Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial (MCCase subunit beta) (EC 6.4.1.4) (3-methylcrotonyl-CoA carboxylase 2) (3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit) (3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta)
1_MWAVL 6_ RLALR 11_ PCARA 16_ SPAGP 21_ RAYHG 26_ DSVAS 31_ LGTQP 36_ DLGSA 41_ LYQEN 46_ YKQMK 51_ ALVNQ 56_ LHERV 61_ EHIKL 66_ GGGEK 71_ ARALH 76_ ISRGK 81_ LLPRE 86_ RIDNL 91_ IDPGS 96_ PFLEL 101_ SQFAG 106_ YQLYD 111_ NEEVP 116_ GGGII 121_ TGIGR 126_ VSGVE 131_ CMIIA 136_ NDATV 141_ KGGAY 146_ YPVTV 151_ KKQLR 156_ AQEIA 161_ MQNRL 166_ PCIYL 171_ VDSGG 176_ AYLPR 181_ QADVF 186_ PDRDH 191_ FGRTF 196_ YNQAI 201_ MSSKN 206_ IAQIA 211_ VVMGS 216_ CTAGG 221_ AYVPA 226_ MADEN 231_ IIVRK 236_ QGTIF 241_ LAGPP 246_ LVKAA 251_ TGEEV 256_ SAEDL 261_ GGADL 266_ HCRKS 271_ GVSDH 276_ WALDD 281_ HHALH 286_ LTRKV 291_ VRNLN 296_ YQKKL 301_ DVTIE 306_ PSEEP 311_ LFPAD 316_ ELYGI 321_ VGANL 326_ KRSFD 331_ VREVI 336_ ARIVD 341_ GSRFT 346_ EFKAF 351_ YGDTL 356_ VTGFA 361_ RIFGY 366_ PVGIV 371_ GNNGV 376_ LFSES 381_ AKKGT 386_ HFVQL 391_ CCQRN 396_ IPLLF 401_ LQNIT 406_ GFMVG 411_ REYEA 416_ EGIAK 421_ DGAKM 426_ VAAVA 431_ CAQVP 436_ KITLI 441_ IGGSY 446_ GAGNY 451_ GMCGR 456_ AYSPR 461_ FLYIW 466_ PNARI 471_ SVMGG 476_ EQAAN 481_ VLATI 486_ TKDQR 491_ AREGK 496_ QFSSA 501_ DEAAL 506_ KEPII 511_ KKFEE 516_ EGNPY 521_ YSSAR 526_ VWDDG 531_ IIDPA 536_ DTRLV 541_ LGLSF 546_ SAALN 551_ APIEK 556_TDFGI
1: Carboxyltransferase subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism