Glutaryl-CoA dehydrogenase, mitochondrial (GCD) (EC 1.3.8.6)
1_MALRG 6_ VSVRL 11_ LSRGP 16_ GLHVL 21_ RTWVS 26_ SAAQT 31_ EKGGR 36_ TQSQL 41_ AKSSR 46_ PEFDW 51_ QDPLV 56_ LEEQL 61_ TTDEI 66_ LIRDT 71_ FRTYC 76_ QERLM 81_ PRILL 86_ ANRNE 91_ VFHRE 96_ IISEM 101_ GELGV 106_ LGPTI 111_ KGYGC 116_ AGVSS 121_ VAYGL 126_ LAREL 131_ ERVDS 136_ GYRSA 141_ MSVQS 146_ SLVMH 151_ PIYAY 156_ GSEEQ 161_ RQKYL 166_ PQLAK 171_ GELLG 176_ CFGLT 181_ EPNSG 186_ SDPSS 191_ METRA 196_ HYNSS 201_ NKSYT 206_ LNGTK 211_ TWITN 216_ SPMAD 221_ LFVVW 226_ ARCED 231_ GCIRG 236_ FLLEK 241_ GMRGL 246_ SAPRI 251_ QGKFS 256_ LRASA 261_ TGMII 266_ MDGVE 271_ VPEEN 276_ VLPGA 281_ SSLGG 286_ PFGCL 291_ NNARY 296_ GIAWG 301_ VLGAS 306_ EFCLH 311_ TARQY 316_ ALDRM 321_ QFGVP 326_ LARNQ 331_ LIQKK 336_ LADML 341_ TEITL 346_ GLHAC 351_ LQLGR 356_ LKDQD 361_ KAAPE 366_ MVSLL 371_ KRNNC 376_ GKALD 381_ IARQA 386_ RDMLG 391_ GNGIS 396_ DEYHV 401_ IRHAM 406_ NLEAV 411_ NTYEG 416_ THDIH 421_ ALILG 426_ RAITG 431_IQAFT
1: Catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and CO(2) in the degradative pathway of L-lysine, L-hydroxylysine, and L-tryptophan metabolism. It uses electron transfer flavoprotein as its electron acceptor. Isoform Short is inactive