Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial (MCCase subunit alpha) (EC 6.4.1.4) (3-methylcrotonyl-CoA carboxylase 1) (3-methylcrotonyl-CoA carboxylase biotin-containing subunit) (3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha)
1_MAAAS 6_ AVSVL 11_ LVAAE 16_ RNRWH 21_ RLPSL 26_ LLPPR 31_ TWVWR 36_ QRTMK 41_ YTTAT 46_ GRNIT 51_ KVLIA 56_ NRGEI 61_ ACRVM 66_ RTAKK 71_ LGVQT 76_ VAVYS 81_ EADRN 86_ SMHVD 91_ MADEA 96_ YSIGP 101_ APSQQ 106_ SYLSM 111_ EKIIQ 116_ VAKTS 121_ AAQAI 126_ HPGCG 131_ FLSEN 136_ MEFAE 141_ LCKQE 146_ GIIFI 151_ GPPPS 156_ AIRDM 161_ GIKST 166_ SKSIM 171_ AAAGV 176_ PVVEG 181_ YHGED 186_ QSDQC 191_ LKEHA 196_ RRIGY 201_ PVMIK 206_ AVRGG 211_ GGKGM 216_ RIVRS 221_ EQEFQ 226_ EQLES 231_ ARREA 236_ KKSFN 241_ DDAML 246_ IEKFV 251_ DTPRH 256_ VEVQV 261_ FGDHH 266_ GNAVY 271_ LFERD 276_ CSVQR 281_ RHQKI 286_ IEEAP 291_ APGIK 296_ SEVRK 301_ KLGEA 306_ AVRAA 311_ KAVNY 316_ VGAGT 321_ VEFIM 326_ DSKHN 331_ FCFME 336_ MNTRL 341_ QVEHP 346_ VTEMI 351_ TGTDL 356_ VEWQL 361_ RIAAG 366_ EKIPL 371_ SQEEI 376_ TLQGH 381_ AFEAR 386_ IYAED 391_ PSNNF 396_ MPVAG 401_ PLVHL 406_ STPRA 411_ DPSTR 416_ IETGV 421_ RQGDE 426_ VSVHY 431_ DPMIA 436_ KLVVW 441_ AADRQ 446_ AALTK 451_ LRYSL 456_ RQYNI 461_ VGLHT 466_ NIDFL 471_ LNLSG 476_ HPEFE 481_ AGNVH 486_ TDFIP 491_ QHHKQ 496_ LLLSR 501_ KAAAK 506_ ESLCQ 511_ AALGL 516_ ILKEK 521_ AMTDT 526_ FTLQA 531_ HDQFS 536_ PFSSS 541_ SGRRL 546_ NISYT 551_ RNMTL 556_ KDGKN 561_ NVAIA 566_ VTYNH 571_ DGSYS 576_ MQIED 581_ KTFQV 586_ LGNLY 591_ SEGDC 596_ TYLKC 601_ SVNGV 606_ ASKAK 611_ LIILE 616_ NTIYL 621_ FSKEG 626_ SIEID 631_ IPVPK 636_ YLSSV 641_ SSQET 646_ QGGPL 651_ APMTG 656_ TIEKV 661_ FVKAG 666_ DKVKA 671_ GDSLM 676_ VMIAM 681_ KMEHT 686_ IKSPK 691_ DGTVK 696_ KVFYR 701_ EGAQA 706_ NRHTP 711_ LVEFE 716_EEESD
1: Biotin-attachment subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism