Xylosyltransferase 1 (EC 2.4.2.26) (Peptide O-xylosyltransferase 1) (Xylosyltransferase I) (XT-I) (XylT-I)
1_MVAAP 6_ CARRL 11_ ARRSH 16_ SALLA 21_ ALTVL 26_ LLQTL 31_ VVWNF 36_ SSLDS 41_ GAGER 46_ RGGAA 51_ VGGGE 56_ QPPPA 61_ PAPRR 66_ ERRDL 71_ PAEPA 76_ AARGG 81_ GGGGG 86_ GGGGG 91_ RGPQA 96_ RARGG 101_ GPGEP 106_ RGQQP 111_ ASRGA 116_ LPARA 121_ LDPHP 126_ SPLIT 131_ LETQD 136_ GYFSH 141_ RPKEK 146_ VRTDS 151_ NNENS 156_ VPKDF 161_ ENVDN 166_ SNFAP 171_ RTQKQ 176_ KHQPE 181_ LAKKP 186_ PSRQK 191_ ELLKR 196_ KLEQQ 201_ EKGKG 206_ HTFPG 211_ KGPGE 216_ VLPPG 221_ DRAAA 226_ NSSHG 231_ KDVSR 236_ PPHAR 241_ KTGGS 246_ SPETK 251_ YDQPP 256_ KCDIS 261_ GKEAI 266_ SALSR 271_ AKSKH 276_ CRQEI 281_ GETYC 286_ RHKLG 291_ LLMPE 296_ KVTRF 301_ CPLEG 306_ KANKN 311_ VQWDE 316_ DSVEY 321_ MPANP 326_ VRIAF 331_ VLVVH 336_ GRASR 341_ QLQRM 346_ FKAIY 351_ HKDHF 356_ YYIHV 361_ DKRSN 366_ YLHRQ 371_ VLQVS 376_ RQYSN 381_ VRVTP 386_ WRMAT 391_ IWGGA 396_ SLLST 401_ YLQSM 406_ RDLLE 411_ MTDWP 416_ WDFFI 421_ NLSAA 426_ DYPIR 431_ TNDQL 436_ VAFLS 441_ RYRDM 446_ NFLKS 451_ HGRDN 456_ ARFIR 461_ KQGLD 466_ RLFLE 471_ CDAHM 476_ WRLGD 481_ RRIPE 486_ GIAVD 491_ GGSDW 496_ FLLNR 501_ RFVEY 506_ VTFST 511_ DDLVT 516_ KMKQF 521_ YSYTL 526_ LPAES 531_ FFHTV 536_ LENSP 541_ HCDTM 546_ VDNNL 551_ RITNW 556_ NRKLG 561_ CKCQY 566_ KHIVD 571_ WCGCS 576_ PNDFK 581_ PQDFH 586_ RFQQT 591_ ARPTF 596_ FARKF 601_ EAVVN 606_ QEIIG 611_ QLDYY 616_ LYGNY 621_ PAGTP 626_ GLRSY 631_ WENVY 636_ DEPDG 641_ IHSLS 646_ DVTLT 651_ LYHSF 656_ ARLGL 661_ RRAET 666_ SLHTD 671_ GENSC 676_ RYYPM 681_ GHPAS 686_ VHLYF 691_ LADRF 696_ QGFLI 701_ KHHAT 706_ NLAVS 711_ KLETL 716_ ETWVM 721_ PKKVF 726_ KIASP 731_ PSDFG 736_ RLQFS 741_ EVGTD 746_ WDAKE 751_ RLFRN 756_ FGGLL 761_ GPMDE 766_ PVGMQ 771_ KWGKG 776_ PNVTV 781_ TVIWV 786_ DPVNV 791_ IAATY 796_ DILIE 801_ STAEF 806_ THYKP 811_ PLNLP 816_ LRPGV 821_ WTVKI 826_ LHHWV 831_ PVAET 836_ KFLVA 841_ PLTFS 846_ NRQPI 851_ KPEEA 856_ LKLHN 861_ GPLRN 866_ AYMEQ 871_ SFQSL 876_ NPVLS 881_ LPINP 886_ AQVEQ 891_ ARRNA 896_ ASTGT 901_ ALEGW 906_ LDSLV 911_ GGMWT 916_ AMDIC 921_ ATGPT 926_ ACPVM 931_ QTCSQ 936_ TAWSS 941_ FSPDP 946_ KSELG 951_AVKPD
1: Catalyzes the first step in the biosynthesis of chondroitin sulfate and dermatan sulfate proteoglycans, such as DCN. Transfers D-xylose from UDP-D-xylose to specific serine residues of the core protein (PubMed:15461586, PubMed:17189265, PubMed:23982343, PubMed:24581741). Required for normal embryonic and postnatal skeleton development, especially of the long bones (PubMed:23982343, PubMed:24581741). Required for normal maturation of chondrocytes during bone development, and normal onset of ossification (By similarity)