Inorganic pyrophosphatase 2, mitochondrial (EC 3.6.1.1) (Pyrophosphatase SID6-306) (Pyrophosphate phospho-hydrolase 2) (PPase 2)
1_MSALL 6_ RLLRT 11_ GAPAA 16_ ACLRL 21_ GTSAG 26_ TGSRR 31_ AMALY 36_ HTEER 41_ GQPCS 46_ QNYRL 51_ FFKNV 56_ TGHYI 61_ SPFHD 66_ IPLKV 71_ NSKEE 76_ NGIPM 81_ KKARN 86_ DEYEN 91_ LFNMI 96_ VEIPR 101_ WTNAK 106_ MEIAT 111_ KEPMN 116_ PIKQY 121_ VKDGK 126_ LRYVA 131_ NIFPY 136_ KGYIW 141_ NYGTL 146_ PQTWE 151_ DPHEK 156_ DKSTN 161_ CFGDN 166_ DPIDV 171_ CEIGS 176_ KILSC 181_ GEVIH 186_ VKILG 191_ ILALI 196_ DEGET 201_ DWKLI 206_ AINAN 211_ DPEAS 216_ KFHDI 221_ DDVKK 226_ FKPGY 231_ LEATL 236_ NWFRL 241_ YKVPD 246_ GKPEN 251_ QFAFN 256_ GEFKN 261_ KAFAL 266_ EVIKS 271_ THQCW 276_ KALLM 281_ KKCNG 286_ GAINC 291_ TNVQI 296_ SDSPF 301_ RCTQE 306_ EARSL 311_ VESVS 316_ SSPNK 321_ ESNEE 326_EQVWH
1: Hydrolyzes inorganic pyrophosphate (PubMed:27523597). This activity is essential for correct regulation of mitochondrial membrane potential, and mitochondrial organization and function (PubMed:27523598)