Xyloside xylosyltransferase 1 (EC 2.4.2.62) (UDP-xylose:alpha-xyloside alpha-1,3-xylosyltransferase)
1_MGLLR 6_ GGLPC 11_ ARAMA 16_ RLGAV 21_ RSHYC 26_ ALLLA 31_ AALAV 36_ CAFYY 41_ LGSGR 46_ ETFSS 51_ ATKRL 56_ KEARA 61_ GAPAA 66_ PSPPA 71_ LELAR 76_ GSVAP 81_ APGAK 86_ AKSLE 91_ GGGAG 96_ PVDYH 101_ LLMMF 106_ TKAEH 111_ NAALQ 116_ AKARV 121_ ALRSL 126_ LRLAK 131_ FEAHE 136_ VLNLH 141_ FVSEE 146_ ASREV 151_ AKGLL 156_ RELLP 161_ PAAGF 166_ KCKVI 171_ FHDVA 176_ VLTDK 181_ LFPIV 186_ EAMQK 191_ HFSAG 196_ LGTYY 201_ SDSIF 206_ FLSVA 211_ MHQIM 216_ PKEIL 221_ QIIQL 226_ DLDLK 231_ FKTNI 236_ RELFE 241_ EFDSF 246_ LPGAI 251_ IGIAR 256_ EMQPV 261_ YRHTF 266_ WQFRH 271_ ENPQT 276_ RVGGP 281_ PPEGL 286_ PGFNS 291_ GVMLL 296_ NLEAM 301_ RQSPL 306_ YSRLL 311_ EPAQV 316_ QQLAD 321_ KYHFR 326_ GHLGD 331_ QDFFT 336_ MIGME 341_ HPKLF 346_ HVLDC 351_ TWNRQ 356_ LCTWW 361_ RDHGY 366_ SDVFE 371_ AYFRC 376_ EGHVK 381_ IYHGN 386_CNTPI
1: Alpha-1,3-xylosyltransferase, which elongates the O-linked xylose-glucose disaccharide attached to EGF-like repeats in the extracellular domain of target proteins by catalyzing the addition of the second xylose (PubMed:22117070, PubMed:8982869). Known targets include Notch proteins and coagulation factors, such as F9 (PubMed:22117070, PubMed:8982869)