Ribitol-5-phosphate xylosyltransferase 1 (EC 2.4.2.61) (Transmembrane protein 5) (UDP-D-xylose:ribitol-5-phosphate beta1,4-xylosyltransferase)
1_MRLTR 6_ KRLCS 11_ FLIAL 16_ YCLFS 21_ LYAAY 26_ HVFFG 31_ RRRQA 36_ PAGSP 41_ RGLRK 46_ GAAPA 51_ RERRG 56_ REQST 61_ LESEE 66_ WNPWE 71_ GDEKN 76_ EQQHR 81_ FKTSL 86_ QILDK 91_ STKGK 96_ TDLSV 101_ QIWGK 106_ AAIGL 111_ YLWEH 116_ IFEGL 121_ LDPSD 126_ VTAQW 131_ REGKS 136_ IVGRT 141_ QYSFI 146_ TGPAV 151_ IPGYF 156_ SVDVN 161_ NVVLI 166_ LNGRE 171_ KAKIF 176_ YATQW 181_ LLYAQ 186_ NLVQI 191_ QKLQH 196_ LAVVL 201_ LGNEH 206_ CDNEW 211_ INPFL 216_ KRNGG 221_ FVELL 226_ FIIYD 231_ SPWIN 236_ DVDVF 241_ QWPLG 246_ VATYR 251_ NFPVV 256_ EASWS 261_ MLHDE 266_ RPYLC 271_ NFLGT 276_ IYENS 281_ SRQAL 286_ MNILK 291_ KDGND 296_ KLCWV 301_ SAREH 306_ WQPQE 311_ TNESL 316_ KNYQD 321_ ALLQS 326_ DLTLC 331_ PVGVN 336_ TECYR 341_ IYEAC 346_ SYGSI 351_ PVVED 356_ VMTAG 361_ NCGNT 366_ SVHHG 371_ APLQL 376_ LKSMG 381_ APFIF 386_ IKNWK 391_ ELPAV 396_ LEKEK 401_ TIILQ 406_ EKIER 411_ RKMLL 416_ QWYQH 421_ FKTEL 426_ KMKFT 431_ NILES 436_SFLMN
1: Acts as a UDP-D-xylose:ribitol-5-phosphate beta1,4-xylosyltransferase, which catalyzes the transfer of UDP-D-xylose to ribitol 5-phosphate (Rbo5P) to form the Xylbeta1-4Rbo5P linkage on O-mannosyl glycan (Probable) (PubMed:27733679, PubMed:29477842). Participates in the biosynthesis of the phosphorylated O-mannosyl trisaccharide (N-acetylgalactosamine-beta-3-N-acetylglucosamine-beta-4-(phosphate-6-)mannose), a carbohydrate structure present in alpha-dystroglycan (DAG1), which is required for binding laminin G-like domain-containing extracellular proteins with high affinity (Probable) (PubMed:25279699, PubMed:27601598, PubMed:27733679)