Gene name: PAAT

Uniprot entry:

Q9H8K7

Protein names:

ATPase PAAT (EC 3.6.1.-) (Protein associated with ABC transporters) (PAAT)

Protein sequence:

1_METRT 6_ EDGGL 11_ TRRPT 16_ LASSW 21_ DVAGG 26_ ALTHS 31_ LLLTR 36_ AGLGP 41_ GDFDW 46_ EELLA 51_ PPAPG 56_ QDLVI 61_ LKRNH 66_ NNKDE 71_ NPCFL 76_ YLRCG 81_ PDGGE 86_ EIASI 91_ GILSS 96_ ARNME 101_ VYLGE 106_ EYCGT 111_ SRGKN 116_ VCTVL 121_ DDSEH 126_ EKIIL 131_ YKKNL 136_ KLESS 141_ THACK 146_ IKLLS 151_ FGERQ 156_ CVFIS 161_ KVVVH 166_ MRSVF 171_ ANSST 176_ SSPAL 181_ GSRID 186_ LDKVQ 191_ TIMES 196_ MGSKL 201_ SPGAQ 206_ QLMDM 211_ VRCQQ 216_ RNCIP 221_ IGEQL 226_ QSVLG 231_ NSGYK 236_ HMIGL 241_ QSSST 246_ LGTLN 251_ KSSST 256_ PFPFR 261_ TGLTS 266_ GNVTE 271_ NLQTY 276_ IDKST 281_ QLPGG 286_ ENSTK 291_ LDECK 296_ VMPQN 301_ HSFLE 306_ NDLKN 311_ AMASF 316_ LPKKV 321_ SDNSN 326_ IPNSE 331_ LLPFL 336_ QNLCS 341_ QVNHL 346_ HVGNK 351_ TECQE 356_ NITKH 361_ GERIL 366_ GVGME 371_ EQSIC 376_ SYLEK 381_ ILSKN 386_ MELME 391_ KKLMD 396_ YIDQR 401_ IHELQ 406_ EHIDD 411_ KIALL 416_ LDLLQ 421_ NPNSP 426_ PTGIP 431_ LRHYD 436_SGERL

Protein annotations

Protein functions:

1: ATPase that regulates mitochondrial ABC transporters ABCB7, ABCB8/MITOSUR and ABCB10 (PubMed:25063848). Regulates mitochondrial ferric concentration and heme biosynthesis and plays a role in the maintenance of mitochondrial homeostasis and cell survival (PubMed:25063848)