Gene name: AASS

Uniprot entry:

Q9UDR5

Protein names:

Alpha-aminoadipic semialdehyde synthase, mitochondrial (LKR/SDH) [Includes: Lysine ketoglutarate reductase (LKR) (LOR) (EC 1.5.1.8); Saccharopine dehydrogenase (SDH) (EC 1.5.1.9)]

Protein sequence:

1_MLQVH 6_ RTGLG 11_ RLGVS 16_ LSKGL 21_ HHKAV 26_ LAVRR 31_ EDVNA 36_ WERRA 41_ PLAPK 46_ HIKGI 51_ TNLGY 56_ KVLIQ 61_ PSNRR 66_ AIHDK 71_ DYVKA 76_ GGILQ 81_ EDISE 86_ ACLIL 91_ GVKRP 96_ PEEKL 101_ MSRKT 106_ YAFFS 111_ HTIKA 116_ QEANM 121_ GLLDE 126_ ILKQE 131_ IRLID 136_ YEKMV 141_ DHRGV 146_ RVVAF 151_ GQWAG 156_ VAGMI 161_ NILHG 166_ MGLRL 171_ LALGH 176_ HTPFM 181_ HIGMA 186_ HNYRN 191_ SSQAV 196_ QAVRD 201_ AGYEI 206_ SLGLM 211_ PKSIG 216_ PLTFV 221_ FTGTG 226_ NVSKG 231_ AQAIF 236_ NELPC 241_ EYVEP 246_ HELKE 251_ VSQTG 256_ DLRKV 261_ YGTVL 266_ SRHHH 271_ LVRKT 276_ DAVYD 281_ PAEYD 286_ KHPER 291_ YISRF 296_ NTDIA 301_ PYTTC 306_ LINGI 311_ YWEQN 316_ TPRLL 321_ TRQDA 326_ QSLLA 331_ PGKFS 336_ PAGVE 341_ GCPAL 346_ PHKLV 351_ AICDI 356_ SADTG 361_ GSIEF 366_ MTECT 371_ TIEHP 376_ FCMYD 381_ ADQHI 386_ IHDSV 391_ EGSGI 396_ LMCSI 401_ DNLPA 406_ QLPIE 411_ ATECF 416_ GDMLY 421_ PYVEE 426_ MILSD 431_ ATQPL 436_ ESQNF 441_ SPVVR 446_ DAVIT 451_ SNGTL 456_ PDKYK 461_ YIQTL 466_ RESRE 471_ RAQSL 476_ SMGTR 481_ RKVLV 486_ LGSGY 491_ ISEPV 496_ LEYLS 501_ RDGNI 506_ EITVG 511_ SDMKN 516_ QIEQL 521_ GKKYN 526_ INPVS 531_ MDICK 536_ QEEKL 541_ GFLVA 546_ KQDLV 551_ ISLLP 556_ YVLHP 561_ LVAKA 566_ CITNK 571_ VNMVT 576_ ASYIT 581_ PALKE 586_ LEKSV 591_ EDAGI 596_ TIIGE 601_ LGLDP 606_ GLDHM 611_ LAMET 616_ IDKAK 621_ EVGAT 626_ IESYI 631_ SYCGG 636_ LPAPE 641_ HSNNP 646_ LRYKF 651_ SWSPV 656_ GVLMN 661_ VMQSA 666_ TYLLD 671_ GKVVN 676_ VAGGI 681_ SFLDA 686_ VTSMD 691_ FFPGL 696_ NLEGY 701_ PNRDS 706_ TKYAE 711_ IYGIS 716_ SAHTL 721_ LRGTL 726_ RYKGY 731_ MKALN 736_ GFVKL 741_ GLINR 746_ EALPA 751_ FRPEA 756_ NPLTW 761_ KQLLC 766_ DLVGI 771_ SPSSE 776_ HDVLK 781_ EAVLK 786_ KLGGD 791_ NTQLE 796_ AAEWL 801_ GLLGD 806_ EQVPQ 811_ AESIL 816_ DALSK 821_ HLVMK 826_ LSYGP 831_ EEKDM 836_ IVMRD 841_ SFGIR 846_ HPSGH 851_ LEHKT 856_ IDLVA 861_ YGDIN 866_ GFSAM 871_ AKTVG 876_ LPTAM 881_ AAKML 886_ LDGEI 891_ GAKGL 896_ MGPFS 901_ KEIYG 906_ PILER 911_ IKAEG 916_ IIYTT 921_QSTIK

Protein annotations

Protein functions:

1: Bifunctional enzyme that catalyzes the first two steps in lysine degradation