Gene name: QRSL1

Uniprot entry:

Q9H0R6

Protein names:

Glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial (Glu-AdT subunit A) (EC 6.3.5.7) (Glutaminyl-tRNA synthase-like protein 1)

Protein sequence:

1_MLGRS 6_ LREVS 11_ AALKQ 16_ GQITP 21_ TELCQ 26_ KCLSL 31_ IKKTK 36_ FLNAY 41_ ITVSE 46_ EVALK 51_ QAEES 56_ EKRYK 61_ NGQSL 66_ GDLDG 71_ IPIAV 76_ KDNFS 81_ TSGIE 86_ TTCAS 91_ NMLKG 96_ YIPPY 101_ NATVV 106_ QKLLD 111_ QGALL 116_ MGKTN 121_ LDEFA 126_ MGSGS 131_ TDGVF 136_ GPVKN 141_ PWSYS 146_ KQYRE 151_ KRKQN 156_ PHSEN 161_ EDSDW 166_ LITGG 171_ SSGGS 176_ AAAVS 181_ AFTCY 186_ AALGS 191_ DTGGS 196_ TRNPA 201_ AHCGL 206_ VGFKP 211_ SYGLV 216_ SRHGL 221_ IPLVN 226_ SMDVP 231_ GILTR 236_ CVDDA 241_ AIVLG 246_ ALAGP 251_ DPRDS 256_ TTVHE 261_ PINKP 266_ FMLPS 271_ LADVS 276_ KLCIG 281_ IPKEY 286_ LVPEL 291_ SSEVQ 296_ SLWSK 301_ AADLF 306_ ESEGA 311_ KVIEV 316_ SLPHT 321_ SYSIV 326_ CYHVL 331_ CTSEV 336_ ASNMA 341_ RFDGL 346_ QYGHR 351_ CDIDV 356_ STEAM 361_ YAATR 366_ REGFN 371_ DVVRG 376_ RILSG 381_ NFFLL 386_ KENYE 391_ NYFVK 396_ AQKVR 401_ RLIAN 406_ DFVNA 411_ FNSGV 416_ DVLLT 421_ PTTLS 426_ EAVPY 431_ LEFIK 436_ EDNRT 441_ RSAQD 446_ DIFTQ 451_ AVNMA 456_ GLPAV 461_ SIPVA 466_ LSNQG 471_ LPIGL 476_ QFIGR 481_ AFCDQ 486_ QLLTV 491_ AKWFE 496_ KQVQF 501_ PVIQL 506_ QELMD 511_ DCSAV 516_ LENEK 521_LASVS

Protein annotations

Protein functions:

1: Allows the formation of correctly charged Gln-tRNA(Gln) through the transamidation of misacylated Glu-tRNA(Gln) in the mitochondria. The reaction takes place in the presence of glutamine and ATP through an activated gamma-phospho-Glu-tRNA(Gln)