 706_ ETDAY 711_ CGRYS 716_ LKNPA 721_ VLFDS 726_ ADVKP 731_ NRRPY 736_ GDILL 741_ FPYNQ 746_ LCLAY 751_ KGFLA 756_ NYIGL 761_ KFQYQ 766_ DNSKI 771_ TRSTD 776_ TQFTY 781_ NFAYG 786_ NNWTY 791_ TCIDL 796_ LDLVR 801_ TKYTG 806_ TNVSL 811_ QRISL 816_ HKASE 821_ SQSFY 826_ VDVVY 831_ IGHTS 836_ TISTL 841_ DEMPK 846_ RRLPA 851_ LANKG 856_ IFLEH 861_ FQVNQ 866_ TKTNG 871_ PTMTN 876_ QYSVT 881_ MTSYN 886_ CSYNI 891_ PMMAV 896_ SFGQI 901_ ITHET 906_ ENEFV 911_ YRGNN 916_ WPGES 921_ KIHIQ 926_ RIQAA 931_ SPPLS 936_ GSFDI 941_ QAYGH 946_ ILKGL 951_ PAAVS 956_ AADLQ 961_ FALQS 966_ LEGMG 971_ RISVT 976_ REGTC 981_ AGYAW 986_ NIKWR 991_ STCGK 996_ QNLLQ 1001_ INDSN 1006_ IIGEK 1011_ ANMTV 1016_ TRIKE 1021_ GGLFR 1026_ QHVLG 1031_ DLLRT 1036_ PSQQP 1041_ QVEVY 1046_ VNGIP 1051_ AKCSG 1056_ DCGFT 1061_ WDSNI 1066_ TPLVL 1071_ AISPS 1076_ QGSYE 1081_ EGTIL 1086_ TIVGS 1091_ GFSPS 1096_ SAVTV 1101_ SVGPV 1106_ GCSLL 1111_ SVDEK 1116_ ELKCQ 1121_ ILNGS 1126_ AGHAP 1131_ VAVSM 1136_ ADVGL 1141_ AQNVG 1146_ GEEFY 1151_ FVYQS 1156_ QISHI 1161_ WPDSG 1166_ SIAGG 1171_ TLLTL 1176_ SGFGF 1181_ NENSK 1186_ VLVGN 1191_ ETCNV 1196_ IEGDL 1201_ NRITC 1206_ RTPKK 1211_ TEGTV 1216_ DISVT 1221_ TNGFQ 1226_ ATARD 1231_ AFSYN 1236_ CLQTP 1241_ IITDF 1246_ SPKVR 1251_ TILGE 1256_ VNLTI 1261_ KGYNF 1266_ GNELT 1271_ QNMAV 1276_ YVGGK 1281_ TCQIL 1286_ HWNFT 1291_ DIRCL 1296_ LPKLS 1301_ PGKHD 1306_ IYVEV 1311_ RNWGF 1316_ ASTRD 1321_ KLNSS 1326_ IQYVL 1331_ EVTSM 1336_ FPQRG 1341_ SLFGG 1346_ TEITI 1351_ RGFGF 1356_ STIPA 1361_ ENTVL 1366_ LGSIP 1371_ CNVTS 1376_ SSENV 1381_ IKCIL 1386_ HSTGN 1391_ IFRIT 1396_ NNGKD 1401_ SVHGL 1406_ GYAWS 1411_ PPVLN 1416_ VSVGD 1421_ TVAWH 1426_ WQTHP 1431_ FLRGI 1436_ GYRIF 1441_ SVSSP 1446_ GSVIY 1451_ DGKGF 1456_ TSGRQ 1461_ KSTSG 1466_ SFSYQ 1471_ FTSPG 1476_ IHYYS 1481_ SGYVD 1486_ EAHSI 1491_ FLQGV 1496_ INVLP 1501_ AETRH 1506_ IPLHL 1511_ FVGRS 1516_ EATYA 1521_ YGGPE 1526_ NLHLG 1531_ SSVAG 1536_ CLATE 1541_ PLCSL 1546_ NNTRV 1551_ KNSKR 1556_ LLFEV 1561_ SSCFS 1566_ PSISN 1571_ ITPST 1576_ GTVNE 1581_ LITII 1586_ GHGFS 1591_ NLPWA 1596_ NKVTI 1601_ GSYPC 1606_ VVEES 1611_ SEDSI 1616_ TCHID 1621_ PQNSM 1626_ DVGIR 1631_ ETVTL 1636_ TVYNL 1641_ GTAIN 1646_ TLSNE 1651_ FDRRF 1656_ VLLPN 1661_ IDLVL 1666_ PNAGS 1671_ TTGMT 1676_ SVTIK 1681_ GSGFA 1686_ VSSAG 1691_ VKVLM 1696_ GHFPC 1701_ KVLSV 1706_ NYTAI 1711_ ECETS 1716_ PAAQQ 1721_ LVDVD 1726_ LLIHG 1731_ VPAQC 1736_ QGNCT 1741_ FSYLE 1746_ SITPY 1751_ ITGVF 1756_ PNSVI 1761_ GSVKV 1766_ LIEGE 1771_ GLGTV 1776_ LEDIA 1781_ VFIGN 1786_ QQFRA 1791_ IEVNE 1796_ NNITA 1801_ LVTPL 1806_ PVGHH 1811_ SVSVV 1816_ VGSKG 1821_ LALGN 1826_ LTVSS 1831_ PPVAS 1836_ LSPTS 1841_ GSIGG 1846_ GTTLV 1851_ ITGNG 1856_ FYPGN 1861_ TTVTI 1866_ GDEPC 1871_ QIISI 1876_ NPNEV 1881_ YCRTP 1886_ AGTTG 1891_ MVDVK 1896_ IFVNT 1901_ IAYPP 1906_ LLFTY 1911_ ALEDT 1916_ PFLRG 1921_ IIPSR 1926_ GPPGT 1931_ EIEIT 1936_ GSNFG 1941_ FEILE 1946_ ISVMI 1951_ NNIQC 1956_ NVTMA 1961_ NDSVV 1966_ QCIVG 1971_ DHAGG 1976_ TFPVM 1981_ MHHKT 1986_ KGSAM 1991_ STVVF 1996_ EYPLN 2001_ IQNIN 2006_ PSQGS 2011_ FGGGQ 2016_ TMTVT 2021_ GTGFN 2026_ PQNSI 2031_ ILVCG 2036_ SECAI 2041_ DRLRS 2046_ DYTTL 2051_ LCEIP 2056_ SNNGT 2061_ GAEQA 2066_ CEVSV 2071_ VNGKD 2076_ LSQSM 2081_ TPFTY 2086_ AVSLT 2091_ PLITA 2096_ VSPKR 2101_ GSTAG 2106_ GTRLT 2111_ VVGSG 2116_ FSENM 2121_ EDVHI 2126_ TIAEA 2131_ KCDVE 2136_ YSNKT 2141_ HIICM 2146_ TDAHT 2151_ LSGWA 2156_ PVCVH 2161_ IRGVG 2166_ MAKLD 2171_ NADFL 2176_ YVDAW 2181_ SSNFS 2186_ WGGKS 2191_ PPEEG 2196_ SLVVI 2201_ TKGQT 2206_ ILLDQ 2211_ STPIL 2216_ KMLLI 2221_ QGGTL 2226_ IFDEA 2231_ DIELQ 2236_ AENIL 2241_ ITDGG 2246_ VLQIG 2251_ TETSP 2256_ FQHKA 2261_ VITLH 2266_ GHLRS 2271_ PELPV 2276_ YGAKT 2281_ LAVRE 2286_ GILDL 2291_ HGVPV 2296_ PVTWT 2301_ RLAHT 2306_ AKAGE 2311_ RILIL 2316_ QEAVT 2321_ WKPGD 2326_ NIVIA 2331_ STGHR 2336_ HSQGE 2341_ NEKMT 2346_ IASVS 2351_ ADGIN 2356_ ITLSN 2361_ PLNYT 2366_ HLGIT 2371_ VTLPD 2376_ GTLFE 2381_ ARAEV 2386_ GILTR 2391_ NILIR 2396_ GSDNV 2401_ EWNNK 2406_ IPACP 2411_ DGFDT 2416_ GEFAT 2421_ QTCLQ 2426_ GKFGE 2431_ EIGSD 2436_ QFGGC 2441_ VMFHA 2446_ PVPGA 2451_ NMVTG 2456_ RIEYV 2461_ EVFHA 2466_ GQAFR 2471_ LGRYP 2476_ IHWHL 2481_ LGDLQ 2486_ FKSYV 2491_ RGCAI 2496_ HQAYN 2501_ RAVTI 2506_ HNTHH 2511_ LLVER 2516_ NIIYD 2521_ IKGGA 2526_ FFIED 2531_ GIEHG 2536_ NILQY 2541_ NLAVF 2546_ VQQST 2551_ SLLND 2556_ DVTPA 2561_ AFWVT 2566_ NPNNT 2571_ IRHNA 2576_ VAGGT 2581_ HFGFW 2586_ YRMNN 2591_ HPDGP 2596_ SYDRN 2601_ ICQKR 2606_ VPLGE 2611_ FFNNT 2616_ VHSQG 2621_ WFGMW 2626_ IFEEY 2631_ FPMQT 2636_ GSCTS 2641_ TVPAP 2646_ AIFNS 2651_ LTTWN 2656_ CQKGA 2661_ EWVNG 2666_ GALQF 2671_ HNFVM 2676_ VNNYE 2681_ AGIET 2686_ KRILA 2691_ PYVGG 2696_ WGETN 2701_ GAVIK 2706_ NAKIV 2711_ GHLDE 2716_ LGMGS 2721_ AFCTA 2726_ KGLVL 2731_ PFSEG 2736_ LTVSS 2741_ VHFMN 2746_ FDRPN 2751_ CVALG 2756_ VTSIS 2761_ GVCND 2766_ RCGGW 2771_ SAKFV 2776_ DVQYS 2781_ HTPNK 2786_ AGFRW 2791_ EHEMV 2796_ MIDVD 2801_ GSLTG 2806_ HKGHT 2811_ VIPHS 2816_ SLLDP 2821_ SHCTQ 2826_ EAEWS 2831_ IGFPG 2836_ SVCDA 2841_ SVSFH 2846_ RLAFN 2851_ QPSPV 2856_ SLLEK 2861_ DVVLS 2866_ DSFGT 2871_ SIIPF 2876_ QKKRL 2881_ THMSG 2886_ WMALI 2891_ PNANH 2896_ INWYF 2901_ KGVDH 2906_ ITNIS 2911_ YTSTF 2916_ YGFKE 2921_ EDYVI 2926_ ISHNF 2931_ TQNPD 2936_ MFNII 2941_ DMRNG 2946_ SSNPL 2951_ NWNTS 2956_ KNGDW 2961_ HLEAN 2966_ TSTLY 2971_ YLVSG 2976_ RNDLH 2981_ QSQLI 2986_ SGNLD 2991_ PDVKD 2996_ VVINF 3001_ QAYCC 3006_ ILQDC 3011_ FPVHP 3016_ PSRKP 3021_ IPKKR 3026_ PATYN 3031_ LWSND 3036_ SFWQS 3041_ SRENN 3046_ YTVPH 3051_ PGANV 3056_ IIPEG 3061_ TWIVA 3066_ DIDMP 3071_ SMERL 3076_ IIWGV 3081_ LELED 3086_ KYNVG 3091_ AAESS 3096_ YREVV 3101_ LNATY 3106_ ISLQG 3111_ GRLIG 3116_ GWEDN 3121_ PFKGD 3126_ LKIVL 3131_ RGNHT 3136_ TQDWA 3141_ LPEGP 3146_ NQGAK 3151_ VLGVF 3156_ GELDL 3161_ HGIPH 3166_ SIYKT 3171_ KLSET 3176_ AFAGS 3181_ KVLSL 3186_ MDAVD 3191_ WQEGE 3196_ EIVIT 3201_ TTSYD 3206_ FHQTE 3211_ TRSIV 3216_ KILHD 3221_ HKILI 3226_ LNDSL 3231_ SYTHF 3236_ AEKYH 3241_ VPGTG 3246_ ESYTL 3251_ AADVG 3256_ ILSRN 3261_ IKIVG 3266_ EDYPG 3271_ WSEDS 3276_ FGARV 3281_ LVGSF 3286_ TENMM 3291_ TFKGN 3296_ ARISN 3301_ VEFYH 3306_ SGQEG 3311_ FRDST 3316_ DPRYA 3321_ VTFLN 3326_ LGQIQ 3331_ EHGSS 3336_ YIRGC 3341_ AFHHG 3346_ FSPAI 3351_ GVFGT 3356_ DGLDI 3361_ DDNII 3366_ HFTVG 3371_ EGIRI 3376_ WGNAN 3381_ RVRGN 3386_ LIALS 3391_ VWPGT 3396_ YQNRK 3401_ DLSST 3406_ LWHAA 3411_ IEINR 3416_ GTNTV 3421_ LQNNV 3426_ VAGFG 3431_ RAGYR 3436_ IDGEP 3441_ CPGQF 3446_ NPVEK 3451_ WFDNE 3456_ AHGGL 3461_ YGIYM 3466_ NQDGL 3471_ PGCSL 3476_ IQGFT 3481_ IWTCW 3486_ DYGIY 3491_ FQTTE 3496_ SVHIY 3501_ NVTLV 3506_ DNGMA 3511_ IFPMI 3516_ YMPAA 3521_ ISHKI 3526_ SSKNV 3531_ QIKSS 3536_ LIVGS 3541_ SPGFN 3546_ CSDVL 3551_ TNDDP 3556_ NIELT 3561_ AAHRS 3566_ PRSPS 3571_ GGRSG 3576_ ICWPT 3581_ FASAH 3586_ NMAPR 3591_ KPHAG 3596_ IMSYN 3601_ AISGL 3606_ LDISG 3611_ STFVG 3616_ FKNVC 3621_ SGETN 3626_ VIFIT 3631_ NPLNE 3636_ DLQHP 3641_ IHVKN 3646_ IKLVD 3651_ TTEQS 3656_ KIFIH 3661_ RPDIS 3666_ KVNPS 3671_ DCVDM 3676_ VCDAK 3681_ RKSFL 3686_ RDIDG 3691_ SFLGN 3696_ AGSVI 3701_ PQAEY 3706_ EWDGN 3711_ SQVGI 3716_ GDYRI 3721_ PKAML 3726_ TFLNG 3731_ SRIPV 3736_ TEKAP 3741_ HKGII 3746_ RDSTC 3751_ KYLPE 3756_ WQSYQ 3761_ CFGME 3766_ YAMMV 3771_ IESLD 3776_ PDTET 3781_ RRLSP 3786_ VAIMG 3791_ NGYVD 3796_ LINGP 3801_ QDHGW 3806_ CAGYT 3811_ CQRRL 3816_ SLFHS 3821_ IVALN 3826_ KSYEV 3831_ YFTGT 3836_ SPQNL 3841_ RLMLL 3846_ NVDHN 3851_ KAVLV 3856_ GIFFS 3861_ TLQRL 3866_ DVYVN 3871_ NLLVC 3876_ PKTTI 3881_ WNAQQ 3886_ KHCEL 3891_ NNHLY 3896_ KDQFL 3901_ PNLDS 3906_ TVLGE 3911_ NYFDG 3916_ TYQML 3921_ YLLVK 3926_ GTIPV 3931_ EIHTA 3936_ TVIFV 3941_ SFQLS 3946_ VATED 3951_ DFYTS 3956_ HNLVK 3961_ NLALF 3966_ LKIPS 3971_ DKIRI 3976_ SKIRG 3981_ KSLRR 3986_ KRSMG 3991_ FIIEI 3996_ EIGDP 4001_ PIQFI 4006_ SNGTT 4011_ GQMQL 4016_ SELQE 4021_ IAGSL 4026_ GQAVI 4031_ LGNIS 4036_ SILGF 4041_ NISSM 4046_ SITNP 4051_ LPSPS 4056_ DSGWI 4061_ KVTAQ 4066_ PVERS 4071_ AFPVH 4076_ HVAFV 4081_ SSLLV 4086_ ITQPV 4091_ AAQPG 4096_ QPFPQ 4101_ QPSVK 4106_ ATDSD 4111_ GNCVS 4116_ VGITA 4121_ LTLRA 4126_ ILKDS 4131_ NNNQV 4136_ NGLSG 4141_ NTTIP 4146_ FSSCW 4151_ ANYTD 4156_ LTPLR 4161_ TGKNY 4166_ KIEFI 4171_ LDNVV 4176_ GVESR 4181_ TFSLL 4186_ AESVS 4191_ SSGSS 4196_ SSSNS 4201_ KASTV 4206_ GTYAQ 4211_ IMTVV 4216_ ISCLV 4221_ GRMWL 4226_ LEIFM 4231_ AAVST 4236_LNITL

Protein annotations

Protein functions:

1: Component of hair-cell stereocilia coat. Required for normal hearing