Gene name: TMEM126A

Uniprot entry:

Q9H061

Protein names:

Transmembrane protein 126A

Protein sequence:

1_MENHK 6_ SNNKE 11_ NITIV 16_ DISRK 21_ INQLP 26_ EAERN 31_ LLENG 36_ SVYVG 41_ LNAAL 46_ CGLIA 51_ NSLFR 56_ RILNV 61_ TKARI 66_ AAGLP 71_ MAGIP 76_ FLTTD 81_ LTYRC 86_ FVSFP 91_ LNTGD 96_ LDCET 101_ CTITR 106_ SGLTG 111_ LVIGG 116_ LYPVF 121_ LAIPV 126_ NGGLA 131_ ARYQS 136_ ALLPH 141_ KGNIL 146_ SYWIR 151_ TSKPV 156_ FRKML 161_ FPILL 166_ QTMFS 171_ AYLGS 176_ EQYKL 181_ LIKAL 186_QLSEP

Protein annotations

Protein functions:

1: Protein required for the cotranslational protein quality control in the inner membrane of the mitochondria (PubMed:38199007). Associates with newly synthesized polypeptides and may act as a chaperone that cooperates with OXA1L for the insertion of newly synthesized mitochondrial proteins into the inner membrane (PubMed:38199007). Required for the assembly of the ND4 module of mitochondrial complex I (PubMed:33879611, PubMed:33882309)