DnaJ homolog subfamily C member 30, mitochondrial (Williams-Beuren syndrome chromosomal region 18 protein)
1_MAAMR 6_ WRWWQ 11_ RLLPW 16_ RLLQA 21_ RGFPQ 26_ NSAPS 31_ LGLGA 36_ RTYSQ 41_ GDCSY 46_ SRTAL 51_ YDLLG 56_ VPSTA 61_ TQAQI 66_ KAAYY 71_ RQCFL 76_ YHPDR 81_ NSGSA 86_ EAAER 91_ FTRIS 96_ QAYVV 101_ LGSAT 106_ LRRKY 111_ DRGLL 116_ SDEDL 121_ RGPGV 126_ RPSRT 131_ PAPDP 136_ GSPRT 141_ PPPTS 146_ RTHDG 151_ SRASP 156_ GANRT 161_ MFNFD 166_ AFYQA 171_ HYGEQ 176_ LERER 181_ RLRAR 186_ REALR 191_ KRQEY 196_ RSMKG 201_ LRWED 206_ TRDTA 211_ AIFLI 216_ FSIFI 221_IIGFY
1: Mitochondrial protein enriched in neurons that acts as a regulator of mitochondrial respiration (By similarity). Associates with the ATP synthase complex and facilitates ATP synthesis (By similarity). May be a chaperone protein involved in the turnover of the subunits of mitochondrial complex I N-module. It facilitates the degradation of N-module subunits damaged by oxidative stress, and contributes to complex I functional efficiency (PubMed:33465056)