Gene name: BCS1L

Uniprot entry:

Q9Y276

Protein names:

Mitochondrial chaperone BCS1 (h-BCS1) (BCS1-like protein)

Protein sequence:

1_MPLSD 6_ FILAL 11_ KDNPY 16_ FGAGF 21_ GLVGV 26_ GTALA 31_ LARKG 36_ VQLGL 41_ VAFRR 46_ HYMIT 51_ LEVPA 56_ RDRSY 61_ AWLLS 66_ WLTRH 71_ STRTQ 76_ HLSVE 81_ TSYLQ 86_ HESGR 91_ ISTKF 96_ EFVPS 101_ PGNHF 106_ IWYRG 111_ KWIRV 116_ ERSRE 121_ MQMID 126_ LQTGT 131_ PWESV 136_ TFTAL 141_ GTDRK 146_ VFFNI 151_ LEEAR 156_ ELALQ 161_ QEEGK 166_ TVMYT 171_ AVGSE 176_ WRPFG 181_ YPRRR 186_ RPLNS 191_ VVLQQ 196_ GLADR 201_ IVRDV 206_ QEFID 211_ NPKWY 216_ TDRGI 221_ PYRRG 226_ YLLYG 231_ PPGCG 236_ KSSFI 241_ TALAG 246_ ELEHS 251_ ICLLS 256_ LTDSS 261_ LSDDR 266_ LNHLL 271_ SVAPQ 276_ QSLVL 281_ LEDVD 286_ AAFLS 291_ RDLAV 296_ ENPVK 301_ YQGLG 306_ RLTFS 311_ GLLNA 316_ LDGVA 321_ STEAR 326_ IVFMT 331_ TNHVD 336_ RLDPA 341_ LIRPG 346_ RVDLK 351_ EYVGY 356_ CSHWQ 361_ LTQMF 366_ QRFYP 371_ GQAPS 376_ LAENF 381_ AEHVL 386_ RATNQ 391_ ISPAQ 396_ VQGYF 401_ MLYKN 406_ DPVGA 411_IHNAE

Protein annotations

Protein functions:

1: Chaperone necessary for the incorporation of Rieske iron-sulfur protein UQCRFS1 into the mitochondrial respiratory chain complex III (PubMed:11528392, PubMed:9878253). Plays an important role in the maintenance of mitochondrial tubular networks, respiratory chain assembly and formation of the LETM1 complex (PubMed:18628306)